Treatment of EARLY‐ONSET Gorham Syndrome with 8‐Year Follow‐Up
Identifieur interne : 007093 ( Istex/Corpus ); précédent : 007092; suivant : 007094Treatment of EARLY‐ONSET Gorham Syndrome with 8‐Year Follow‐Up
Auteurs : Annabel Maruani ; Sylvie Thimon ; Benoît De Courtivron ; Gonzague De Pinieux ; Françoise Baulieu ; Laurent Machet ; Gérard LoretteSource :
- Pediatric Dermatology [ 0736-8046 ] ; 2013-05.
Abstract
Abstract: A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. At 8 years old, lymphedema of the right inferior leg had increased, leg lengths still differed, but other clinical signs were absent.
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DOI: 10.1111/j.1525-1470.2011.01712.x
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Machet</name><affiliation><mods:affiliation>Departments of Dermatology</mods:affiliation></affiliation><affiliation><mods:affiliation>CHRU Tours</mods:affiliation></affiliation><affiliation><mods:affiliation>Inserm U930, Tours, France</mods:affiliation></affiliation></author><author><name sortKey="Lorette, Gerard" sort="Lorette, Gerard" uniqKey="Lorette G" first="Gérard" last="Lorette">Gérard Lorette</name><affiliation><mods:affiliation>Departments of Dermatology</mods:affiliation></affiliation><affiliation><mods:affiliation>CHRU Tours</mods:affiliation></affiliation></author></analytic><monogr></monogr><series><title level="j" type="main">Pediatric Dermatology</title><title level="j" type="alt">PEDIATRIC DERMATOLOGY</title><idno type="ISSN">0736-8046</idno><idno type="eISSN">1525-1470</idno><imprint><biblScope unit="vol">30</biblScope><biblScope unit="issue">3</biblScope><biblScope unit="page" from="391">391</biblScope><biblScope unit="page" to="394">394</biblScope><biblScope unit="page-count">4</biblScope><publisher>Blackwell Publishing Ltd</publisher><pubPlace>Oxford, UK</pubPlace><date type="published" when="2013-05">2013-05</date></imprint><idno type="ISSN">0736-8046</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0736-8046</idno></seriesStmt></fileDesc><profileDesc><textClass></textClass></profileDesc></teiHeader><front><div type="abstract">Abstract: A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. At 8 years old, lymphedema of the right inferior leg had increased, leg lengths still differed, but other clinical signs were absent.</div></front></TEI><istex><corpusName>wiley</corpusName><keywords><teeft><json:string>osteolysis</json:string><json:string>massive osteolysis</json:string><json:string>gorham disease</json:string><json:string>onychomadesis</json:string><json:string>dermatology</json:string><json:string>lymphatic</json:string><json:string>dermatol</json:string><json:string>lymphedema</json:string><json:string>tibia</json:string><json:string>bone sample</json:string><json:string>oncol</json:string><json:string>surg</json:string><json:string>pediatr</json:string><json:string>idiopathic</json:string><json:string>clin</json:string><json:string>ifag</json:string><json:string>candida</json:string><json:string>lymphangioma</json:string><json:string>subcutaneous</json:string><json:string>radiotherapy</json:string><json:string>ndings</json:string><json:string>nodule</json:string><json:string>right cheek</json:string><json:string>candida infection</json:string><json:string>radiation therapy</json:string><json:string>bone tissue</json:string><json:string>brous tissue</json:string><json:string>chacha nehru hospital</json:string><json:string>aseptic granuloma</json:string><json:string>syndrome</json:string><json:string>pediatric dermatology</json:string><json:string>right side</json:string><json:string>magnetic resonance imaging</json:string><json:string>heterogeneous intensity</json:string><json:string>heterogenous dystrophy</json:string><json:string>lymphatic marker</json:string><json:string>contralateral cheek</json:string><json:string>spontaneous recovery</json:string><json:string>lymphatic proliferation</json:string><json:string>severe cases</json:string><json:string>gorham syndrome</json:string><json:string>case report</json:string><json:string>nail plate</json:string><json:string>bone miner</json:string><json:string>pediatr hematol oncol</json:string><json:string>annabel maruani</json:string><json:string>chru tours</json:string><json:string>ultrasound study</json:string><json:string>hypoechoic lesion</json:string><json:string>right tibia</json:string><json:string>interesting hypotheses</json:string><json:string>pyodermite froide</json:string><json:string>right foot</json:string><json:string>childhood rosacea</json:string><json:string>acad dermatol</json:string><json:string>recurrent chalazions</json:string><json:string>yellowish cutaneous mass</json:string><json:string>pathogenesis</json:string></teeft></keywords><author><json:item><name>Annabel Maruani M.D., Ph.D.