Serveur d'exploration sur le lymphœdème

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

Intestinal lymphangiectasia and reversible high liver stiffness.

Identifieur interne : 002974 ( Main/Merge ); précédent : 002973; suivant : 002975

Intestinal lymphangiectasia and reversible high liver stiffness.

Auteurs : Laura Milazzo [Italie] ; Anna Maria Peri ; Lucia Lodi ; Guido Gubertini ; Anna Lisa Ridolfo ; Spinello Antinori

Source :

RBID : pubmed:24449480

Descripteurs français

English descriptors

Abstract

Primary intestinal lymphangiectasia (PIL) is a protein-losing enteropathy characterized by tortuous and dilated lymph channels of the small bowel. The main symptoms are bilateral lower limb edema, serosal effusions, and vitamin D malabsorption resulting in osteoporosis. We report here a case of long-lasting misdiagnosed PIL with a peculiar liver picture, characterized by a very high stiffness value at transient elastography, which decreased with clinical improvement. The complex interplay between lymphatic and hepatic circulatory system is discussed.

DOI: 10.1002/hep.27025
PubMed: 24449480

Links toward previous steps (curation, corpus...)


Links to Exploration step

pubmed:24449480

Le document en format XML

<record>
<TEI>
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en">Intestinal lymphangiectasia and reversible high liver stiffness.</title>
<author>
<name sortKey="Milazzo, Laura" sort="Milazzo, Laura" uniqKey="Milazzo L" first="Laura" last="Milazzo">Laura Milazzo</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Milan, Italy.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Peri, Anna Maria" sort="Peri, Anna Maria" uniqKey="Peri A" first="Anna Maria" last="Peri">Anna Maria Peri</name>
</author>
<author>
<name sortKey="Lodi, Lucia" sort="Lodi, Lucia" uniqKey="Lodi L" first="Lucia" last="Lodi">Lucia Lodi</name>
</author>
<author>
<name sortKey="Gubertini, Guido" sort="Gubertini, Guido" uniqKey="Gubertini G" first="Guido" last="Gubertini">Guido Gubertini</name>
</author>
<author>
<name sortKey="Ridolfo, Anna Lisa" sort="Ridolfo, Anna Lisa" uniqKey="Ridolfo A" first="Anna Lisa" last="Ridolfo">Anna Lisa Ridolfo</name>
</author>
<author>
<name sortKey="Antinori, Spinello" sort="Antinori, Spinello" uniqKey="Antinori S" first="Spinello" last="Antinori">Spinello Antinori</name>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">PubMed</idno>
<date when="2014">2014</date>
<idno type="RBID">pubmed:24449480</idno>
<idno type="pmid">24449480</idno>
<idno type="doi">10.1002/hep.27025</idno>
<idno type="wicri:Area/PubMed/Corpus">001718</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">001718</idno>
<idno type="wicri:Area/PubMed/Curation">001718</idno>
<idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Curation">001718</idno>
<idno type="wicri:Area/PubMed/Checkpoint">001718</idno>
<idno type="wicri:explorRef" wicri:stream="Checkpoint" wicri:step="PubMed">001718</idno>
<idno type="wicri:Area/Ncbi/Merge">006201</idno>
<idno type="wicri:Area/Ncbi/Curation">006201</idno>
<idno type="wicri:Area/Ncbi/Checkpoint">006201</idno>
<idno type="wicri:Area/Main/Merge">002974</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title xml:lang="en">Intestinal lymphangiectasia and reversible high liver stiffness.</title>
<author>
<name sortKey="Milazzo, Laura" sort="Milazzo, Laura" uniqKey="Milazzo L" first="Laura" last="Milazzo">Laura Milazzo</name>
<affiliation wicri:level="3">
<nlm:affiliation>Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Milan, Italy.</nlm:affiliation>
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Peri, Anna Maria" sort="Peri, Anna Maria" uniqKey="Peri A" first="Anna Maria" last="Peri">Anna Maria Peri</name>
</author>
<author>
<name sortKey="Lodi, Lucia" sort="Lodi, Lucia" uniqKey="Lodi L" first="Lucia" last="Lodi">Lucia Lodi</name>
</author>
<author>
<name sortKey="Gubertini, Guido" sort="Gubertini, Guido" uniqKey="Gubertini G" first="Guido" last="Gubertini">Guido Gubertini</name>
</author>
<author>
