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Idiopathic retroperitoneal fibrosis.

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Idiopathic retroperitoneal fibrosis.

Auteurs : Y. Sakai ; T. Nasu

Source :

RBID : pubmed:998244

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English descriptors

Abstract

This report presents the first autopsy case in Japan of idiopathic retroperitoneal fibrosis which had developed in a 71-year-old man. The clinical course was of extremely long duration of more than 10 years. Malignancy was suspected on biopsy, and at one stage chylous ascites developed. The cause of this retroperitoneal fibrosis could not be determined, but it is considered that the vicious circle of inflammatory processes such as cellulitis and lymphangitis in the retroperitoneum and lymphedema as well as lymphorrhage attributable to mechanical lymphatic obstruction brought about the retroperitoneal fibrosis.

PubMed: 998244

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pubmed:998244

Le document en format XML

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<title level="j">Acta pathologica japonica</title>
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<term>Aged</term>
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<term>Chylous Ascites (complications)</term>
<term>Humans</term>
<term>Inflammation (complications)</term>
<term>Kidney (pathology)</term>
<term>Lymphocytes (pathology)</term>
<term>Male</term>
<term>Middle Aged</term>
<term>Retroperitoneal Fibrosis (complications)</term>
<term>Retroperitoneal Fibrosis (etiology)</term>
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<term>Adulte d'âge moyen</term>
<term>Ascite chyleuse ()</term>
<term>Autopsie</term>
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<term>Fibrose rétropéritonéale (anatomopathologie)</term>
<term>Fibrose rétropéritonéale (étiologie)</term>
<term>Humains</term>
<term>Inflammation ()</term>
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<term>Fibrose rétropéritonéale</term>
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<term>Chylous Ascites</term>
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<term>Retroperitoneal Fibrosis</term>
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<term>Kidney</term>
<term>Lymphocytes</term>
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<term>Fibrose rétropéritonéale</term>
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<term>Adulte d'âge moyen</term>
<term>Ascite chyleuse</term>
<term>Autopsie</term>
<term>Fibrose rétropéritonéale</term>
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<div type="abstract" xml:lang="en">This report presents the first autopsy case in Japan of idiopathic retroperitoneal fibrosis which had developed in a 71-year-old man. The clinical course was of extremely long duration of more than 10 years. Malignancy was suspected on biopsy, and at one stage chylous ascites developed. The cause of this retroperitoneal fibrosis could not be determined, but it is considered that the vicious circle of inflammatory processes such as cellulitis and lymphangitis in the retroperitoneum and lymphedema as well as lymphorrhage attributable to mechanical lymphatic obstruction brought about the retroperitoneal fibrosis.</div>
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