</name><affiliations><json:string>CHRU Tours</json:string><json:string>Inserm U930, Tours, France</json:string></affiliations></json:item><json:item><name>Sylvie Thimon M.D.</name><affiliations><json:string>Departments of Dermatology</json:string><json:string>CHRU Tours</json:string></affiliations></json:item><json:item><name>Benoît de Courtivron M.D.</name><affiliations><json:string>Pediatric Orthopaedic Surgery</json:string><json:string>CHRU Tours</json:string></affiliations></json:item><json:item><name>Gonzague de Pinieux M.D.</name><affiliations><json:string>Pathology, and</json:string><json:string>CHRU Tours</json:string></affiliations></json:item><json:item><name>Françoise Baulieu M.D.</name><affiliations><json:string>Nuclear Medicine, University François Rabelais Tours</json:string><json:string>CHRU Tours</json:string></affiliations></json:item><json:item><name>Laurent Machet M.D., Ph.D.</name><affiliations><json:string>Departments of Dermatology</json:string><json:string>CHRU Tours</json:string><json:string>Inserm U930, Tours, France</json:string></affiliations></json:item><json:item><name>Gérard Lorette M.D.</name><affiliations><json:string>Departments of Dermatology</json:string><json:string>CHRU Tours</json:string></affiliations></json:item></author><articleId><json:string>PDE1712</json:string></articleId><language><json:string>eng</json:string></language><originalGenre><json:string>shortCommunication</json:string></originalGenre><abstract>Abstract: A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. 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key="FR"></country></address></affiliation></author><author xml:id="author-0001"><persName><forename type="first">Sylvie</forename><surname>Thimon</surname><roleName type="degree">M.D.</roleName></persName><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation></author><author xml:id="author-0002"><persName><forename type="first">Benoît</forename><surname>de Courtivron</surname><roleName type="degree">M.D.</roleName></persName><affiliation>Pediatric Orthopaedic Surgery</affiliation><affiliation>CHRU Tours</affiliation></author><author xml:id="author-0003"><persName><forename type="first">Gonzague</forename><surname>de Pinieux</surname><roleName type="degree">M.D.</roleName></persName><affiliation>Pathology, and</affiliation><affiliation>CHRU Tours</affiliation></author><author xml:id="author-0004"><persName><forename type="first">Françoise</forename><surname>Baulieu</surname><roleName type="degree">M.D.</roleName></persName><affiliation>Nuclear Medicine, University François Rabelais Tours</affiliation><affiliation>CHRU Tours</affiliation></author><author xml:id="author-0005"><persName><forename type="first">Laurent</forename><surname>Machet</surname><roleName type="degree">M.D., Ph.D.</roleName></persName><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation><affiliation>Inserm U930, Tours, France<address><country key="FR"></country></address></affiliation></author><author xml:id="author-0006"><persName><forename type="first">Gérard</forename><surname>Lorette</surname><roleName type="degree">M.D.</roleName></persName><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation></author><idno type="istex">F0D1740F52188D686E72072236E3A07D884D7BCC</idno><idno type="DOI">10.1111/j.1525-1470.2011.01712.x</idno><idno type="unit">PDE1712</idno><idno type="toTypesetVersion">file:PDE.PDE1712.pdf</idno></analytic><monogr><title level="j" type="main">Pediatric Dermatology</title><title level="j" type="alt">PEDIATRIC DERMATOLOGY</title><idno type="pISSN">0736-8046</idno><idno type="eISSN">1525-1470</idno><idno type="book-DOI">10.1111/(ISSN)1525-1470</idno><idno type="book-part-DOI">10.1111/pde.2013.30.issue-3</idno><idno type="product">PDE</idno><idno type="publisherDivision">ST</idno><imprint><biblScope unit="vol">30</biblScope><biblScope unit="issue">3</biblScope><biblScope unit="page" from="391">391</biblScope><biblScope unit="page" to="394">394</biblScope><biblScope unit="page-count">4</biblScope><publisher>Blackwell Publishing Ltd</publisher><pubPlace>Oxford, UK</pubPlace><date type="published" when="2013-05"></date></imprint></monogr></biblStruct></sourceDesc></fileDesc><profileDesc><abstract xml:lang="en" style="main"><p><hi rend="bold">Abstract: </hi> A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. At 8 years old, lymphedema of the right inferior leg had increased, leg lengths still differed, but other clinical signs were absent.