Links to Exploration step
Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en">Familial Intrahepatic Cholestasis: An Update</title><author><name sortKey="Riely, Caroline A" sort="Riely, Caroline A" uniqKey="Riely C" first="Caroline A." last="Riely">Caroline A. Riely</name></author></titleStmt><publicationStmt><idno type="wicri:source">PMC</idno><idno type="pmid">452627</idno><idno type="pmc">2595717</idno><idno type="url">http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2595717</idno><idno type="RBID">PMC:2595717</idno><date when="1979">1979</date><idno type="wicri:Area/Pmc/Corpus">001C33</idno><idno type="wicri:explorRef" wicri:stream="Pmc" wicri:step="Corpus" wicri:corpus="PMC">001C33</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en" level="a" type="main">Familial Intrahepatic Cholestasis: An Update</title><author><name sortKey="Riely, Caroline A" sort="Riely, Caroline A" uniqKey="Riely C" first="Caroline A." last="Riely">Caroline A. Riely</name></author></analytic><series><title level="j">The Yale Journal of Biology and Medicine</title><idno type="ISSN">0044-0086</idno><idno type="eISSN">1551-4056</idno><imprint><date when="1979">1979</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en"><p>Familial intrahepatic cholestasis is a confusing group of syndromes. Four forms are defined and discussed in detail (“arteriohepatic dysplasia,” the Byler syndrome, the THCA syndrome, and Norwegian cholestasis). A comparison of the distinguishing characteristics of these syndromes demonstrates that they share many features, including areflexia, retinal degeneration, and paucity of the intrahepatic bile ducts on biopsy. Alternatively, some traits appear to be specific for a single syndrome: posterior embryotoxon and bony anomalies for arteriohepatic dysplasia, the presence of an abnormal bile acid for the THCA syndrome, and giant cell transformation for Norwegian cholestasis. These syndromes, although rare, merit complete evaluation because, as nature's experiments in bile formation, they represent models of cholestasis and may provide clues to the understanding both of other forms of cholestasis of unknown etiology and of the normal mechanisms of bile formation.</p><sec sec-type="scanned-figures"><title>Images</title><fig id="F1"><label>FIG. 1</label><graphic xlink:href="yjbm00124-0096-a" xlink:role="95"></graphic></fig></sec></div></front></TEI><pmc article-type="research-article"><pmc-dir>properties open_access</pmc-dir>
<front><journal-meta><journal-id journal-id-type="nlm-ta">Yale J Biol Med</journal-id><journal-title>The Yale Journal of Biology and Medicine</journal-title><issn pub-type="ppub">0044-0086</issn><issn pub-type="epub">1551-4056</issn></journal-meta><article-meta><article-id pub-id-type="pmid">452627</article-id><article-id pub-id-type="pmc">2595717</article-id><article-categories><subj-group subj-group-type="heading"><subject>Articles</subject></subj-group></article-categories><title-group><article-title>Familial Intrahepatic Cholestasis: An Update</article-title></title-group><contrib-group><contrib contrib-type="author"><name><surname>Riely</surname><given-names>Caroline A.</given-names></name></contrib></contrib-group><pub-date pub-type="ppub"><season>Jan-Feb</season><year>1979</year></pub-date><volume>52</volume><issue>1</issue><fpage>89</fpage><lpage>98</lpage><abstract><p>Familial intrahepatic cholestasis is a confusing group of syndromes. Four forms are defined and discussed in detail (“arteriohepatic dysplasia,” the Byler syndrome, the THCA syndrome, and Norwegian cholestasis). A comparison of the distinguishing characteristics of these syndromes demonstrates that they share many features, including areflexia, retinal degeneration, and paucity of the intrahepatic bile ducts on biopsy. Alternatively, some traits appear to be specific for a single syndrome: posterior embryotoxon and bony anomalies for arteriohepatic dysplasia, the presence of an abnormal bile acid for the THCA syndrome, and giant cell transformation for Norwegian cholestasis. These syndromes, although rare, merit complete evaluation because, as nature's experiments in bile formation, they represent models of cholestasis and may provide clues to the understanding both of other forms of cholestasis of unknown etiology and of the normal mechanisms of bile formation.</p><sec sec-type="scanned-figures"><title>Images</title><fig id="F1"><label>FIG. 1</label><graphic xlink:href="yjbm00124-0096-a" xlink:role="95"></graphic></fig></sec></abstract></article-meta></front><body><supplementary-material content-type="scanned-pages"><graphic xlink:href="yjbm00124-0090.tif" xlink:title="scanned-page" xlink:role="89" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0091.tif" xlink:title="scanned-page" xlink:role="90" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0092.tif" xlink:title="scanned-page" xlink:role="91" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0093.tif" xlink:title="scanned-page" xlink:role="92" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0094.tif" xlink:title="scanned-page" xlink:role="93" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0095.tif" xlink:title="scanned-page" xlink:role="94" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0096.tif" xlink:title="scanned-page" xlink:role="95" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0097.tif" xlink:title="scanned-page" xlink:role="96" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0098.tif" xlink:title="scanned-page" xlink:role="97" mimetype="image" mime-subtype="tiff"></graphic><graphic xlink:href="yjbm00124-0099.tif" xlink:title="scanned-page" xlink:role="98" mimetype="image" mime-subtype="tiff"></graphic></supplementary-material></body></pmc></record>Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/Pmc/Corpus
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 001C33 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/Pmc/Corpus/biblio.hfd -nk 001C33 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien
|wiki= Wicri/Sante
|area= LymphedemaV1
|flux= Pmc
|étape= Corpus
|type= RBID
|clé=
|texte=
}}
| This area was generated with Dilib version V0.6.31. |  |