LymphedemaV1, Ncbi, Curation, bibRecord, 007714

Lymphangiosarcoma in chronic hereditary oedema (Milroy's disease).

Identifieur interne : 007714 ( Ncbi/Curation ); précédent : 007713; suivant : 007715

Lymphangiosarcoma in chronic hereditary oedema (Milroy's disease).

Auteurs : L A Broström [Suède] ; U. Nilsonne ; M. Kronberg ; G. Söderberg

Source :

Annales chirurgiae et gynaecologiae [ 0355-9521 ] ; 1989.

RBID : pubmed:2624407

Descripteurs français

KwdFr :
- Adulte, Bras, Enfant, Femelle, Humains, Jambe, Lymphangiosarcome (), Lymphoedème (), Tumeurs des tissus mous ().
MESH :
- Adulte, Bras, Enfant, Femelle, Humains, Jambe, Lymphangiosarcome, Lymphoedème, Tumeurs des tissus mous.

English descriptors

KwdEn :
- Adult, Arm, Child, Female, Humans, Leg, Lymphangiosarcoma (complications), Lymphedema (complications), Lymphedema (congenital), Soft Tissue Neoplasms (complications).
MESH :
- complications : Lymphangiosarcoma, Lymphedema, Soft Tissue Neoplasms.
- congenital : Lymphedema.
- Adult, Arm, Child, Female, Humans, Leg.

Abstract

Lymphangiosarcoma arising in chronic lymphoedema is extremely rare. In a reference population of about four million people, during a thirty year period (1957-1987), only four patients were treated for such a tumour. The neoplasm is almost exclusively seen in elderly patients after mastectomy but in two of our patients, reported in this paper, it arose in chronic hereditary oedema (Milroy's disease). In both these patients there was a considerable treatment delay because of wrong diagnosis. The tumour extent was difficult to assess macroscopically and ablative surgery had to be a disarticulation of the involved extremity. Macular or papular purple lesions in a lymphoedematous extremity should be a manifestation of this aggressive neoplasm.

PubMed: 2624407

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pubmed:2624407

Le document en format XML

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<author><name sortKey="Brostrom, L A" sort="Brostrom, L A" uniqKey="Brostrom L" first="L A" last="Broström">L A Broström</name>
<affiliation wicri:level="3"><nlm:affiliation>Department of Orthopaedics, Karolinska Hospital and Institute, Stockholm, Sweden.</nlm:affiliation>
<country xml:lang="fr">Suède</country>
<wicri:regionArea>Department of Orthopaedics, Karolinska Hospital and Institute, Stockholm</wicri:regionArea>
<placeName><settlement type="city">Stockholm</settlement>
<region nuts="2">Svealand</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Nilsonne, U" sort="Nilsonne, U" uniqKey="Nilsonne U" first="U" last="Nilsonne">U. Nilsonne</name>
</author>
<author><name sortKey="Kronberg, M" sort="Kronberg, M" uniqKey="Kronberg M" first="M" last="Kronberg">M. Kronberg</name>
</author>
<author><name sortKey="Soderberg, G" sort="Soderberg, G" uniqKey="Soderberg G" first="G" last="Söderberg">G. Söderberg</name>
</author>
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<sourceDesc><biblStruct><analytic><title xml:lang="en">Lymphangiosarcoma in chronic hereditary oedema (Milroy's disease).</title>
<author><name sortKey="Brostrom, L A" sort="Brostrom, L A" uniqKey="Brostrom L" first="L A" last="Broström">L A Broström</name>
<affiliation wicri:level="3"><nlm:affiliation>Department of Orthopaedics, Karolinska Hospital and Institute, Stockholm, Sweden.</nlm:affiliation>
<country xml:lang="fr">Suède</country>
<wicri:regionArea>Department of Orthopaedics, Karolinska Hospital and Institute, Stockholm</wicri:regionArea>
<placeName><settlement type="city">Stockholm</settlement>
<region nuts="2">Svealand</region>
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<author><name sortKey="Nilsonne, U" sort="Nilsonne, U" uniqKey="Nilsonne U" first="U" last="Nilsonne">U. Nilsonne</name>
</author>
<author><name sortKey="Kronberg, M" sort="Kronberg, M" uniqKey="Kronberg M" first="M" last="Kronberg">M. Kronberg</name>
</author>
<author><name sortKey="Soderberg, G" sort="Soderberg, G" uniqKey="Soderberg G" first="G" last="Söderberg">G. Söderberg</name>
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<series><title level="j">Annales chirurgiae et gynaecologiae</title>
<idno type="ISSN">0355-9521</idno>
<imprint><date when="1989" type="published">1989</date>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Adult</term>
<term>Arm</term>
<term>Child</term>
<term>Female</term>
<term>Humans</term>
<term>Leg</term>
<term>Lymphangiosarcoma (complications)</term>
<term>Lymphedema (complications)</term>
<term>Lymphedema (congenital)</term>
<term>Soft Tissue Neoplasms (complications)</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr"><term>Adulte</term>
<term>Bras</term>
<term>Enfant</term>
<term>Femelle</term>
<term>Humains</term>
<term>Jambe</term>
<term>Lymphangiosarcome ()</term>
<term>Lymphoedème ()</term>
<term>Tumeurs des tissus mous ()</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiosarcoma</term>
<term>Lymphedema</term>
<term>Soft Tissue Neoplasms</term>
</keywords>
<keywords scheme="MESH" qualifier="congenital" xml:lang="en"><term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Arm</term>
<term>Child</term>
<term>Female</term>
<term>Humans</term>
<term>Leg</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr"><term>Adulte</term>
<term>Bras</term>
<term>Enfant</term>
<term>Femelle</term>
<term>Humains</term>
<term>Jambe</term>
<term>Lymphangiosarcome</term>
<term>Lymphoedème</term>
<term>Tumeurs des tissus mous</term>
</keywords>
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</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Lymphangiosarcoma arising in chronic lymphoedema is extremely rare. In a reference population of about four million people, during a thirty year period (1957-1987), only four patients were treated for such a tumour. The neoplasm is almost exclusively seen in elderly patients after mastectomy but in two of our patients, reported in this paper, it arose in chronic hereditary oedema (Milroy's disease). In both these patients there was a considerable treatment delay because of wrong diagnosis. The tumour extent was difficult to assess macroscopically and ablative surgery had to be a disarticulation of the involved extremity. Macular or papular purple lesions in a lymphoedematous extremity should be a manifestation of this aggressive neoplasm.</div>
</front>
</TEI>
</record>

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Lymphangiosarcoma in chronic hereditary oedema (Milroy's disease).

Lymphangiosarcoma in chronic hereditary oedema (Milroy's disease).

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

Pour générer des pages wiki