Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited
Identifieur interne : 005C74 ( Ncbi/Merge ); précédent : 005C73; suivant : 005C75Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited
Auteurs : Ks Ravichandra ; Chaitanya Ram Kandregula ; Srikanth Koya ; Disha LakhotiaSource :
- International Journal of Clinical Pediatric Dentistry [ 0974-7052 ] ; 2015.
Abstract
First described in 1932 by Dearborn as ‘congenital pure analgesia’, congenital insensitivity to pain and anhydrosis (CIPA) or hereditary sensory and autonomic neuropathy (HSAN) type IV is an extremely rare autosomal recessive disorder. A 7-year-old female child who is an established case of congenital insensitivity to pain and anhydrosis visited the department of pediatric medicine with osteoarthritic neuropathy. A multidisciplinary team approach was utilized to treat the child under general anesthesia. This article also discusses the diagnostic and therapeutic dilemmas involved in treating this type of children.
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DOI: 10.5005/jp-journals-10005-1288
PubMed: 26124587
PubMed Central: 4472877
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<author><name sortKey="Kandregula, Chaitanya Ram" sort="Kandregula, Chaitanya Ram" uniqKey="Kandregula C" first="Chaitanya Ram" last="Kandregula">Chaitanya Ram Kandregula</name>
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<author><name sortKey="Lakhotia, Disha" sort="Lakhotia, Disha" uniqKey="Lakhotia D" first="Disha" last="Lakhotia">Disha Lakhotia</name>
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<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a" type="main">Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited</title>
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<front><div type="abstract" xml:lang="en"><title>ABSTRACT</title>
<p>First described in 1932 by Dearborn as ‘congenital pure analgesia’, congenital insensitivity to pain and anhydrosis (CIPA) or hereditary sensory and autonomic neuropathy (HSAN) type IV is an extremely rare autosomal recessive disorder. A 7-year-old female child who is an established case of congenital insensitivity to pain and anhydrosis visited the department of pediatric medicine with osteoarthritic neuropathy. A multidisciplinary team approach was utilized to treat the child under general anesthesia. This article also discusses the diagnostic and therapeutic dilemmas involved in treating this type of children.</p>
<p><bold>How to cite this article:</bold>
Ravichandra KS, Kandregula CR, Koya S, Lakhotia D. Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited. Int J Clin Pediatr Dent 2015;8(1):75-81.</p>
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<pmc article-type="case-report"><pmc-dir>properties open_access</pmc-dir>
<front><journal-meta><journal-id journal-id-type="nlm-ta">Int J Clin Pediatr Dent</journal-id>
<journal-id journal-id-type="iso-abbrev">Int J Clin Pediatr Dent</journal-id>
<journal-id journal-id-type="publisher-id">IJCPD</journal-id>
<journal-title-group><journal-title>International Journal of Clinical Pediatric Dentistry</journal-title>
</journal-title-group>
<issn pub-type="ppub">0974-7052</issn>
<issn pub-type="epub">0975-1904</issn>
<publisher><publisher-name>Jaypee Brothers Medical Publishers</publisher-name>
</publisher>
</journal-meta>
<article-meta><article-id pub-id-type="pmid">26124587</article-id>
<article-id pub-id-type="pmc">4472877</article-id>
<article-id pub-id-type="doi">10.5005/jp-journals-10005-1288</article-id>
<article-categories><subj-group subj-group-type="heading"><subject>Case Report</subject>
</subj-group>
</article-categories>
<title-group><article-title>Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited</article-title>
