LymphedemaV1, France, Analysis, bibRecord, 000127

AA amyloidosis as a complication of primary lymphedema.

Identifieur interne : 000127 ( France/Analysis ); précédent : 000126; suivant : 000128

AA amyloidosis as a complication of primary lymphedema.

Auteurs : François Beloncle [France] ; Johnny Sayegh ; Caroline Eymerit-Morin ; Agnès Duveau ; Jean-François Augusto

Source :

Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis [ 1744-2818 ] ; 2014.

RBID : pubmed:23964754

Descripteurs français

KwdFr :
- Adulte d'âge moyen, Amyloïdose (diagnostic), Amyloïdose (étiologie), Femelle, Humains, Issue fatale, Lymphoedème (), Mâle, Protéine amyloïde A sérique (métabolisme), Ulcère cutané (diagnostic), Ulcère cutané (étiologie).
MESH :
- diagnostic : Amyloïdose, Ulcère cutané.
- métabolisme : Protéine amyloïde A sérique.
- étiologie : Amyloïdose, Ulcère cutané.
- Adulte d'âge moyen, Femelle, Humains, Issue fatale, Lymphoedème, Mâle.

English descriptors

KwdEn :
- Amyloidosis (diagnosis), Amyloidosis (etiology), Fatal Outcome, Female, Humans, Lymphedema (complications), Male, Middle Aged, Serum Amyloid A Protein (metabolism), Skin Ulcer (diagnosis), Skin Ulcer (etiology).
MESH :
- chemical , metabolism : Serum Amyloid A Protein.
- complications : Lymphedema.
- diagnosis : Amyloidosis, Skin Ulcer.
- etiology : Amyloidosis, Skin Ulcer.
- Fatal Outcome, Female, Humans, Male, Middle Aged.

Abstract

Primary lymphedema is a rare disease caused by a disorder of lymphangiogenesis. Clinical presentation and age at onset are variable. AA amyloidosis is usually due to chronic inflammatory diseases, malignant tumors or less frequently chronic infectious diseases. We report here the first two cases of AA amyloidosis present with renal failure and nephrotic syndrome in patients with primary lymphedema-induced chronic leg ulcers. The first patient was a 62-year-old female who presented with chronic untreated leg ulcers for 8 years secondary to primary lymphedema. A kidney biopsy done for nephrotic syndrome allowed the diagnosis of AA amyloidosis. The second patient was a 54-year-old male who presented with hereditary lymphedema and elephantiasis since the age of 12. A salivary gland biopsy allowed the diagnosis of AA amyloidosis. Renal function deteriorated progressively needing chronic haemodialysis. Chronic leg ulcers have been rarely reported to induce AA amyloidosis. Only five other cases have been reported in the literature, but none of them with chronic lymphedema. We believe that the relation between lymphedema, chronic leg ulcers and AA amyloidosis is underestimated.

DOI: 10.3109/13506129.2013.829032
PubMed: 23964754

Affiliations:

France

Links to Exploration step

pubmed:23964754

Le document en format XML

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<term>Issue fatale</term>
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<front><div type="abstract" xml:lang="en">Primary lymphedema is a rare disease caused by a disorder of lymphangiogenesis. Clinical presentation and age at onset are variable. AA amyloidosis is usually due to chronic inflammatory diseases, malignant tumors or less frequently chronic infectious diseases. We report here the first two cases of AA amyloidosis present with renal failure and nephrotic syndrome in patients with primary lymphedema-induced chronic leg ulcers. The first patient was a 62-year-old female who presented with chronic untreated leg ulcers for 8 years secondary to primary lymphedema. A kidney biopsy done for nephrotic syndrome allowed the diagnosis of AA amyloidosis. The second patient was a 54-year-old male who presented with hereditary lymphedema and elephantiasis since the age of 12. A salivary gland biopsy allowed the diagnosis of AA amyloidosis. Renal function deteriorated progressively needing chronic haemodialysis. Chronic leg ulcers have been rarely reported to induce AA amyloidosis. Only five other cases have been reported in the literature, but none of them with chronic lymphedema. We believe that the relation between lymphedema, chronic leg ulcers and AA amyloidosis is underestimated.</div>
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Serveur d'exploration sur le lymphœdème

AA amyloidosis as a complication of primary lymphedema.

AA amyloidosis as a complication of primary lymphedema.

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

Links to Exploration step

Le document en format XML

Pour manipuler ce document sous Unix (Dilib)

Pour mettre un lien sur cette page dans le réseau Wicri

Pour générer des pages wiki

	Serveur d'exploration sur le lymphœdème
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