85. Die Lymphangioleiomyomatose
Identifieur interne : 005532 ( Istex/Corpus ); précédent : 005531; suivant : 00553385. Die Lymphangioleiomyomatose
Auteurs : H. S. Brieler ; E. W. Schwarze ; Ch. Stambolis ; H. Haage ; A. ThiedeSource :
- Langenbecks Archiv für Chirurgie [ 0023-8236 ] ; 1975-12-01.
Abstract
Symmary: A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. Proliferation of smooth, muscle cells in the lymphatic system leads to chylothorax, sometimes associated with chylopericardium or chylascos. Honeycomblung is found at radiologic examination in later stages. Conservative therapy has only a temporary effect, whilst operative treatment with pleurodesis prolongs survival only for a short time. This illness, with its poor prognosis, is seen in women only.
Url:
DOI: 10.1007/BF01257571
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ISTEX:B5AF426735E2C385B0D635FB3FB40B7A8667FE2ELe document en format XML
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Brieler</name><affiliation><mods:affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</mods:affiliation></affiliation></author><author><name sortKey="Schwarze, E W" sort="Schwarze, E W" uniqKey="Schwarze E" first="E. W." last="Schwarze">E. W. Schwarze</name><affiliation><mods:affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</mods:affiliation></affiliation></author><author><name sortKey="Stambolis, Ch" sort="Stambolis, Ch" uniqKey="Stambolis C" first="Ch." last="Stambolis">Ch. Stambolis</name><affiliation><mods:affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</mods:affiliation></affiliation></author><author><name sortKey="Haage, H" sort="Haage, H" uniqKey="Haage H" first="H." last="Haage">H. Haage</name><affiliation><mods:affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</mods:affiliation></affiliation></author><author><name sortKey="Thiede, A" sort="Thiede, A" uniqKey="Thiede A" first="A." last="Thiede">A. Thiede</name><affiliation><mods:affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</mods:affiliation></affiliation></author></analytic><monogr></monogr><series><title level="j">Langenbecks Archiv für Chirurgie</title><title level="j" type="abbrev">Langenbecks Arch Chiv</title><idno type="ISSN">0023-8236</idno><idno type="eISSN">1435-2451</idno><imprint><publisher>Springer-Verlag</publisher><pubPlace>Berlin/Heidelberg</pubPlace><date type="published" when="1975-12-01">1975-12-01</date><biblScope unit="volume">339</biblScope><biblScope unit="issue">1</biblScope><biblScope unit="page" from="642">642</biblScope><biblScope unit="page" to="643">643</biblScope></imprint><idno type="ISSN">0023-8236</idno></series></biblStruct></sourceDesc><seriesStmt><idno type="ISSN">0023-8236</idno></seriesStmt></fileDesc><profileDesc><textClass></textClass><langUsage><language ident="de">de</language></langUsage></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Symmary: A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. Proliferation of smooth, muscle cells in the lymphatic system leads to chylothorax, sometimes associated with chylopericardium or chylascos. Honeycomblung is found at radiologic examination in later stages. Conservative therapy has only a temporary effect, whilst operative treatment with pleurodesis prolongs survival only for a short time. This illness, with its poor prognosis, is seen in women only.</div></front></TEI><istex><corpusName>springer</corpusName><author><json:item><name>H. S. Brieler</name><affiliations><json:string>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</json:string></affiliations></json:item><json:item><name>E. W. Schwarze</name><affiliations><json:string>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</json:string></affiliations></json:item><json:item><name>Ch. Stambolis</name><affiliations><json:string>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</json:string></affiliations></json:item><json:item><name>H. Haage</name><affiliations><json:string>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</json:string></affiliations></json:item><json:item><name>A. Thiede</name><affiliations><json:string>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</json:string></affiliations></json:item></author><articleId><json:string>BF01257571</json:string><json:string>Art91</json:string></articleId><language><json:string>ger</json:string></language><originalGenre><json:string>OriginalPaper</json:string></originalGenre><abstract>Symmary: A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. 