LymphedemaV1, Ncbi, Merge, bibRecord, 001A53

[Limb lymphedema as a first manifestation of primary intestinal lymphangiectasia (Waldmann's disease)].

Identifieur interne : 001A53 ( Ncbi/Merge ); précédent : 001A52; suivant : 001A54

[Limb lymphedema as a first manifestation of primary intestinal lymphangiectasia (Waldmann's disease)].

Auteurs : V. Boursier [France] ; S. Vignes

Source :

Journal des maladies vasculaires [ 0398-0499 ] ; 2004.

RBID : pubmed:15229406

Descripteurs français

KwdFr :
- Adulte, Biopsie, Duodénum (anatomopathologie), Humains, Lymphangiectasie intestinale (), Lymphangiectasie intestinale (anatomopathologie), Lymphangiectasie intestinale (diagnostic), Lymphoedème (), Lymphoedème (imagerie diagnostique), Membres, Mâle, Scintigraphie.
MESH :
- anatomopathologie : Duodénum, Lymphangiectasie intestinale.
- diagnostic : Lymphangiectasie intestinale.
- imagerie diagnostique : Lymphoedème.
- Adulte, Biopsie, Humains, Lymphangiectasie intestinale, Lymphoedème, Membres, Mâle, Scintigraphie.

English descriptors

KwdEn :
- Adult, Biopsy, Duodenum (pathology), Extremities, Humans, Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnosis), Lymphangiectasis, Intestinal (pathology), Lymphedema (complications), Lymphedema (diagnostic imaging), Lymphedema (therapy), Male, Radionuclide Imaging.
MESH :
- complications : Lymphangiectasis, Intestinal, Lymphedema.
- diagnosis : Lymphangiectasis, Intestinal.
- diagnostic imaging : Lymphedema.
- pathology : Duodenum, Lymphangiectasis, Intestinal.
- therapy : Lymphedema.
- Adult, Biopsy, Extremities, Humans, Male, Radionuclide Imaging.

Abstract

Primary intestinal lymphangiectasia (Waldmann's disease) is characterized by protein-losing enteropathy occurring more frequently in childhood. Chronic diarrhea and diffuse edema are the main clinical manifestations. Peripheral lymphedema may also be associated. Lymphedema is usually present at the time of diagnosis or appears later in the course of the disease. We report the observation of a 31-year-old man suffering from an upper, lower limb and genital lymphedema many years before diagnosis of primary intestinal lymphangiectasia was established. Lower limb lymphoscintigraphy confirmed lymphedema and duodenal biopsies lymphangiectasia. Hypoproteinemia, lymphopenia and hypogammaglobulinemia were also noted. Treatment of lymphedema included low stretch bandaging and elastic stocking. No dietary management with a low-fat diet was added. Search for primary intestinal lymphangiectasia with biological parameters would be useful when primary lymphedema is present. Especially since primary intestinal lymphangiectasia may be complicated by occurrence of B cell lymphoma.

PubMed: 15229406

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Le document en format XML

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<front><div type="abstract" xml:lang="en">Primary intestinal lymphangiectasia (Waldmann's disease) is characterized by protein-losing enteropathy occurring more frequently in childhood. Chronic diarrhea and diffuse edema are the main clinical manifestations. Peripheral lymphedema may also be associated. Lymphedema is usually present at the time of diagnosis or appears later in the course of the disease. We report the observation of a 31-year-old man suffering from an upper, lower limb and genital lymphedema many years before diagnosis of primary intestinal lymphangiectasia was established. Lower limb lymphoscintigraphy confirmed lymphedema and duodenal biopsies lymphangiectasia. Hypoproteinemia, lymphopenia and hypogammaglobulinemia were also noted. Treatment of lymphedema included low stretch bandaging and elastic stocking. No dietary management with a low-fat diet was added. Search for primary intestinal lymphangiectasia with biological parameters would be useful when primary lymphedema is present. Especially since primary intestinal lymphangiectasia may be complicated by occurrence of B cell lymphoma.</div>
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[Limb lymphedema as a first manifestation of primary intestinal lymphangiectasia (Waldmann's disease)].

[Limb lymphedema as a first manifestation of primary intestinal lymphangiectasia (Waldmann's disease)].

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

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