</p></abstract><textClass><classCode scheme="tocHeading1">BRIEF REPORTS</classCode><classCode scheme="articleCategory">BRIEF REPORT</classCode></textClass><langUsage><language ident="EN"></language></langUsage></profileDesc></teiHeader></istex:fulltextTEI><json:item><extension>txt</extension><original>false</original><mimetype>text/plain</mimetype><uri>https://api.istex.fr/document/F0D1740F52188D686E72072236E3A07D884D7BCC/fulltext/txt</uri></json:item></fulltext><metadata><istex:metadataXml wicri:clean="Wiley, elements deleted: body"><istex:xmlDeclaration>version="1.0" encoding="UTF-8" standalone="yes"</istex:xmlDeclaration><istex:document><component version="2.0" type="serialArticle" xml:lang="en"><header><publicationMeta level="product"><publisherInfo><publisherName>Blackwell Publishing Ltd</publisherName><publisherLoc>Oxford, 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correspondence to Annabel Maruani, M.D., Ph.D., Department of Dermatology, Trousseau Hospital, CHRU Tours, Avenue de la République, 37044 Tours Cedex 9, France, or e‐mail: <email normalForm="annabel.maruani@univ-tours.fr">annabel.maruani@univ-tours.fr</email>.</correspondenceTo><linkGroup><link type="toTypesetVersion" href="file:PDE.PDE1712.pdf"></link></linkGroup></publicationMeta><contentMeta><countGroup><count type="figureTotal" number="4"></count><count type="tableTotal" number="0"></count></countGroup><titleGroup><title type="main">Treatment of EARLY‐ONSET Gorham Syndrome with 8‐Year Follow‐Up</title><title type="short">Brief Report</title></titleGroup><creators><creator creatorRole="author" xml:id="cr1" affiliationRef="#a5 #a6"><personName><givenNames>Annabel</givenNames><familyName>Maruani</familyName><degrees>M.D., Ph.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr2" affiliationRef="#a1 #a5"><personName><givenNames>Sylvie</givenNames><familyName>Thimon</familyName><degrees>M.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr3" affiliationRef="#a2 #a5"><personName><givenNames>Benoît</givenNames><familyName>de Courtivron</familyName><degrees>M.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr4" affiliationRef="#a3 #a5"><personName><givenNames>Gonzague</givenNames><familyName>de Pinieux</familyName><degrees>M.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr5" affiliationRef="#a4 #a5"><personName><givenNames>Françoise</givenNames><familyName>Baulieu</familyName><degrees>M.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr6" affiliationRef="#a1 #a5 #a6"><personName><givenNames>Laurent</givenNames><familyName>Machet</familyName><degrees>M.D., Ph.D.</degrees></personName></creator><creator creatorRole="author" xml:id="cr7" affiliationRef="#a1 #a5"><personName><givenNames>Gérard</givenNames><familyName>Lorette</familyName><degrees>M.D.</degrees></personName></creator></creators><affiliationGroup><affiliation xml:id="a1"><unparsedAffiliation>Departments of Dermatology</unparsedAffiliation></affiliation><affiliation xml:id="a2"><unparsedAffiliation>Pediatric Orthopaedic Surgery</unparsedAffiliation></affiliation><affiliation xml:id="a3"><unparsedAffiliation>Pathology, and</unparsedAffiliation></affiliation><affiliation xml:id="a4"><unparsedAffiliation>Nuclear Medicine, University François Rabelais Tours</unparsedAffiliation></affiliation><affiliation xml:id="a5"><unparsedAffiliation>CHRU Tours</unparsedAffiliation></affiliation><affiliation xml:id="a6" countryCode="FR"><unparsedAffiliation>Inserm U930, Tours, France</unparsedAffiliation></affiliation></affiliationGroup><abstractGroup><abstract type="main" xml:lang="en"><p><b>Abstract: </b> A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. At 8 years old, lymphedema of the right inferior leg had increased, leg lengths still differed, but other clinical signs were absent.</p></abstract></abstractGroup></contentMeta></header></component></istex:document></istex:metadataXml><mods version="3.6"><titleInfo lang="en"><title>Treatment of EARLY‐ONSET Gorham Syndrome with 8‐Year Follow‐Up</title></titleInfo><titleInfo type="abbreviated" lang="en"><title>Brief Report</title></titleInfo><titleInfo type="alternative" contentType="CDATA" lang="en"><title>Treatment of EARLY‐ONSET Gorham Syndrome with 8‐Year Follow‐Up</title></titleInfo><name type="personal"><namePart type="given">Annabel</namePart><namePart type="family">Maruani</namePart><namePart type="termsOfAddress">M.D., Ph.D.