Therapeutic Effect of Sirolimus for Lymphangioleiomyomatosis Remaining in the Abdominopelvic Region After Lung Transplantation: A Case Report.
Identifieur interne : 012909 ( Main/Exploration ); précédent : 012908; suivant : 012910Therapeutic Effect of Sirolimus for Lymphangioleiomyomatosis Remaining in the Abdominopelvic Region After Lung Transplantation: A Case Report.
Auteurs : T. Ito [Japon] ; M. Suno [Japon] ; K. Sakamoto [Japon] ; Y. Yoshizaki [Japon] ; K. Yamamoto [Japon] ; R. Nakanishi [Japon] ; Y. Hirano [Japon] ; M. Irie [Japon] ; T. Kurosaki [Japon] ; S. Otani [Japon] ; M. Yamane [Japon] ; S. Sugimoto [Japon] ; K. Miyoshi [Japon] ; T. Oto [Japon]Source :
- Transplantation proceedings [ 1873-2623 ]
Descripteurs français
- KwdFr :
- Abdomen (anatomopathologie), Acide mycophénolique (analogues et dérivés), Acide mycophénolique (usage thérapeutique), Adulte, Femelle, Humains, Immunosuppresseurs (usage thérapeutique), Immunosuppression thérapeutique (), Lymphangioléiomyomatose (), Lymphangioléiomyomatose (anatomopathologie), Lymphangioléiomyomatose (traitement médicamenteux), Lymphoedème (traitement médicamenteux), Lymphoedème (étiologie), Maladie résiduelle, Pelvis (anatomopathologie), Prednisolone (usage thérapeutique), Qualité de vie, Sirolimus (usage thérapeutique), Tacrolimus (usage thérapeutique), Transplantation pulmonaire, Tumeurs du poumon (anatomopathologie), Tumeurs du poumon (traitement médicamenteux).
- MESH :
- analogues et dérivés : Acide mycophénolique.
- anatomopathologie : Abdomen, Lymphangioléiomyomatose, Pelvis, Tumeurs du poumon.
- traitement médicamenteux : Lymphangioléiomyomatose, Lymphoedème, Tumeurs du poumon.
- usage thérapeutique : Acide mycophénolique, Immunosuppresseurs, Prednisolone, Sirolimus, Tacrolimus.
- étiologie : Lymphoedème.
- Adulte, Femelle, Humains, Immunosuppression thérapeutique, Lymphangioléiomyomatose, Maladie résiduelle, Qualité de vie, Transplantation pulmonaire.
English descriptors
- KwdEn :
- Abdomen (pathology), Adult, Female, Humans, Immunosuppression (methods), Immunosuppressive Agents (therapeutic use), Lung Neoplasms (drug therapy), Lung Neoplasms (pathology), Lung Transplantation, Lymphangioleiomyomatosis (drug therapy), Lymphangioleiomyomatosis (pathology), Lymphangioleiomyomatosis (surgery), Lymphedema (drug therapy), Lymphedema (etiology), Mycophenolic Acid (analogs & derivatives), Mycophenolic Acid (therapeutic use), Neoplasm, Residual, Pelvis (pathology), Prednisolone (therapeutic use), Quality of Life, Sirolimus (therapeutic use), Tacrolimus (therapeutic use).
- MESH :
- chemical , analogs & derivatives : Mycophenolic Acid.
- chemical , therapeutic use : Immunosuppressive Agents, Mycophenolic Acid, Prednisolone, Sirolimus, Tacrolimus.
- drug therapy : Lung Neoplasms, Lymphangioleiomyomatosis, Lymphedema.
- etiology : Lymphedema.
- methods : Immunosuppression.
- pathology : Abdomen, Lung Neoplasms, Lymphangioleiomyomatosis, Pelvis.
- surgery : Lymphangioleiomyomatosis.
- Adult, Female, Humans, Lung Transplantation, Neoplasm, Residual, Quality of Life.
Abstract
Sirolimus (SRL) is used to treat pulmonary lymphangioleiomyomatosis (P-LAM). There is limited evidence that SRL has systemic efficacy for the patients with extrapulmonary lymphangioleiomyomatosis (E-LAM) remaining after lung transplantation (LT) for P-LAM. This report examines the efficacy of SRL treatment for the patient with E-LAM remaining after an LT for P-LAM.
DOI: 10.1016/j.transproceed.2015.12.021
PubMed: 26915883
Affiliations:
Links toward previous steps (curation, corpus...)
