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[Elastolytic granulomas of the legs in familial visceral lymphangiodysplasia with chronic lymphedema].

Identifieur interne : 008675 ( Main/Curation ); précédent : 008674; suivant : 008676

[Elastolytic granulomas of the legs in familial visceral lymphangiodysplasia with chronic lymphedema].

Auteurs : Mehmet Baltaci [Autriche] ; Norbert Sepp ; Gerlinde Obermoser ; Edwin Kaiserling ; Bernhard Zelger ; Peter Fritsch

Source :

RBID : pubmed:16279221

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English descriptors

Abstract

Annular elastolytic giant cell granuloma is a rare skin condition of unknown origin characterized by giant cell granulomas with elastophagocytosis and loss of elastic tissue. Sun-exposed areas are most commonly affected. We report on an unusual case of elastolytic granulomas developing in chronic lymphedema of the legs in a female patient with visceral lymphangiodysplasia.

PubMed: 16279221

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pubmed:16279221

Le document en format XML

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<title xml:lang="en">[Elastolytic granulomas of the legs in familial visceral lymphangiodysplasia with chronic lymphedema].</title>
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<name sortKey="Baltaci, Mehmet" sort="Baltaci, Mehmet" uniqKey="Baltaci M" first="Mehmet" last="Baltaci">Mehmet Baltaci</name>
<affiliation wicri:level="1">
<nlm:affiliation>Universitätsklinik für Dermatologie und Venerologie, Innsbruck, Osterreich. mehmet.baltaci@uibk.ac.at</nlm:affiliation>
<country xml:lang="fr" wicri:curation="lc">Autriche</country>
<wicri:regionArea>Universitätsklinik für Dermatologie und Venerologie, Innsbruck</wicri:regionArea>
<wicri:noRegion>Innsbruck</wicri:noRegion>
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<name sortKey="Sepp, Norbert" sort="Sepp, Norbert" uniqKey="Sepp N" first="Norbert" last="Sepp">Norbert Sepp</name>
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<name sortKey="Obermoser, Gerlinde" sort="Obermoser, Gerlinde" uniqKey="Obermoser G" first="Gerlinde" last="Obermoser">Gerlinde Obermoser</name>
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<name sortKey="Kaiserling, Edwin" sort="Kaiserling, Edwin" uniqKey="Kaiserling E" first="Edwin" last="Kaiserling">Edwin Kaiserling</name>
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<name sortKey="Zelger, Bernhard" sort="Zelger, Bernhard" uniqKey="Zelger B" first="Bernhard" last="Zelger">Bernhard Zelger</name>
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<name sortKey="Fritsch, Peter" sort="Fritsch, Peter" uniqKey="Fritsch P" first="Peter" last="Fritsch">Peter Fritsch</name>
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<title xml:lang="en">[Elastolytic granulomas of the legs in familial visceral lymphangiodysplasia with chronic lymphedema].</title>
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<name sortKey="Baltaci, Mehmet" sort="Baltaci, Mehmet" uniqKey="Baltaci M" first="Mehmet" last="Baltaci">Mehmet Baltaci</name>
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<nlm:affiliation>Universitätsklinik für Dermatologie und Venerologie, Innsbruck, Osterreich. mehmet.baltaci@uibk.ac.at</nlm:affiliation>
<country xml:lang="fr" wicri:curation="lc">Autriche</country>
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<name sortKey="Sepp, Norbert" sort="Sepp, Norbert" uniqKey="Sepp N" first="Norbert" last="Sepp">Norbert Sepp</name>
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<name sortKey="Obermoser, Gerlinde" sort="Obermoser, Gerlinde" uniqKey="Obermoser G" first="Gerlinde" last="Obermoser">Gerlinde Obermoser</name>
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<name sortKey="Kaiserling, Edwin" sort="Kaiserling, Edwin" uniqKey="Kaiserling E" first="Edwin" last="Kaiserling">Edwin Kaiserling</name>
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<name sortKey="Zelger, Bernhard" sort="Zelger, Bernhard" uniqKey="Zelger B" first="Bernhard" last="Zelger">Bernhard Zelger</name>