</namePart><affiliation>CHRU Tours</affiliation><affiliation>Inserm U930, Tours, France</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Sylvie</namePart><namePart type="family">Thimon</namePart><namePart type="termsOfAddress">M.D.</namePart><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Benoît</namePart><namePart type="family">de Courtivron</namePart><namePart type="termsOfAddress">M.D.</namePart><affiliation>Pediatric Orthopaedic Surgery</affiliation><affiliation>CHRU Tours</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Gonzague</namePart><namePart type="family">de Pinieux</namePart><namePart type="termsOfAddress">M.D.</namePart><affiliation>Pathology, and</affiliation><affiliation>CHRU Tours</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Françoise</namePart><namePart type="family">Baulieu</namePart><namePart type="termsOfAddress">M.D.</namePart><affiliation>Nuclear Medicine, University François Rabelais Tours</affiliation><affiliation>CHRU Tours</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Laurent</namePart><namePart type="family">Machet</namePart><namePart type="termsOfAddress">M.D., Ph.D.</namePart><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation><affiliation>Inserm U930, Tours, France</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Gérard</namePart><namePart type="family">Lorette</namePart><namePart type="termsOfAddress">M.D.</namePart><affiliation>Departments of Dermatology</affiliation><affiliation>CHRU Tours</affiliation><role><roleTerm type="text">author</roleTerm></role></name><typeOfResource>text</typeOfResource><genre type="brief-communication" displayLabel="shortCommunication"></genre><originInfo><publisher>Blackwell Publishing Ltd</publisher><place><placeTerm type="text">Oxford, UK</placeTerm></place><dateIssued encoding="w3cdtf">2013-05</dateIssued><copyrightDate encoding="w3cdtf">2013</copyrightDate></originInfo><language><languageTerm type="code" authority="rfc3066">en</languageTerm><languageTerm type="code" authority="iso639-2b">eng</languageTerm></language><physicalDescription><internetMediaType>text/html</internetMediaType><extent unit="figures">4</extent></physicalDescription><abstract>Abstract: A case of Gorham disease with several years of follow‐up is reported. At birth he had a mass in the thigh which was had pathology demonstrating a lymphangioma. By age 3 years, he had lymphedema of the ipsilateral foot and discrepant leg lengths. Radiography revealed heterogenous dystrophy of the bones and osteolysis of the hallux. At age 6, a spontaneous fracture of the right tibia was treated with surgery. Histopathology of a bone sample demonstrated bone remodelling, fibrous tissue, and large vascular lacunas within bone tissue, bordered by cells expressing the lymphaticmarker D2–40. At 8 years old, lymphedema of the right inferior leg had increased, leg lengths still differed, but other clinical signs were absent.</abstract><relatedItem type="host"><titleInfo><title>Pediatric Dermatology</title></titleInfo><genre type="journal">journal</genre><subject><genre>article-category</genre><topic>BRIEF REPORT</topic></subject><identifier type="ISSN">0736-8046</identifier><identifier type="eISSN">1525-1470</identifier><identifier type="DOI">10.1111/(ISSN)1525-1470</identifier><identifier type="PublisherID">PDE</identifier><part><date>2013</date><detail type="volume"><caption>vol.</caption><number>30</number></detail><detail type="issue"><caption>no.</caption><number>3</number></detail><extent unit="pages"><start>391</start><end>394</end><total>4</total></extent></part></relatedItem><identifier type="istex">F0D1740F52188D686E72072236E3A07D884D7BCC</identifier><identifier type="DOI">10.1111/j.1525-1470.2011.01712.x</identifier><identifier type="ArticleID">PDE1712</identifier><accessCondition type="use and reproduction" contentType="copyright">© 2012 Wiley Periodicals, Inc.</accessCondition><recordInfo><recordContentSource>WILEY</recordContentSource><recordOrigin>Blackwell Publishing Ltd</recordOrigin></recordInfo></mods></metadata><serie></serie></istex></record>Pour manipuler ce document sous Unix (Dilib)
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