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Die Lymphangioleiomyomatose</title><title level="a" type="alt" xml:lang="en">Lymphangioleiomyomatosis</title><author xml:id="author-0000"><persName><forename type="first">H.</forename><surname>Brieler</surname></persName><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation></author><author xml:id="author-0001"><persName><forename type="first">E.</forename><surname>Schwarze</surname></persName><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation></author><author xml:id="author-0002"><persName><forename type="first">Ch.</forename><surname>Stambolis</surname></persName><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation></author><author xml:id="author-0003"><persName><forename type="first">H.</forename><surname>Haage</surname></persName><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation></author><author xml:id="author-0004"><persName><forename type="first">A.</forename><surname>Thiede</surname></persName><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation></author><idno type="istex">B5AF426735E2C385B0D635FB3FB40B7A8667FE2E</idno><idno type="DOI">10.1007/BF01257571</idno><idno type="ArticleID">BF01257571</idno><idno type="ArticleID">Art91</idno></analytic><monogr><title level="j">Langenbecks Archiv für Chirurgie</title><title level="j" type="abbrev">Langenbecks Arch Chiv</title><idno type="pISSN">0023-8236</idno><idno type="eISSN">1435-2451</idno><idno type="journal-ID">true</idno><idno type="issue-article-count">243</idno><idno type="volume-issue-count">0</idno><imprint><publisher>Springer-Verlag</publisher><pubPlace>Berlin/Heidelberg</pubPlace><date type="published" when="1975-12-01"></date><biblScope unit="volume">339</biblScope><biblScope unit="issue">1</biblScope><biblScope unit="page" from="642">642</biblScope><biblScope unit="page" to="643">643</biblScope></imprint></monogr></biblStruct></sourceDesc></fileDesc><profileDesc><creation><date>1975</date></creation><langUsage><language ident="de">de</language></langUsage><abstract xml:lang="en"><p>Symmary: A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. Proliferation of smooth, muscle cells in the lymphatic system leads to chylothorax, sometimes associated with chylopericardium or chylascos. Honeycomblung is found at radiologic examination in later stages. Conservative therapy has only a temporary effect, whilst operative treatment with pleurodesis prolongs survival only for a short time. This illness, with its poor prognosis, is seen in women only.</p></abstract><abstract xml:lang="de"><p>Zusammenfassung: An Hand klinischer, lymphographischer, intraoperativer und autoptischer Befunde wird fiber eine 24jährige Frau mit einer generalisierten Lymphan-gioleiomyomatose mit diffusem Lungenbefall berichtet. Die Proliferation glatter Muskel zellen im lymphatischen System führt zu Chylothorax, seltener zum Chyloperikard oder Chylaskos. Röntgenologisch besteht im Spätstadium das Bild einer Wabenlunge. Eine konservative Therapie führt nur passager zur Besserung, eine Pleurodese hat lebensverlängemden Effekt. Betroffen werden nur Frauen. Die Prognose der generalisierten Form ist infaust.</p></abstract><textClass><keywords scheme="Journal Subject"><list><head>Medicine & Public Health</head><item><term>Abdominal Surgery</term></item><item><term>Cardiac Surgery</term></item><item><term>General Surgery</term></item><item><term>Thoracic Surgery</term></item><item><term>Traumatic Surgery</term></item><item><term>Vascular Surgery</term></item></list></keywords></textClass></profileDesc><revisionDesc><change when="1975-12-01">Published</change></revisionDesc></teiHeader></istex:fulltextTEI><json:item><extension>txt</extension><original>false</original><mimetype>text/plain</mimetype><uri>https://api.istex.fr/document/B5AF426735E2C385B0D635FB3FB40B7A8667FE2E/fulltext/txt</uri></json:item></fulltext><metadata><istex:metadataXml wicri:clean="Springer, Publisher found" wicri:toSee="no header"><istex:xmlDeclaration>version="1.0" encoding="UTF-8"</istex:xmlDeclaration><istex:docType PUBLIC="-//Springer-Verlag//DTD A++ V2.4//EN" URI="http://devel.springer.de/A++/V2.4/DTD/A++V2.4.dtd" name="istex:docType"></istex:docType><istex:document><Publisher><PublisherInfo><PublisherName>Springer-Verlag</PublisherName><PublisherLocation>Berlin/Heidelberg</PublisherLocation></PublisherInfo><Journal><JournalInfo