Serveur d'exploration sur le lymphœdème

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report

Identifieur interne : 000817 ( PascalFrancis/Checkpoint ); précédent : 000816; suivant : 000818

Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report

Auteurs : Brigitte Granel [France] ; Jacques Serratrice [France] ; Valérie Juhan [France] ; Pierre Champsaur [France] ; Claude Weiller-Merli [France] ; Xavier Pache [France] ; Laure Swiader [France] ; Patrick Disdier [France] ; Pierre-Jean Weiller [France]

Source :

RBID : Pascal:01-0378023

Descripteurs français

English descriptors

Abstract

Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.


Affiliations:


Links toward previous steps (curation, corpus...)


Links to Exploration step

Pascal:01-0378023

Le document en format XML

<record>
<TEI>
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en" level="a">Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report</title>
<author>
<name sortKey="Granel, Brigitte" sort="Granel, Brigitte" uniqKey="Granel B" first="Brigitte" last="Granel">Brigitte Granel</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Serratrice, Jacques" sort="Serratrice, Jacques" uniqKey="Serratrice J" first="Jacques" last="Serratrice">Jacques Serratrice</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Juhan, Valerie" sort="Juhan, Valerie" uniqKey="Juhan V" first="Valérie" last="Juhan">Valérie Juhan</name>
<affiliation wicri:level="3">
<inist:fA14 i1="02">
<s1>Service de Radiologie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Champsaur, Pierre" sort="Champsaur, Pierre" uniqKey="Champsaur P" first="Pierre" last="Champsaur">Pierre Champsaur</name>
<affiliation wicri:level="3">
<inist:fA14 i1="02">
<s1>Service de Radiologie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
<affiliation wicri:level="3">
<inist:fA14 i1="03">
<s1>Laboratoire d'Anatomie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Weiller Merli, Claude" sort="Weiller Merli, Claude" uniqKey="Weiller Merli C" first="Claude" last="Weiller-Merli">Claude Weiller-Merli</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Pache, Xavier" sort="Pache, Xavier" uniqKey="Pache X" first="Xavier" last="Pache">Xavier Pache</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Swiader, Laure" sort="Swiader, Laure" uniqKey="Swiader L" first="Laure" last="Swiader">Laure Swiader</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Disdier, Patrick" sort="Disdier, Patrick" uniqKey="Disdier P" first="Patrick" last="Disdier">Patrick Disdier</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Weiller, Pierre Jean" sort="Weiller, Pierre Jean" uniqKey="Weiller P" first="Pierre-Jean" last="Weiller">Pierre-Jean Weiller</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">INIST</idno>
<idno type="inist">01-0378023</idno>
<date when="2001">2001</date>
<idno type="stanalyst">PASCAL 01-0378023 INIST</idno>
<idno type="RBID">Pascal:01-0378023</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">000838</idno>
<idno type="wicri:Area/PascalFrancis/Curation">000122</idno>
<idno type="wicri:Area/PascalFrancis/Checkpoint">000817</idno>
<idno type="wicri:explorRef" wicri:stream="PascalFrancis" wicri:step="Checkpoint">000817</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title xml:lang="en" level="a">Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report</title>
<author>
