LymphedemaV1, Ncbi, Checkpoint, bibRecord, 009B75

Chronic lymphangiectasis in Turner's syndrome.

Identifieur interne : 009B75 ( Ncbi/Checkpoint ); précédent : 009B74; suivant : 009B76

Chronic lymphangiectasis in Turner's syndrome.

Auteurs : H D Perry ; A J Cossari

Source :

The British Journal of Ophthalmology [ 0007-1161 ] ; 1986.

RBID : PMC:1041022

Descripteurs français

KwdFr :
- Conjonctive (anatomopathologie), Enfant d'âge préscolaire, Femelle, Humains, Lymphangiectasie (), Lymphoedème (), Lymphoedème (anatomopathologie), Syndrome de Turner (), Système lymphatique (anatomopathologie), Tissu conjonctif (anatomopathologie).
MESH :
- anatomopathologie : Conjonctive, Lymphoedème, Système lymphatique, Tissu conjonctif.
- Enfant d'âge préscolaire, Femelle, Humains, Lymphangiectasie, Lymphoedème, Syndrome de Turner.

English descriptors

KwdEn :
- Child, Preschool, Conjunctiva (pathology), Connective Tissue (pathology), Female, Humans, Lymphangiectasis (complications), Lymphatic System (pathology), Lymphedema (complications), Lymphedema (congenital), Lymphedema (pathology), Turner Syndrome (complications).
MESH :
- complications : Lymphangiectasis, Lymphedema, Turner Syndrome.
- congenital : Lymphedema.
- pathology : Conjunctiva, Connective Tissue, Lymphatic System, Lymphedema.
- Child, Preschool, Female, Humans.

Abstract

A 3 1/2-year-old female presented with Turner's syndrome and Nonne-Milroy-Meige disease. Ocular findings included strabismus and bilateral chemosis which was unchanging and persisted throughout the four years the patient was followed up. Histopathological findings included diffuse lymphangiectasia and dense connective tissue surrounding the dilated lymph channels. Although the association between congenital lymphoedema and Turner's syndrome is common, the lymphoedema usually disappears by the first year of life. The persistence of the lymphoedema beyond this age is rare, as is the presence of the persistent chemosis. This report represents the first histopathological documentation of congenital lymphangiectasis in association with Turner's syndrome.

Images

Url:

http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1041022

PubMed: 3964640
PubMed Central: 1041022

Affiliations:

Links to Exploration step

PMC:1041022

Le document en format XML

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<term>Humans</term>
<term>Lymphangiectasis (complications)</term>
<term>Lymphatic System (pathology)</term>
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<term>Lymphangiectasie ()</term>
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<term>Lymphoedème</term>
<term>Système lymphatique</term>
<term>Tissu conjonctif</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiectasis</term>
<term>Lymphedema</term>
<term>Turner Syndrome</term>
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<keywords scheme="MESH" qualifier="congenital" xml:lang="en"><term>Lymphedema</term>
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<term>Lymphatic System</term>
<term>Lymphedema</term>
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<front><div type="abstract" xml:lang="en"><p>A 3 1/2-year-old female presented with Turner's syndrome and Nonne-Milroy-Meige disease. Ocular findings included strabismus and bilateral chemosis which was unchanging and persisted throughout the four years the patient was followed up. Histopathological findings included diffuse lymphangiectasia and dense connective tissue surrounding the dilated lymph channels. Although the association between congenital lymphoedema and Turner's syndrome is common, the lymphoedema usually disappears by the first year of life. The persistence of the lymphoedema beyond this age is rare, as is the presence of the persistent chemosis. This report represents the first histopathological documentation of congenital lymphangiectasis in association with Turner's syndrome.</p>
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Serveur d'exploration sur le lymphœdème

Chronic lymphangiectasis in Turner's syndrome.

Chronic lymphangiectasis in Turner's syndrome.

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

Pour générer des pages wiki

	Serveur d'exploration sur le lymphœdème
	Attention, ce site est en cours de développement ! Attention, site généré par des moyens informatiques à partir de corpus bruts. Les informations ne sont donc pas validées.