Amniotic band syndrom at Bobo Dioulasso university teaching hospital (Burkina-Faso): about two cases
Identifieur interne : 002164 ( Main/Exploration ); précédent : 002163; suivant : 002165Amniotic band syndrom at Bobo Dioulasso university teaching hospital (Burkina-Faso): about two cases
Auteurs : Cyprien Zaré [Burkina Faso] ; Ibrahim Alain Traoré [Burkina Faso] ; Patrick Wendpuoiré Hamed Dakouré [Burkina Faso] ; Salif Gandéma [Burkina Faso] ; Bakary Gustave Sano [Burkina Faso] ; Lazard Bouma Bénao [Burkina Faso] ; Hermann Belemlilga [Burkina Faso] ; Nassirou Yabré [Burkina Faso]Source :
- The Pan African Medical Journal [ 1937-8688 ] ; 2015.
Descripteurs français
- KwdFr :
- Burkina, Humains, Hôpitaux universitaires, Maladie des brides amniotiques (), Maladie des brides amniotiques (anatomopathologie), Maladie des brides amniotiques (diagnostic), Mâle, Nouveau-né, Pied bot varus équin congénital (), Pied bot varus équin congénital (anatomopathologie), Pied bot varus équin congénital (étiologie), Syndactylie (), Syndactylie (anatomopathologie), Syndactylie (étiologie).
- MESH :
- anatomopathologie : Maladie des brides amniotiques, Pied bot varus équin congénital, Syndactylie.
- diagnostic : Maladie des brides amniotiques.
- étiologie : Pied bot varus équin congénital, Syndactylie.
- Burkina, Humains, Hôpitaux universitaires, Maladie des brides amniotiques, Mâle, Nouveau-né, Pied bot varus équin congénital, Syndactylie.
English descriptors
- KwdEn :
- Amniotic Band Syndrome (diagnosis), Amniotic Band Syndrome (pathology), Amniotic Band Syndrome (surgery), Burkina Faso, Clubfoot (etiology), Clubfoot (pathology), Clubfoot (surgery), Hospitals, University, Humans, Infant, Newborn, Male, Syndactyly (etiology), Syndactyly (pathology), Syndactyly (surgery).
- MESH :
- diagnosis : Amniotic Band Syndrome.
- etiology : Clubfoot, Syndactyly.
- pathology : Amniotic Band Syndrome, Clubfoot, Syndactyly.
- surgery : Amniotic Band Syndrome, Clubfoot, Syndactyly.
- Burkina Faso, Hospitals, University, Humans, Infant, Newborn, Male.
Abstract
Amniotic band syndrome is a rare congenital disorder. The authors report the first cases documented at Souro Sanou University Hospital in Bobo-Dioulasso (CHUSS) in 2 male new borns. The malformations found at birth, were worn only on limbs and were in the form of skin furrow necking with a major lymphedema downstream. In both cases, the constriction furrow at member pelvic was associated with a club foot and a pseudosyndactyly in one case. Surgical treatment consisted of a section of the constrictor ring and a Z-plasty. The functional outcome was satisfactory with the acquisition of a plantar support for both children. Through these two observations, epidemiological, diagnostic, and particularities of the management of this condition are discussed in the Burkina-Faso.
Url:
DOI: 10.11604/pamj.2015.22.187.7863
PubMed: 26918082
PubMed Central: 4752845
Affiliations:
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Le document en format XML
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<term>Amniotic Band Syndrome (pathology)</term>
<term>Amniotic Band Syndrome (surgery)</term>
<term>Burkina Faso</term>
<term>Clubfoot (etiology)</term>
<term>Clubfoot (pathology)</term>
<term>Clubfoot (surgery)</term>
<term>Hospitals, University</term>
<term>Humans</term>
<term>Infant, Newborn</term>
<term>Male</term>
<term>Syndactyly (etiology)</term>
<term>Syndactyly (pathology)</term>
<term>Syndactyly (surgery)</term>
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<term>Hôpitaux universitaires</term>
<term>Maladie des brides amniotiques ()</term>
<term>Maladie des brides amniotiques (anatomopathologie)</term>
<term>Maladie des brides amniotiques (diagnostic)</term>
<term>Mâle</term>
<term>Nouveau-né</term>
<term>Pied bot varus équin congénital ()</term>
<term>Pied bot varus équin congénital (anatomopathologie)</term>
<term>Pied bot varus équin congénital (étiologie)</term>
<term>Syndactylie ()</term>
<term>Syndactylie (anatomopathologie)</term>
<term>Syndactylie (étiologie)</term>
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<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr"><term>Maladie des brides amniotiques</term>
<term>Pied bot varus équin congénital</term>
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<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Amniotic Band Syndrome</term>
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<front><div type="abstract" xml:lang="en"><p>Amniotic band syndrome is a rare congenital disorder. The authors report the first cases documented at Souro Sanou University Hospital in Bobo-Dioulasso (CHUSS) in 2 male new borns. The malformations found at birth, were worn only on limbs and were in the form of skin furrow necking with a major lymphedema downstream. In both cases, the constriction furrow at member pelvic was associated with a club foot and a pseudosyndactyly in one case. Surgical treatment consisted of a section of the constrictor ring and a Z-plasty. The functional outcome was satisfactory with the acquisition of a plantar support for both children. Through these two observations, epidemiological, diagnostic, and particularities of the management of this condition are discussed in the Burkina-Faso.</p>
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<name sortKey="Belemlilga, Hermann" sort="Belemlilga, Hermann" uniqKey="Belemlilga H" first="Hermann" last="Belemlilga">Hermann Belemlilga</name>
<name sortKey="Benao, Lazard Bouma" sort="Benao, Lazard Bouma" uniqKey="Benao L" first="Lazard Bouma" last="Bénao">Lazard Bouma Bénao</name>
<name sortKey="Dakoure, Patrick Wendpuoire Hamed" sort="Dakoure, Patrick Wendpuoire Hamed" uniqKey="Dakoure P" first="Patrick Wendpuoiré Hamed" last="Dakouré">Patrick Wendpuoiré Hamed Dakouré</name>
<name sortKey="Gandema, Salif" sort="Gandema, Salif" uniqKey="Gandema S" first="Salif" last="Gandéma">Salif Gandéma</name>
<name sortKey="Sano, Bakary Gustave" sort="Sano, Bakary Gustave" uniqKey="Sano B" first="Bakary Gustave" last="Sano">Bakary Gustave Sano</name>
<name sortKey="Traore, Ibrahim Alain" sort="Traore, Ibrahim Alain" uniqKey="Traore I" first="Ibrahim Alain" last="Traoré">Ibrahim Alain Traoré</name>
<name sortKey="Yabre, Nassirou" sort="Yabre, Nassirou" uniqKey="Yabre N" first="Nassirou" last="Yabré">Nassirou Yabré</name>
</country>
</tree>
</affiliations>
</record>
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