<name sortKey="Granel, Brigitte" sort="Granel, Brigitte" uniqKey="Granel B" first="Brigitte" last="Granel">Brigitte Granel</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Serratrice, Jacques" sort="Serratrice, Jacques" uniqKey="Serratrice J" first="Jacques" last="Serratrice">Jacques Serratrice</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Juhan, Valerie" sort="Juhan, Valerie" uniqKey="Juhan V" first="Valérie" last="Juhan">Valérie Juhan</name>
<affiliation wicri:level="3">
<inist:fA14 i1="02">
<s1>Service de Radiologie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Champsaur, Pierre" sort="Champsaur, Pierre" uniqKey="Champsaur P" first="Pierre" last="Champsaur">Pierre Champsaur</name>
<affiliation wicri:level="3">
<inist:fA14 i1="02">
<s1>Service de Radiologie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
<affiliation wicri:level="3">
<inist:fA14 i1="03">
<s1>Laboratoire d'Anatomie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>4 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Weiller Merli, Claude" sort="Weiller Merli, Claude" uniqKey="Weiller Merli C" first="Claude" last="Weiller-Merli">Claude Weiller-Merli</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Pache, Xavier" sort="Pache, Xavier" uniqKey="Pache X" first="Xavier" last="Pache">Xavier Pache</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Swiader, Laure" sort="Swiader, Laure" uniqKey="Swiader L" first="Laure" last="Swiader">Laure Swiader</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Disdier, Patrick" sort="Disdier, Patrick" uniqKey="Disdier P" first="Patrick" last="Disdier">Patrick Disdier</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Weiller, Pierre Jean" sort="Weiller, Pierre Jean" uniqKey="Weiller P" first="Pierre-Jean" last="Weiller">Pierre-Jean Weiller</name>
<affiliation wicri:level="3">
<inist:fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</inist:fA14>
<country>France</country>
<placeName>
<region type="region">Provence-Alpes-Côte d'Azur</region>
<region type="old region">Provence-Alpes-Côte d'Azur</region>
<settlement type="city">Marseille</settlement>
</placeName>
</affiliation>
</author>
</analytic>
<series>
<title level="j" type="main">Angiology</title>
<title level="j" type="abbreviated">Angiology</title>
<idno type="ISSN">0003-3197</idno>
<imprint>
<date when="2001">2001</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt>
<title level="j" type="main">Angiology</title>
<title level="j" type="abbreviated">Angiology</title>
<idno type="ISSN">0003-3197</idno>
</seriesStmt>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="KwdEn" xml:lang="en">
<term>Case study</term>
<term>Clinical form</term>
<term>Human</term>
<term>Lower limb</term>
<term>Lymphedema</term>
<term>Polysplenia</term>
<term>Severity score</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr">
<term>Lymphoedème</term>
<term>Membre inférieur</term>
<term>Indice gravité</term>
<term>Polysplénie</term>
<term>Forme clinique</term>
<term>Homme</term>
<term>Etude cas</term>
</keywords>
<keywords scheme="Wicri" type="topic" xml:lang="fr">
<term>Homme</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.</div>
</front>
</TEI>
<inist>
<standard h6="B">
<pA>
<fA01 i1="01" i2="1">
<s0>0003-3197</s0>
</fA01>
<fA02 i1="01">
<s0>ANGIAB</s0>
</fA02>
<fA03 i2="1">
<s0>Angiology</s0>
</fA03>
<fA05>
<s2>52</s2>
</fA05>
<fA06>
