[Early congenital lymphedema of the lower extremities combined with pachyonychia].
Identifieur interne : 00D934 ( Main/Curation ); précédent : 00D933; suivant : 00D935[Early congenital lymphedema of the lower extremities combined with pachyonychia].
Auteurs : G I Sukolin ; O A PasportnikovaSource :
- Vestnik dermatologii i venerologii [ 0042-4609 ] ; 1990.
Descripteurs français
- KwdFr :
- Bronchite (traitement médicamenteux), Effets différés de l'exposition prénatale aux facteurs de risque, Enfant d'âge préscolaire, Femelle, Grossesse, Humains, Jambe, Lymphoedème (), Lymphoedème (anatomopathologie), Lymphoedème (diagnostic), Lymphoedème (étiologie), Onychopathies (), Onychopathies (anatomopathologie), Onychopathies (diagnostic), Onychopathies (étiologie), Prééclampsie (traitement médicamenteux), Sulfamides (effets indésirables).
- MESH :
- anatomopathologie : Lymphoedème, Onychopathies.
- diagnostic : Lymphoedème, Onychopathies.
- effets indésirables : Sulfamides.
- traitement médicamenteux : Bronchite, Prééclampsie.
- étiologie : Lymphoedème, Onychopathies.
- Effets différés de l'exposition prénatale aux facteurs de risque, Enfant d'âge préscolaire, Femelle, Grossesse, Humains, Jambe, Lymphoedème, Onychopathies.
English descriptors
- KwdEn :
- Bronchitis (drug therapy), Child, Preschool, Female, Humans, Leg, Lymphedema (congenital), Lymphedema (diagnosis), Lymphedema (etiology), Lymphedema (pathology), Nail Diseases (congenital), Nail Diseases (diagnosis), Nail Diseases (etiology), Nail Diseases (pathology), Pre-Eclampsia (drug therapy), Pregnancy, Prenatal Exposure Delayed Effects, Sulfanilamides (adverse effects).
- MESH :
- chemical , adverse effects : Sulfanilamides.
- congenital : Lymphedema, Nail Diseases.
- diagnosis : Lymphedema, Nail Diseases.
- drug therapy : Bronchitis, Pre-Eclampsia.
- etiology : Lymphedema, Nail Diseases.
- pathology : Lymphedema, Nail Diseases.
- Child, Preschool, Female, Humans, Leg, Pregnancy, Prenatal Exposure Delayed Effects.
Abstract
A four-year-old girl with early congenital lymphedema of the lower limbs in combination with the nail plate involvement (pachyonychia) is described. Such a combination is not characteristic of early lymphedema, it is usually described in late edema of the lower limbs. The described case was a sporadic one in the family. It cannot be excluded that lymphedema development was induced by impaired embryogenesis of the lymph vessels resultant from sulphanilamides intake for severe bronchitis that proband's mother had suffered during pregnancy.
PubMed: 2220066
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pubmed:2220066Le document en format XML
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<author><name sortKey="Pasportnikova, O A" sort="Pasportnikova, O A" uniqKey="Pasportnikova O" first="O A" last="Pasportnikova">O A Pasportnikova</name>
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<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Bronchitis (drug therapy)</term>
<term>Child, Preschool</term>
<term>Female</term>
<term>Humans</term>
<term>Leg</term>
<term>Lymphedema (congenital)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (etiology)</term>
<term>Lymphedema (pathology)</term>
<term>Nail Diseases (congenital)</term>
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<term>Effets différés de l'exposition prénatale aux facteurs de risque</term>
<term>Enfant d'âge préscolaire</term>
<term>Femelle</term>
<term>Grossesse</term>
<term>Humains</term>
<term>Jambe</term>
<term>Lymphoedème ()</term>
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<term>Onychopathies (étiologie)</term>
<term>Prééclampsie (traitement médicamenteux)</term>
<term>Sulfamides (effets indésirables)</term>
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<term>Onychopathies</term>
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<term>Nail Diseases</term>
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<term>Onychopathies</term>
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<term>Femelle</term>
<term>Grossesse</term>
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<term>Jambe</term>
<term>Lymphoedème</term>
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<front><div type="abstract" xml:lang="en">A four-year-old girl with early congenital lymphedema of the lower limbs in combination with the nail plate involvement (pachyonychia) is described. Such a combination is not characteristic of early lymphedema, it is usually described in late edema of the lower limbs. The described case was a sporadic one in the family. It cannot be excluded that lymphedema development was induced by impaired embryogenesis of the lymph vessels resultant from sulphanilamides intake for severe bronchitis that proband's mother had suffered during pregnancy.</div>
</front>
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