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Angiosarcoma Arising in an Ovarian Fibroma: A Case Report

Identifieur interne : 004010 ( Ncbi/Checkpoint ); précédent : 004009; suivant : 004011

Angiosarcoma Arising in an Ovarian Fibroma: A Case Report

Auteurs : Eduardo Cambruzzi [Brésil] ; Karla Lais Pegas [Brésil] ; Daniel Marini Milani [Brésil] ; Ricardo Pedrini Cruz [Brésil] ; Enilde Heloena Guerra [Brésil] ; Márcio Balbinotti Ferrari [Brésil]

Source :

RBID : PMC:2989701

Abstract

Primary ovarian angiosarcoma is a very rare gynaecological sarcoma, with poor prognosis. These tumors are though to arise from carcinosarcomas, teratomas, or the ovarian vasculature and occur at any age. There are only a few cases reported in the international literature, most commonly associated to surface epithelial-stromal or germ cell tumours. Herein, the authors report the clinicopathologic features of an angiosarcoma arising in an ovarian fibroma. A 65-year-old patient was admitted with a palpable mass in the hypogastrium. Grossly, the removed ovary was completely replaced by a solid tumor mass. On histological analysis, the lesion revealed the typical histological features of angiosarcoma with sinusoidal patterns and anaplastic cells, admixed with spindle-shaped cells arranged in fascicles or in a storiform pattern, compatible with a fibroma. The vascular component was strongly immunopositive for CD31 and CD34. The patient was submitted to chemotherapy, and she was alive for two months after surgical proceedings.


Url:
DOI: 10.4061/2010/842592
PubMed: 21151524
PubMed Central: 2989701


Affiliations:


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PMC:2989701

Le document en format XML

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<p>Primary ovarian angiosarcoma is a very rare gynaecological sarcoma, with poor prognosis. These tumors are though to arise from carcinosarcomas, teratomas, or the ovarian vasculature and occur at any age. There are only a few cases reported in the international literature, most commonly associated to surface epithelial-stromal or germ cell tumours. Herein, the authors report the clinicopathologic features of an angiosarcoma arising in an ovarian fibroma. A 65-year-old patient was admitted with a palpable mass in the hypogastrium. Grossly, the removed ovary was completely replaced by a solid tumor mass. On histological analysis, the lesion revealed the typical histological features of angiosarcoma with sinusoidal patterns and anaplastic cells, admixed with spindle-shaped cells arranged in fascicles or in a storiform pattern, compatible with a fibroma. The vascular component was strongly immunopositive for CD31 and CD34. The patient was submitted to chemotherapy, and she was alive for two months after surgical proceedings.</p>
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