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Le document en format XML
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<term>Mycophenolic Acid (therapeutic use)</term>
<term>Neoplasm, Residual</term>
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<term>Immunosuppression thérapeutique ()</term>
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<term>Lymphangioléiomyomatose (anatomopathologie)</term>
<term>Lymphangioléiomyomatose (traitement médicamenteux)</term>
<term>Lymphoedème (traitement médicamenteux)</term>
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<term>Prednisolone (usage thérapeutique)</term>
<term>Qualité de vie</term>
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<term>Tacrolimus (usage thérapeutique)</term>
<term>Transplantation pulmonaire</term>
<term>Tumeurs du poumon (anatomopathologie)</term>
<term>Tumeurs du poumon (traitement médicamenteux)</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="analogs & derivatives" xml:lang="en"><term>Mycophenolic Acid</term>
</keywords>
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<term>Mycophenolic Acid</term>
<term>Prednisolone</term>
<term>Sirolimus</term>
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</keywords>
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</keywords>
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<term>Lymphangioléiomyomatose</term>
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<term>Tumeurs du poumon</term>
</keywords>
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<term>Lymphedema</term>
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<term>Lung Neoplasms</term>
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<term>Pelvis</term>
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<term>Prednisolone</term>
<term>Sirolimus</term>
<term>Tacrolimus</term>
</keywords>
<keywords scheme="MESH" qualifier="étiologie" xml:lang="fr"><term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Female</term>
<term>Humans</term>
<term>Lung Transplantation</term>
<term>Neoplasm, Residual</term>
<term>Quality of Life</term>
</keywords>
<keywords scheme="MESH" xml:lang="fr"><term>Adulte</term>
<term>Femelle</term>
<term>Humains</term>
<term>Immunosuppression thérapeutique</term>
<term>Lymphangioléiomyomatose</term>
<term>Maladie résiduelle</term>
<term>Qualité de vie</term>
<term>Transplantation pulmonaire</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Sirolimus (SRL) is used to treat pulmonary lymphangioleiomyomatosis (P-LAM). There is limited evidence that SRL has systemic efficacy for the patients with extrapulmonary lymphangioleiomyomatosis (E-LAM) remaining after lung transplantation (LT) for P-LAM. This report examines the efficacy of SRL treatment for the patient with E-LAM remaining after an LT for P-LAM.</div>
</front>
</TEI>
<affiliations><list><country><li>Japon</li>
</country>
</list>
<tree><country name="Japon"><noRegion><name sortKey="Ito, T" sort="Ito, T" uniqKey="Ito T" first="T" last="Ito">T. Ito</name>
</noRegion>
<name sortKey="Hirano, Y" sort="Hirano, Y" uniqKey="Hirano Y" first="Y" last="Hirano">Y. Hirano</name>
<name sortKey="Irie, M" sort="Irie, M" uniqKey="Irie M" first="M" last="Irie">M. Irie</name>
<name sortKey="Kurosaki, T" sort="Kurosaki, T" uniqKey="Kurosaki T" first="T" last="Kurosaki">T. Kurosaki</name>
<name sortKey="Miyoshi, K" sort="Miyoshi, K" uniqKey="Miyoshi K" first="K" last="Miyoshi">K. Miyoshi</name>
<name sortKey="Nakanishi, R" sort="Nakanishi, R" uniqKey="Nakanishi R" first="R" last="Nakanishi">R. Nakanishi</name>
<name sortKey="Otani, S" sort="Otani, S" uniqKey="Otani S" first="S" last="Otani">S. Otani</name>
<name sortKey="Oto, T" sort="Oto, T" uniqKey="Oto T" first="T" last="Oto">T. Oto</name>
<name sortKey="Sakamoto, K" sort="Sakamoto, K" uniqKey="Sakamoto K" first="K" last="Sakamoto">K. Sakamoto</name>
<name sortKey="Sugimoto, S" sort="Sugimoto, S" uniqKey="Sugimoto S" first="S" last="Sugimoto">S. Sugimoto</name>
<name sortKey="Suno, M" sort="Suno, M" uniqKey="Suno M" first="M" last="Suno">M. Suno</name>
<name sortKey="Yamamoto, K" sort="Yamamoto, K" uniqKey="Yamamoto K" first="K" last="Yamamoto">K. Yamamoto</name>
<name sortKey="Yamane, M" sort="Yamane, M" uniqKey="Yamane M" first="M" last="Yamane">M. Yamane</name>
<name sortKey="Yoshizaki, Y" sort="Yoshizaki, Y" uniqKey="Yoshizaki Y" first="Y" last="Yoshizaki">Y. Yoshizaki</name>
</country>
</tree>
</affiliations>
</record>
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