LymphedemaV1, Main, Exploration, bibRecord, 001D05

How to treat an extensive form of primary intestinal lymphangiectasia?

Identifieur interne : 001D05 ( Main/Exploration ); précédent : 001D04; suivant : 001D06

How to treat an extensive form of primary intestinal lymphangiectasia?

Auteurs : Rosana Troskot ; Dragan Jur I ; Ante Bili ; Marija Gomer I Pal I ; Stanko Težak ; Ivana Brajkovi

Source :

World Journal of Gastroenterology : WJG [ 1007-9327 ] ; 2015.

RBID : PMC:4476896

Descripteurs français

KwdFr :
- Adulte, Agents gastro-intestinaux (usage thérapeutique), Agrégat d'albumine marquée au technétium (99mTc), Biopsie, Entéroscopie double ballon, Grand mal épileptique (étiologie), Humains, Intestins (), Intestins (anatomopathologie), Intestins (imagerie diagnostique), Lymphangiectasie intestinale (), Lymphangiectasie intestinale (diagnostic), Lymphangiectasie intestinale (traitement médicamenteux), Lymphoedème (), Lymphoedème (diagnostic), Lymphoedème (traitement médicamenteux), Mâle, Octréotide (usage thérapeutique), Radiopharmaceutiques, Résultat thérapeutique, Scintigraphie, Valeur prédictive des tests.
MESH :
- anatomopathologie : Intestins.
- diagnostic : Lymphangiectasie intestinale, Lymphoedème.
- imagerie diagnostique : Intestins.
- traitement médicamenteux : Lymphangiectasie intestinale, Lymphoedème.
- usage thérapeutique : Agents gastro-intestinaux, Octréotide.
- étiologie : Grand mal épileptique.
- Adulte, Agrégat d'albumine marquée au technétium (99mTc), Biopsie, Entéroscopie double ballon, Humains, Intestins, Lymphangiectasie intestinale, Lymphoedème, Mâle, Radiopharmaceutiques, Résultat thérapeutique, Scintigraphie, Valeur prédictive des tests.

English descriptors

KwdEn :
- Adult, Biopsy, Double-Balloon Enteroscopy, Epilepsy, Tonic-Clonic (etiology), Gastrointestinal Agents (therapeutic use), Humans, Intestines (diagnostic imaging), Intestines (drug effects), Intestines (pathology), Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnosis), Lymphangiectasis, Intestinal (drug therapy), Lymphedema (complications), Lymphedema (diagnosis), Lymphedema (drug therapy), Male, Octreotide (therapeutic use), Predictive Value of Tests, Radionuclide Imaging, Radiopharmaceuticals, Technetium Tc 99m Aggregated Albumin, Treatment Outcome.
MESH :
- chemical , therapeutic use : Gastrointestinal Agents, Octreotide.
- complications : Lymphangiectasis, Intestinal, Lymphedema.
- diagnosis : Lymphangiectasis, Intestinal, Lymphedema.
- diagnostic imaging : Intestines.
- drug effects : Intestines.
- drug therapy : Lymphangiectasis, Intestinal, Lymphedema.
- etiology : Epilepsy, Tonic-Clonic.
- pathology : Intestines.
- Adult, Biopsy, Double-Balloon Enteroscopy, Humans, Male, Predictive Value of Tests, Radionuclide Imaging, Radiopharmaceuticals, Technetium Tc 99m Aggregated Albumin, Treatment Outcome.

Abstract

We report a case of a 42-year-old man with a rare disorder known as primary intestinal lymphangiectasia, which is characterized by dilated intestinal lymphatics that lead to the development of protein-losing enteropathy. The patient presented with a grand mal seizure caused by malabsorption-derived electrolytes and a protein disorder. Signs of the disease, including chronic diarrhea and peripheral edema, manifested 10 years ago, but a diagnosis was never made. The diagnosis was suspected because of the clinical manifestations, laboratory tests, imaging and endoscopic findings. Hyperemic and edematous mucosa of the small intestine corresponded to scattered white spots with dilated intestinal lymphatics and whitish villi in the histological specimen of the biopsied jejunal mucosa. Although numerous therapeutic strategies are available, only octreotide therapy proved to be an effective means of therapeutic resolution in this patient. Although the patient had a partial remission following the use of a slow release formula of octreotide, his prognosis, clinical course, and future treatment challenges are yet to be determined.

Url:

http://www.ncbi.nlm.nih.gov/pmc/articles/PMC4476896

DOI: 10.3748/wjg.v21.i23.7320
PubMed: 26109821
PubMed Central: 4476896

Affiliations:

Le document en format XML

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<term>Treatment Outcome</term>
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<term>Agrégat d'albumine marquée au technétium (99mTc)</term>
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<term>Entéroscopie double ballon</term>
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<term>Lymphangiectasie intestinale (traitement médicamenteux)</term>
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<term>Lymphoedème (traitement médicamenteux)</term>
<term>Mâle</term>
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<term>Résultat thérapeutique</term>
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<term>Lymphedema</term>
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<term>Predictive Value of Tests</term>
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<term>Radiopharmaceuticals</term>
<term>Technetium Tc 99m Aggregated Albumin</term>
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<term>Biopsie</term>
<term>Entéroscopie double ballon</term>
<term>Humains</term>
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<front><div type="abstract" xml:lang="en"><p>We report a case of a 42-year-old man with a rare disorder known as primary intestinal lymphangiectasia, which is characterized by dilated intestinal lymphatics that lead to the development of protein-losing enteropathy. The patient presented with a grand mal seizure caused by malabsorption-derived electrolytes and a protein disorder. Signs of the disease, including chronic diarrhea and peripheral edema, manifested 10 years ago, but a diagnosis was never made. The diagnosis was suspected because of the clinical manifestations, laboratory tests, imaging and endoscopic findings. Hyperemic and edematous mucosa of the small intestine corresponded to scattered white spots with dilated intestinal lymphatics and whitish villi in the histological specimen of the biopsied jejunal mucosa. Although numerous therapeutic strategies are available, only octreotide therapy proved to be an effective means of therapeutic resolution in this patient. Although the patient had a partial remission following the use of a slow release formula of octreotide, his prognosis, clinical course, and future treatment challenges are yet to be determined.</p>
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Serveur d'exploration sur le lymphœdème

How to treat an extensive form of primary intestinal lymphangiectasia?

How to treat an extensive form of primary intestinal lymphangiectasia?

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

Pour générer des pages wiki

	Serveur d'exploration sur le lymphœdème
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