JournalProductType="ArchiveJournal" NumberingStyle="Unnumbered"><JournalID>423</JournalID><JournalPrintISSN>0023-8236</JournalPrintISSN><JournalElectronicISSN>1435-2451</JournalElectronicISSN><JournalTitle>Langenbecks Archiv für Chirurgie</JournalTitle><JournalAbbreviatedTitle>Langenbecks Arch Chiv</JournalAbbreviatedTitle><JournalSubjectGroup><JournalSubject Type="Primary">Medicine & Public Health</JournalSubject><JournalSubject Type="Secondary">Abdominal Surgery</JournalSubject><JournalSubject Type="Secondary">Cardiac Surgery</JournalSubject><JournalSubject Type="Secondary">General Surgery</JournalSubject><JournalSubject Type="Secondary">Thoracic Surgery</JournalSubject><JournalSubject Type="Secondary">Traumatic Surgery</JournalSubject><JournalSubject Type="Secondary">Vascular Surgery</JournalSubject></JournalSubjectGroup></JournalInfo><Volume><VolumeInfo VolumeType="Regular" TocLevels="0"><VolumeIDStart>339</VolumeIDStart><VolumeIDEnd>339</VolumeIDEnd><VolumeIssueCount>0</VolumeIssueCount></VolumeInfo><Issue IssueType="Regular"><IssueInfo TocLevels="0"><IssueIDStart>1</IssueIDStart><IssueIDEnd>1</IssueIDEnd><IssueArticleCount>243</IssueArticleCount><IssueHistory><CoverDate><DateString>1975</DateString><Year>1975</Year><Month>12</Month></CoverDate></IssueHistory><IssueCopyright><CopyrightHolderName>Springer-Verlag</CopyrightHolderName><CopyrightYear>1975</CopyrightYear></IssueCopyright></IssueInfo><Article ID="Art91"><ArticleInfo Language="De" ArticleType="OriginalPaper" NumberingStyle="Unnumbered" TocLevels="0" ContainsESM="No"><ArticleID>BF01257571</ArticleID><ArticleDOI>10.1007/BF01257571</ArticleDOI><ArticleSequenceNumber>91</ArticleSequenceNumber><ArticleTitle Language="De">85. Die Lymphangioleiomyomatose</ArticleTitle><ArticleTitle Language="En">Lymphangioleiomyomatosis</ArticleTitle><ArticleCategory>B. Wissenschaftliches Programm</ArticleCategory><ArticleSubCategory>III. Freie Vortrdge mit Diskussionen A. Die ungewöhnliche Beobachtung</ArticleSubCategory><ArticleFirstPage>642</ArticleFirstPage><ArticleLastPage>643</ArticleLastPage><ArticleHistory><RegistrationDate><Year>2005</Year><Month>2</Month><Day>17</Day></RegistrationDate></ArticleHistory><ArticleCopyright><CopyrightHolderName>Springer-Verlag</CopyrightHolderName><CopyrightYear>1975</CopyrightYear></ArticleCopyright><ArticleGrants Type="Regular"><MetadataGrant Grant="OpenAccess"></MetadataGrant><AbstractGrant Grant="OpenAccess"></AbstractGrant><BodyPDFGrant Grant="Restricted"></BodyPDFGrant><BodyHTMLGrant Grant="Restricted"></BodyHTMLGrant><BibliographyGrant Grant="Restricted"></BibliographyGrant><ESMGrant Grant="Restricted"></ESMGrant></ArticleGrants><ArticleContext><JournalID>423</JournalID><VolumeIDStart>339</VolumeIDStart><VolumeIDEnd>339</VolumeIDEnd><IssueIDStart>1</IssueIDStart><IssueIDEnd>1</IssueIDEnd></ArticleContext></ArticleInfo><ArticleHeader><AuthorGroup><Author AffiliationIDS="Aff1"><AuthorName DisplayOrder="Western"><GivenName>H.</GivenName><GivenName>S.</GivenName><FamilyName>Brieler</FamilyName></AuthorName></Author><Author AffiliationIDS="Aff1"><AuthorName DisplayOrder="Western"><GivenName>E.</GivenName><GivenName>W.</GivenName><FamilyName>Schwarze</FamilyName></AuthorName></Author><Author AffiliationIDS="Aff1"><AuthorName DisplayOrder="Western"><GivenName>Ch.</GivenName><FamilyName>Stambolis</FamilyName></AuthorName></Author><Author AffiliationIDS="Aff1"><AuthorName DisplayOrder="Western"><GivenName>H.</GivenName><FamilyName>Haage</FamilyName></AuthorName></Author><Author AffiliationIDS="Aff1"><AuthorName DisplayOrder="Western"><GivenName>A.</GivenName><FamilyName>Thiede</FamilyName></AuthorName></Author><Affiliation ID="Aff1"><OrgName>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität</OrgName><OrgAddress><City>Kiel</City></OrgAddress></Affiliation></AuthorGroup><Abstract ID="Abs1" Language="En"><Heading>Symmary</Heading><Para>A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. Proliferation of smooth, muscle cells in the lymphatic system leads to chylothorax, sometimes associated with chylopericardium or chylascos. Honeycomblung is found at radiologic examination in later stages. Conservative therapy has only a temporary effect, whilst operative treatment with pleurodesis prolongs survival only for a short time. This illness, with its poor prognosis, is seen in women only.