Cutaneous angiosarcoma: report of three different and typical cases admitted in a unique dermatology clinic*
Identifieur interne : 009118 ( Ncbi/Checkpoint ); précédent : 009117; suivant : 009119Cutaneous angiosarcoma: report of three different and typical cases admitted in a unique dermatology clinic*
Auteurs : Aline Neves Freitas Cabral [Brésil] ; Rafael Henrique Rocha [Brésil] ; Ana Cristina Vervloet Do Amaral [Brésil] ; Karina Bittencourt Medeiros [Brésil] ; Paulo Sérgio Emerich Nogueira [Brésil] ; Lucia Martins Diniz [Brésil]Source :
- Anais Brasileiros de Dermatologia [ 0365-0596 ] ; 2017.
Abstract
Angiosarcoma is a rare and aggressive tumor with high rates of metastasis and relapse. It shows a particular predilection for the skin and superficial soft tissues. We report three distinct and typical cases of angiosarcoma that were diagnosed in a single dermatology clinic over the course of less than a year: i) Angiosarcoma in lower limb affected by chronic lymphedema, featuring Stewart-Treves syndrome; ii) a case of the most common type of angiosarcoma loated in the scalp and face of elderly man and; iii) a skin Angiosarcoma in previously irradiated breast. All lesions presented characteristic histopathological findings: irregular vascular proliferation that dissects the collagen bundles with atypical endothelial nuclei projection toward the lumen.
Url:
DOI: 10.1590/abd1806-4841.20175326
PubMed: 28538886
PubMed Central: 5429112
Affiliations:
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PMC:5429112Le document en format XML
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<front><div type="abstract" xml:lang="en"><p>Angiosarcoma is a rare and aggressive tumor with high rates of metastasis and
relapse. It shows a particular predilection for the skin and superficial soft
tissues. We report three distinct and typical cases of angiosarcoma that were
diagnosed in a single dermatology clinic over the course of less than a year: i)
Angiosarcoma in lower limb affected by chronic lymphedema, featuring
Stewart-Treves syndrome; ii) a case of the most common type of angiosarcoma
loated in the scalp and face of elderly man and; iii) a skin Angiosarcoma in
previously irradiated breast. All lesions presented characteristic
histopathological findings: irregular vascular proliferation that dissects the
collagen bundles with atypical endothelial nuclei projection toward the
lumen.</p>
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