Angiosarcoma Arising in an Ovarian Fibroma: A Case Report
Identifieur interne : 004010 ( Ncbi/Checkpoint ); précédent : 004009; suivant : 004011Angiosarcoma Arising in an Ovarian Fibroma: A Case Report
Auteurs : Eduardo Cambruzzi [Brésil] ; Karla Lais Pegas [Brésil] ; Daniel Marini Milani [Brésil] ; Ricardo Pedrini Cruz [Brésil] ; Enilde Heloena Guerra [Brésil] ; Márcio Balbinotti Ferrari [Brésil]Source :
- Pathology Research International [ 2090-8091 ] ; 2010.
Abstract
Primary ovarian angiosarcoma is a very rare gynaecological sarcoma, with poor prognosis. These tumors are though to arise from carcinosarcomas, teratomas, or the ovarian vasculature and occur at any age. There are only a few cases reported in the international literature, most commonly associated to surface epithelial-stromal or germ cell tumours. Herein, the authors report the clinicopathologic features of an angiosarcoma arising in an ovarian fibroma. A 65-year-old patient was admitted with a palpable mass in the hypogastrium. Grossly, the removed ovary was completely replaced by a solid tumor mass. On histological analysis, the lesion revealed the typical histological features of angiosarcoma with sinusoidal patterns and anaplastic cells, admixed with spindle-shaped cells arranged in fascicles or in a storiform pattern, compatible with a fibroma. The vascular component was strongly immunopositive for CD31 and CD34. The patient was submitted to chemotherapy, and she was alive for two months after surgical proceedings.
Url:
DOI: 10.4061/2010/842592
PubMed: 21151524
PubMed Central: 2989701
Affiliations:
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<front><div type="abstract" xml:lang="en"><p>Primary ovarian angiosarcoma is a very rare gynaecological sarcoma, with poor prognosis. These tumors are though to arise from carcinosarcomas, teratomas, or the ovarian vasculature and occur at any age. There are only a few cases reported in the international literature, most commonly associated to surface epithelial-stromal or germ cell tumours. Herein, the authors report the clinicopathologic features of an angiosarcoma arising in an ovarian fibroma. A 65-year-old patient was admitted with a palpable mass in the hypogastrium. Grossly, the removed ovary was completely replaced by a solid tumor mass. On histological analysis, the lesion revealed the typical histological features of angiosarcoma with sinusoidal patterns and anaplastic cells, admixed with spindle-shaped cells arranged in fascicles or in a storiform pattern, compatible with a fibroma. The vascular component was strongly immunopositive for CD31 and CD34. The patient was submitted to chemotherapy, and she was alive for two months after surgical proceedings.</p>
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</author>
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<author><name sortKey="Prat, J" uniqKey="Prat J">J Prat</name>
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</author>
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</author>
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<author><name sortKey="Lifschitz Mercer, B" uniqKey="Lifschitz Mercer B">B Lifschitz-Mercer</name>
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