<s2>6</s2>
</fA06>
<fA08 i1="01" i2="1" l="ENG">
<s1>Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report</s1>
</fA08>
<fA11 i1="01" i2="1">
<s1>GRANEL (Brigitte)</s1>
</fA11>
<fA11 i1="02" i2="1">
<s1>SERRATRICE (Jacques)</s1>
</fA11>
<fA11 i1="03" i2="1">
<s1>JUHAN (Valérie)</s1>
</fA11>
<fA11 i1="04" i2="1">
<s1>CHAMPSAUR (Pierre)</s1>
</fA11>
<fA11 i1="05" i2="1">
<s1>WEILLER-MERLI (Claude)</s1>
</fA11>
<fA11 i1="06" i2="1">
<s1>PACHE (Xavier)</s1>
</fA11>
<fA11 i1="07" i2="1">
<s1>SWIADER (Laure)</s1>
</fA11>
<fA11 i1="08" i2="1">
<s1>DISDIER (Patrick)</s1>
</fA11>
<fA11 i1="09" i2="1">
<s1>WEILLER (Pierre-Jean)</s1>
</fA11>
<fA14 i1="01">
<s1>Service de Médecine Interne, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>1 aut.</sZ>
<sZ>2 aut.</sZ>
<sZ>5 aut.</sZ>
<sZ>6 aut.</sZ>
<sZ>7 aut.</sZ>
<sZ>8 aut.</sZ>
<sZ>9 aut.</sZ>
</fA14>
<fA14 i1="02">
<s1>Service de Radiologie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>3 aut.</sZ>
<sZ>4 aut.</sZ>
</fA14>
<fA14 i1="03">
<s1>Laboratoire d'Anatomie, CHU Timone</s1>
<s2>Marseille</s2>
<s3>FRA</s3>
<sZ>4 aut.</sZ>
</fA14>
<fA20>
<s1>421-423</s1>
</fA20>
<fA21>
<s1>2001</s1>
</fA21>
<fA23 i1="01">
<s0>ENG</s0>
</fA23>
<fA43 i1="01">
<s1>INIST</s1>
<s2>8327</s2>
<s5>354000096623970080</s5>
</fA43>
<fA44>
<s0>0000</s0>
<s1>© 2001 INIST-CNRS. All rights reserved.</s1>
</fA44>
<fA45>
<s0>8 ref.</s0>
</fA45>
<fA47 i1="01" i2="1">
<s0>01-0378023</s0>
</fA47>
<fA60>
<s1>P</s1>
</fA60>
<fA61>
<s0>A</s0>
</fA61>
<fA64 i1="01" i2="1">
<s0>Angiology</s0>
</fA64>
<fA66 i1="01">
<s0>USA</s0>
</fA66>
<fC01 i1="01" l="ENG">
<s0>Polysplenia syndrome includes a group of congenital abnormalities involving the spleen, gastrointestinal tract, liver, and cardiovascular system. A case of severe lower limbs lymphedema occurring in a young woman with polysplenia, azygous continuation of the inferior vena cava, short pancreas, and preduodenal portal vein is reported. Lower limb lymphedema could represent a new clinical manifestation associated with polysplenia syndrome. Lymphedema could be the result of a primary anomaly of the lymphatic system or be induced by high pressure in the venous system or by compression of the lymphatic circulation by the hypertrophic azygous vessels in the posterior mediastinum.</s0>
</fC01>
<fC02 i1="01" i2="X">
<s0>002B12B04</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE">
<s0>Lymphoedème</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="ENG">
<s0>Lymphedema</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="SPA">
<s0>Linfedema</s0>
<s5>01</s5>
</fC03>
<fC03 i1="02" i2="X" l="FRE">
<s0>Membre inférieur</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="ENG">
<s0>Lower limb</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="SPA">
<s0>Miembro inferior</s0>
<s5>02</s5>
</fC03>
<fC03 i1="03" i2="X" l="FRE">
<s0>Indice gravité</s0>
<s5>03</s5>
</fC03>
<fC03 i1="03" i2="X" l="ENG">
<s0>Severity score</s0>
<s5>03</s5>
</fC03>
<fC03 i1="03" i2="X" l="SPA">
<s0>Indicio gravedad</s0>
<s5>03</s5>
</fC03>
<fC03 i1="04" i2="X" l="FRE">
<s0>Polysplénie</s0>
<s5>04</s5>
</fC03>
<fC03 i1="04" i2="X" l="ENG">
<s0>Polysplenia</s0>
<s5>04</s5>
</fC03>
<fC03 i1="04" i2="X" l="SPA">
<s0>Poliesplenia</s0>
<s5>04</s5>
</fC03>
<fC03 i1="05" i2="X" l="FRE">
<s0>Forme clinique</s0>
<s5>17</s5>
</fC03>
<fC03 i1="05" i2="X" l="ENG">
<s0>Clinical form</s0>
