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Congenital annular constricting band : a case report with pseudarthrosis and review of the literature

Identifieur interne : 000954 ( France/Analysis ); précédent : 000953; suivant : 000955

Congenital annular constricting band : a case report with pseudarthrosis and review of the literature

Auteurs : V. Martinot-Duquennoy [France] ; M. Bonnevalle [France] ; B. Herbaux [France] ; P. Pellerin [France] ; P. Debeugny [France]

Source :

RBID : Pascal:96-0052737

Descripteurs français

English descriptors

Abstract

Les auteurs rapportent le cas d'un patient porteur d'une maladie des brides amniotiques avec pseudarthrose du tibia et du péroné, et ouverture cutanée. La souffrance vasculaire, le déficit neurologique et le lymphoedème majeur étaient présents. L'enfant a été traité en urgence avec mise en place d'un fixateur externe et excision en un temps du sillon de striction. Les auteurs proposent une revue de la littérature. Les amputations sont fréquentes, par contre les pseudarthroses sont rares. La récupération nerveuse est classique. Le risque ischémique incite à réaliser un traitement chirurgical.


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Pascal:96-0052737

Le document en format XML

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<term>Amniotic Band Syndrome (diagnosis)</term>
<term>Amniotic Band Syndrome (surgery)</term>
<term>Amniotic band</term>
<term>Case study</term>
<term>External Fixators</term>
<term>Fibula</term>
<term>Fibula (injuries)</term>
<term>Fibula (surgery)</term>
<term>Follow-Up Studies</term>
<term>Fracture Healing (physiology)</term>
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<term>Humans</term>
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<term>Leg Injuries (diagnosis)</term>
<term>Leg Injuries (surgery)</term>
<term>Newborn</term>
<term>Pseudarthrosis (congenital)</term>
<term>Pseudarthrosis (diagnosis)</term>
<term>Pseudarthrosis (surgery)</term>
<term>Pseudoarthrosis</term>
<term>Tibia</term>
<term>Tibial Fractures (congenital)</term>
<term>Tibial Fractures (diagnosis)</term>
<term>Tibial Fractures (surgery)</term>
</keywords>
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<term>Consolidation de fracture (physiologie)</term>
<term>Fibula ()</term>
<term>Fibula (traumatismes)</term>
<term>Fixateurs externes</term>
<term>Fractures du tibia ()</term>
<term>Fractures du tibia (diagnostic)</term>
<term>Fractures ouvertes ()</term>
<term>Fractures ouvertes (diagnostic)</term>
<term>Humains</term>
<term>Maladie des brides amniotiques ()</term>
<term>Maladie des brides amniotiques (diagnostic)</term>
<term>Nourrisson</term>
<term>Nouveau-né</term>
<term>Pseudarthrose ()</term>
<term>Pseudarthrose (diagnostic)</term>
<term>Traumatismes de la jambe ()</term>
<term>Traumatismes de la jambe (diagnostic)</term>
<term>Études de suivi</term>
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<term>Traumatismes de la jambe</term>
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<front>
<div type="abstract" xml:lang="fr">Les auteurs rapportent le cas d'un patient porteur d'une maladie des brides amniotiques avec pseudarthrose du tibia et du péroné, et ouverture cutanée. La souffrance vasculaire, le déficit neurologique et le lymphoedème majeur étaient présents. L'enfant a été traité en urgence avec mise en place d'un fixateur externe et excision en un temps du sillon de striction. Les auteurs proposent une revue de la littérature. Les amputations sont fréquentes, par contre les pseudarthroses sont rares. La récupération nerveuse est classique. Le risque ischémique incite à réaliser un traitement chirurgical.</div>
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