</Para></Abstract><Abstract ID="Abs2" Language="De"><Heading>Zusammenfassung</Heading><Para>An Hand klinischer, lymphographischer, intraoperativer und autoptischer Befunde wird fiber eine 24jährige Frau mit einer generalisierten Lymphan-gioleiomyomatose mit diffusem Lungenbefall berichtet. Die Proliferation glatter Muskel zellen im lymphatischen System führt zu Chylothorax, seltener zum Chyloperikard oder Chylaskos. Röntgenologisch besteht im Spätstadium das Bild einer Wabenlunge. Eine konservative Therapie führt nur passager zur Besserung, eine Pleurodese hat lebensverlängemden Effekt. Betroffen werden nur Frauen. Die Prognose der generalisierten Form ist infaust.</Para></Abstract><KeywordGroup Language="En"><Heading>Key words</Heading><Keyword>Chylothorax</Keyword><Keyword>Lymphangioleiomyomatosis</Keyword><Keyword>Myomatous, proliferation</Keyword><Keyword>Honeycomblung</Keyword></KeywordGroup><KeywordGroup Language="De"><Heading>Schlüsselwörter</Heading><Keyword>Chylothorax</Keyword><Keyword>Lymphangioleiomyomatose</Keyword><Keyword>Myomatbse Proliferation</Keyword><Keyword>Honigwabenlunge</Keyword></KeywordGroup></ArticleHeader><NoBody></NoBody></Article></Issue></Volume></Journal></Publisher></istex:document></istex:metadataXml><mods version="3.6"><titleInfo lang="de"><title>85. Die Lymphangioleiomyomatose</title></titleInfo><titleInfo type="alternative" contentType="CDATA" lang="de"><title>85. Die Lymphangioleiomyomatose</title></titleInfo><titleInfo lang="en"><title>Lymphangioleiomyomatosis</title></titleInfo><titleInfo type="alternative" contentType="CDATA" lang="en"><title>Lymphangioleiomyomatosis</title></titleInfo><name type="personal"><namePart type="given">H.</namePart><namePart type="given">S.</namePart><namePart type="family">Brieler</namePart><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">E.</namePart><namePart type="given">W.</namePart><namePart type="family">Schwarze</namePart><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">Ch.</namePart><namePart type="family">Stambolis</namePart><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">H.</namePart><namePart type="family">Haage</namePart><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation><role><roleTerm type="text">author</roleTerm></role></name><name type="personal"><namePart type="given">A.</namePart><namePart type="family">Thiede</namePart><affiliation>Chirurgische and Radiologische Klinik and Pathologisches Institut der Universität, Kiel</affiliation><role><roleTerm type="text">author</roleTerm></role></name><typeOfResource>text</typeOfResource><genre type="research-article" displayLabel="OriginalPaper"></genre><originInfo><publisher>Springer-Verlag</publisher><place><placeTerm type="text">Berlin/Heidelberg</placeTerm></place><dateIssued encoding="w3cdtf">1975-12-01</dateIssued><copyrightDate encoding="w3cdtf">1975</copyrightDate></originInfo><language><languageTerm type="code" authority="rfc3066">de</languageTerm><languageTerm type="code" authority="iso639-2b">ger</languageTerm></language><physicalDescription><internetMediaType>text/html</internetMediaType></physicalDescription><abstract lang="en">Symmary: A case of generalized lymphangioleiomyomatosis with pulmonary manifestation in a 24-year-old woman is reported with clinical, lymphographic, operative and autoptic findings. Proliferation of smooth, muscle cells in the lymphatic system leads to chylothorax, sometimes associated with chylopericardium or chylascos. Honeycomblung is found at radiologic examination in later stages. Conservative therapy has only a temporary effect, whilst operative treatment with pleurodesis prolongs survival only for a short time. This illness, with its poor prognosis, is seen in women only.</abstract><abstract lang="de">Zusammenfassung: An Hand klinischer, lymphographischer, intraoperativer und autoptischer Befunde wird fiber eine 24jährige Frau mit einer generalisierten Lymphan-gioleiomyomatose mit diffusem Lungenbefall berichtet. Die Proliferation glatter Muskel zellen im lymphatischen System führt zu Chylothorax, seltener zum Chyloperikard oder Chylaskos. Röntgenologisch besteht im Spätstadium das Bild einer Wabenlunge. Eine konservative Therapie führt nur passager zur Besserung, eine Pleurodese hat lebensverlängemden Effekt. Betroffen werden nur Frauen. Die Prognose der generalisierten Form ist infaust.</abstract><note>B. Wissenschaftliches Programm/III. Freie Vortrdge mit Diskussionen A. 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