Tuberous sclerosis with pulmonary involvement.
Identifieur interne : 004531 ( Pmc/Checkpoint ); précédent : 004530; suivant : 004532Tuberous sclerosis with pulmonary involvement.
Auteurs : B. A. Liberman ; D. W. Chamberlain ; R. S. GoldsteinSource :
- Canadian Medical Association Journal [ 0008-4409 ] ; 1984.
Abstract
Pulmonary tuberous sclerosis produced interstitial disease in a woman with normal-sized lungs; numerous hemosiderin-laden macrophages were found in the fluid obtained through bronchoalveolar lavage. The pathological changes seen in the lungs were identical to those of pulmonary lymphangiomyomatosis, in which the constellation of clinical signs usually found in tuberous sclerosis is absent. The two conditions are sufficiently similar in clinical presentation, pathological changes and prognosis to be considered variants of the same disease. The recent findings of progestin receptors in lung tissue from patients with pulmonary lymphangiomyomatosis will likely direct future management towards hormonal manipulation.
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PubMed: 6692213
PubMed Central: 1875338
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<front><journal-meta><journal-id journal-id-type="nlm-ta">Can Med Assoc J</journal-id><journal-title>Canadian Medical Association Journal</journal-title><issn pub-type="ppub">0008-4409</issn></journal-meta><article-meta><article-id pub-id-type="pmid">6692213</article-id><article-id pub-id-type="pmc">1875338</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group></article-categories><title-group><article-title>Tuberous sclerosis with pulmonary involvement.</article-title></title-group><contrib-group><contrib contrib-type="author"><name><surname>Liberman</surname><given-names>B. A.</given-names></name></contrib><contrib contrib-type="author"><name><surname>Chamberlain</surname><given-names>D. W.</given-names></name></contrib><contrib contrib-type="author"><name><surname>Goldstein</surname><given-names>R. S.</given-names></name></contrib></contrib-group><pub-date pub-type="ppub"><day>1</day><month>2</month><year>1984</year></pub-date><volume>130</volume><issue>3</issue><fpage>287</fpage><lpage>289</lpage><abstract><p>Pulmonary tuberous sclerosis produced interstitial disease in a woman with normal-sized lungs; numerous hemosiderin-laden macrophages were found in the fluid obtained through bronchoalveolar lavage. The pathological changes seen in the lungs were identical to those of pulmonary lymphangiomyomatosis, in which the constellation of clinical signs usually found in tuberous sclerosis is absent. The two conditions are sufficiently similar in clinical presentation, pathological changes and prognosis to be considered variants of the same disease. The recent findings of progestin receptors in lung tissue from patients with pulmonary lymphangiomyomatosis will likely direct future management towards hormonal manipulation.</p><sec sec-type="scanned-figures"><title>Images</title><fig id="F1"><label>FIG. 1</label><graphic xlink:href="canmedaj01408-0049-a" xlink:role="287"></graphic></fig><fig id="F2"><label>FIG. 2</label><graphic xlink:href="canmedaj01408-0050-a" xlink:role="288"></graphic></fig><fig id="F3"><label>FIG. 3</label><graphic xlink:href="canmedaj01408-0050-b" xlink:role="288"></graphic></fig></sec></abstract></article-meta></front></pmc><affiliations><list></list><tree><noCountry><name sortKey="Chamberlain, D W" sort="Chamberlain, D W" uniqKey="Chamberlain D" first="D. W." last="Chamberlain">D. W. Chamberlain</name><name sortKey="Goldstein, R S" sort="Goldstein, R S" uniqKey="Goldstein R" first="R. S." last="Goldstein">R. S. Goldstein</name><name sortKey="Liberman, B A" sort="Liberman, B A" uniqKey="Liberman B" first="B. A." last="Liberman">B. A. Liberman</name></noCountry></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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