<s5>17</s5>
</fC03>
<fC03 i1="05" i2="X" l="SPA">
<s0>Forma clínica</s0>
<s5>17</s5>
</fC03>
<fC03 i1="06" i2="X" l="FRE">
<s0>Homme</s0>
<s5>20</s5>
</fC03>
<fC03 i1="06" i2="X" l="ENG">
<s0>Human</s0>
<s5>20</s5>
</fC03>
<fC03 i1="06" i2="X" l="SPA">
<s0>Hombre</s0>
<s5>20</s5>
</fC03>
<fC03 i1="07" i2="X" l="FRE">
<s0>Etude cas</s0>
<s5>21</s5>
</fC03>
<fC03 i1="07" i2="X" l="ENG">
<s0>Case study</s0>
<s5>21</s5>
</fC03>
<fC03 i1="07" i2="X" l="SPA">
<s0>Estudio caso</s0>
<s5>21</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE">
<s0>Appareil circulatoire pathologie</s0>
<s5>37</s5>
</fC07>
<fC07 i1="01" i2="X" l="ENG">
<s0>Cardiovascular disease</s0>
<s5>37</s5>
</fC07>
<fC07 i1="01" i2="X" l="SPA">
<s0>Aparato circulatorio patología</s0>
<s5>37</s5>
</fC07>
<fC07 i1="02" i2="X" l="FRE">
<s0>Lymphatique pathologie</s0>
<s5>38</s5>
</fC07>
<fC07 i1="02" i2="X" l="ENG">
<s0>Lymphatic vessel disease</s0>
<s5>38</s5>
</fC07>
<fC07 i1="02" i2="X" l="SPA">
<s0>Linfático patología</s0>
<s5>38</s5>
</fC07>
<fN21>
<s1>267</s1>
</fN21>
</pA>
</standard>
</inist>
<affiliations>
<list>
<country>
<li>France</li>
</country>
<region>
<li>Provence-Alpes-Côte d'Azur</li>
</region>
<settlement>
<li>Marseille</li>
</settlement>
</list>
<tree>
<country name="France">
<region name="Provence-Alpes-Côte d'Azur">
<name sortKey="Granel, Brigitte" sort="Granel, Brigitte" uniqKey="Granel B" first="Brigitte" last="Granel">Brigitte Granel</name>
</region>
<name sortKey="Champsaur, Pierre" sort="Champsaur, Pierre" uniqKey="Champsaur P" first="Pierre" last="Champsaur">Pierre Champsaur</name>
<name sortKey="Champsaur, Pierre" sort="Champsaur, Pierre" uniqKey="Champsaur P" first="Pierre" last="Champsaur">Pierre Champsaur</name>
<name sortKey="Disdier, Patrick" sort="Disdier, Patrick" uniqKey="Disdier P" first="Patrick" last="Disdier">Patrick Disdier</name>
<name sortKey="Juhan, Valerie" sort="Juhan, Valerie" uniqKey="Juhan V" first="Valérie" last="Juhan">Valérie Juhan</name>
<name sortKey="Pache, Xavier" sort="Pache, Xavier" uniqKey="Pache X" first="Xavier" last="Pache">Xavier Pache</name>
<name sortKey="Serratrice, Jacques" sort="Serratrice, Jacques" uniqKey="Serratrice J" first="Jacques" last="Serratrice">Jacques Serratrice</name>
<name sortKey="Swiader, Laure" sort="Swiader, Laure" uniqKey="Swiader L" first="Laure" last="Swiader">Laure Swiader</name>
<name sortKey="Weiller Merli, Claude" sort="Weiller Merli, Claude" uniqKey="Weiller Merli C" first="Claude" last="Weiller-Merli">Claude Weiller-Merli</name>
<name sortKey="Weiller, Pierre Jean" sort="Weiller, Pierre Jean" uniqKey="Weiller P" first="Pierre-Jean" last="Weiller">Pierre-Jean Weiller</name>
</country>
</tree>
</affiliations>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/PascalFrancis/Checkpoint
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000817 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/PascalFrancis/Checkpoint/biblio.hfd -nk 000817 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Sante
   |area=    LymphedemaV1
   |flux=    PascalFrancis
   |étape=   Checkpoint
   |type=    RBID
   |clé=     Pascal:01-0378023
   |texte=   Severe lower limbs lymphedema of late onset revealing polysplenia syndrome : A case report
}}

Wicri

This area was generated with Dilib version V0.6.31.
Data generation: Sat Nov 4 17:40:35 2017. Site generation: Tue Feb 13 16:42:16 2024