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<name sortKey="Fritsch, Peter" sort="Fritsch, Peter" uniqKey="Fritsch P" first="Peter" last="Fritsch">Peter Fritsch</name>
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<title level="j">Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDG</title>
<idno type="ISSN">1610-0379</idno>
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<date when="2004" type="published">2004</date>
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<keywords scheme="KwdEn" xml:lang="en">
<term>Adult</term>
<term>Angiodysplasia (complications)</term>
<term>Angiodysplasia (genetics)</term>
<term>Angiodysplasia (pathology)</term>
<term>Chronic Disease</term>
<term>Facial Dermatoses (complications)</term>
<term>Facial Dermatoses (pathology)</term>
<term>Female</term>
<term>Granuloma, Giant Cell (complications)</term>
<term>Granuloma, Giant Cell (pathology)</term>
<term>Humans</term>
<term>Leg (pathology)</term>
<term>Lymphatic System (abnormalities)</term>
<term>Lymphatic System (pathology)</term>
<term>Lymphedema (complications)</term>
<term>Lymphedema (pathology)</term>
<term>Viscera (abnormalities)</term>
<term>Viscera (pathology)</term>
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<term>Adulte</term>
<term>Angiodysplasie ()</term>
<term>Angiodysplasie (anatomopathologie)</term>
<term>Angiodysplasie (génétique)</term>
<term>Dermatoses faciales ()</term>
<term>Dermatoses faciales (anatomopathologie)</term>
<term>Femelle</term>
<term>Granulome à cellules géantes ()</term>
<term>Granulome à cellules géantes (anatomopathologie)</term>
<term>Humains</term>
<term>Jambe (anatomopathologie)</term>
<term>Lymphoedème ()</term>
<term>Lymphoedème (anatomopathologie)</term>
<term>Maladie chronique</term>
<term>Système lymphatique (anatomopathologie)</term>
<term>Système lymphatique (malformations)</term>
<term>Viscères (anatomopathologie)</term>
<term>Viscères (malformations)</term>
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<keywords scheme="MESH" qualifier="abnormalities" xml:lang="en">
<term>Lymphatic System</term>
<term>Viscera</term>
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<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr">
<term>Angiodysplasie</term>
<term>Dermatoses faciales</term>
<term>Granulome à cellules géantes</term>
<term>Jambe</term>
<term>Lymphoedème</term>
<term>Système lymphatique</term>
<term>Viscères</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en">
<term>Angiodysplasia</term>
<term>Facial Dermatoses</term>
<term>Granuloma, Giant Cell</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="genetics" xml:lang="en">
<term>Angiodysplasia</term>
</keywords>
<keywords scheme="MESH" qualifier="génétique" xml:lang="fr">
<term>Angiodysplasie</term>
</keywords>
<keywords scheme="MESH" qualifier="malformations" xml:lang="fr">
<term>Système lymphatique</term>
<term>Viscères</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en">
<term>Angiodysplasia</term>
<term>Facial Dermatoses</term>
<term>Granuloma, Giant Cell</term>
<term>Leg</term>
<term>Lymphatic System</term>
<term>Lymphedema</term>
<term>Viscera</term>
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<term>Adult</term>
<term>Chronic Disease</term>
<term>Female</term>
<term>Humans</term>
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<term>Adulte</term>
<term>Angiodysplasie</term>
<term>Dermatoses faciales</term>
<term>Femelle</term>
<term>Granulome à cellules géantes</term>
<term>Humains</term>
<term>Lymphoedème</term>
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<front>
<div type="abstract" xml:lang="en">Annular elastolytic giant cell granuloma is a rare skin condition of unknown origin characterized by giant cell granulomas with elastophagocytosis and loss of elastic tissue. Sun-exposed areas are most commonly affected. We report on an unusual case of elastolytic granulomas developing in chronic lymphedema of the legs in a female patient with visceral lymphangiodysplasia.</div>
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