<name sortKey="Ridolfo, Anna Lisa" sort="Ridolfo, Anna Lisa" uniqKey="Ridolfo A" first="Anna Lisa" last="Ridolfo">Anna Lisa Ridolfo</name>
</author>
<author>
<name sortKey="Antinori, Spinello" sort="Antinori, Spinello" uniqKey="Antinori S" first="Spinello" last="Antinori">Spinello Antinori</name>
</author>
</analytic>
<series>
<title level="j">Hepatology (Baltimore, Md.)</title>
<idno type="eISSN">1527-3350</idno>
<imprint>
<date when="2014" type="published">2014</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="KwdEn" xml:lang="en">
<term>Elasticity Imaging Techniques (methods)</term>
<term>Female</term>
<term>Humans</term>
<term>Liver (pathology)</term>
<term>Liver (physiopathology)</term>
<term>Liver Circulation (physiology)</term>
<term>Lymphangiectasis, Intestinal (pathology)</term>
<term>Lymphangiectasis, Intestinal (physiopathology)</term>
<term>Lymphatic Vessels (physiology)</term>
<term>Lymphedema (pathology)</term>
<term>Lymphedema (physiopathology)</term>
<term>Middle Aged</term>
</keywords>
<keywords scheme="KwdFr" xml:lang="fr">
<term>Adulte d'âge moyen</term>
<term>Circulation hépatique (physiologie)</term>
<term>Femelle</term>
<term>Foie (anatomopathologie)</term>
<term>Foie (physiopathologie)</term>
<term>Humains</term>
<term>Imagerie d'élasticité tissulaire ()</term>
<term>Lymphangiectasie intestinale (anatomopathologie)</term>
<term>Lymphangiectasie intestinale (physiopathologie)</term>
<term>Lymphoedème (anatomopathologie)</term>
<term>Lymphoedème (physiopathologie)</term>
<term>Vaisseaux lymphatiques (physiologie)</term>
</keywords>
<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr">
<term>Foie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" qualifier="methods" xml:lang="en">
<term>Elasticity Imaging Techniques</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en">
<term>Liver</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="physiologie" xml:lang="fr">
<term>Circulation hépatique</term>
<term>Vaisseaux lymphatiques</term>
</keywords>
<keywords scheme="MESH" qualifier="physiology" xml:lang="en">
<term>Liver Circulation</term>
<term>Lymphatic Vessels</term>
</keywords>
<keywords scheme="MESH" qualifier="physiopathologie" xml:lang="fr">
<term>Foie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" qualifier="physiopathology" xml:lang="en">
<term>Liver</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Female</term>
<term>Humans</term>
<term>Middle Aged</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr">
<term>Adulte d'âge moyen</term>
<term>Femelle</term>
<term>Humains</term>
<term>Imagerie d'élasticité tissulaire</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">Primary intestinal lymphangiectasia (PIL) is a protein-losing enteropathy characterized by tortuous and dilated lymph channels of the small bowel. The main symptoms are bilateral lower limb edema, serosal effusions, and vitamin D malabsorption resulting in osteoporosis. We report here a case of long-lasting misdiagnosed PIL with a peculiar liver picture, characterized by a very high stiffness value at transient elastography, which decreased with clinical improvement. The complex interplay between lymphatic and hepatic circulatory system is discussed.</div>
</front>
</TEI>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Sante/explor/LymphedemaV1/Data/Main/Merge
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 002974 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/Main/Merge/biblio.hfd -nk 002974 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Sante
   |area=    LymphedemaV1
   |flux=    Main
   |étape=   Merge
   |type=    RBID
   |clé=     pubmed:24449480
   |texte=   Intestinal lymphangiectasia and reversible high liver stiffness.
}}

Pour générer des pages wiki

HfdIndexSelect -h $EXPLOR_AREA/Data/Main/Merge/RBID.i   -Sk "pubmed:24449480" \
       | HfdSelect -Kh $EXPLOR_AREA/Data/Main/Merge/biblio.hfd   \
       | NlmPubMed2Wicri -a LymphedemaV1 

Wicri

This area was generated with Dilib version V0.6.31.
Data generation: Sat Nov 4 17:40:35 2017. Site generation: Tue Feb 13 16:42:16 2024