</title-group>
<contrib-group><contrib contrib-type="author" corresp="yes"><name><surname>Ravichandra</surname>
<given-names>KS</given-names>
</name>
<aff>Professor and Head, Department of Pedodontics and Preventive Dentistry, Drs Sudha and Nageswara Rao Siddhartha Institute of Health Sciences, Chinnoutpalli, Andhra Pradesh, India</aff>
</contrib>
<contrib contrib-type="author"><name><surname>Kandregula</surname>
<given-names>Chaitanya Ram</given-names>
</name>
<aff>Senior Lecturer, Department of Pedodontics, Drs Sudha and Nageswara Rao Siddhartha Institute of Dental Sciences, Chinnoutpalli Andhra Pradesh, India</aff>
</contrib>
<contrib contrib-type="author"><name><surname>Koya</surname>
<given-names>Srikanth</given-names>
</name>
<aff>Senior Lecturer, Department of Pedodontics, Drs Sudha and Nageswara Rao Siddhartha Institute of Dental Sciences, Chinnoutpalli Andhra Pradesh, India</aff>
</contrib>
<contrib contrib-type="author"><name><surname>Lakhotia</surname>
<given-names>Disha</given-names>
</name>
<aff>Senior Lecturer, Department of Pedodontics, Drs Sudha and Nageswara Rao Siddhartha Institute of Dental Sciences, Chinnoutpalli Andhra Pradesh, India</aff>
</contrib>
</contrib-group>
<author-notes><corresp id="cor">KS Ravichandra, Professor and Head, Department of Pedodontics and Preventive Dentistry Drs Sudha and Nageswara Rao Siddhartha Institute of Health Sciences, Chinnoutpalli, Gannavaram Mandal-521286 Krishna District, Andhra Pradesh, India, Phone: 9849049668 e-mail: kotharavi@rediffmail.com</corresp>
</author-notes>
<pub-date pub-type="ppub"><season>Jan-Apr</season>
<year>2015</year>
</pub-date>
<pub-date pub-type="epub"><day>28</day>
<month>4</month>
<year>2015</year>
</pub-date>
<volume>8</volume>
<issue>1</issue>
<fpage>75</fpage>
<lpage>81</lpage>
<history><date date-type="received"><day>12</day>
<month>5</month>
<year>2014</year>
</date>
<date date-type="accepted"><day>02</day>
<month>9</month>
<year>2014</year>
</date>
</history>
<permissions><copyright-statement>Copyright © 2015; Jaypee Brothers Medical Publishers (P) Ltd.</copyright-statement>
<copyright-year>2015</copyright-year>
<license license-type="open-access"><license-p>This work is licensed under a Creative Commons Attribution 3.0 Unported License. To view a copy of this license, visit
<ext-link ext-link-type="uri" xlink:href="http://creativecommons.org/licenses/by/3.0/">http://creativecommons.org/licenses/by/3.0/</ext-link>
</license-p>
</license>
</permissions>
<abstract><title>ABSTRACT</title>
<p>First described in 1932 by Dearborn as ‘congenital pure analgesia’, congenital insensitivity to pain and anhydrosis (CIPA) or hereditary sensory and autonomic neuropathy (HSAN) type IV is an extremely rare autosomal recessive disorder. A 7-year-old female child who is an established case of congenital insensitivity to pain and anhydrosis visited the department of pediatric medicine with osteoarthritic neuropathy. A multidisciplinary team approach was utilized to treat the child under general anesthesia. This article also discusses the diagnostic and therapeutic dilemmas involved in treating this type of children.</p>
<p><bold>How to cite this article:</bold>
Ravichandra KS, Kandregula CR, Koya S, Lakhotia D. Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited. Int J Clin Pediatr Dent 2015;8(1):75-81.</p>
</abstract>
<kwd-group><title>Keywords</title>
<kwd>Congenital insensitivity to pain and anhydrosis</kwd>
<kwd>Pain insensitivity</kwd>
<kwd>Marvan syndrome</kwd>
<kwd>Painless whitlows.</kwd>
</kwd-group>
</article-meta>
</front>
</pmc>
<affiliations><list></list>
<tree><noCountry><name sortKey="Kandregula, Chaitanya Ram" sort="Kandregula, Chaitanya Ram" uniqKey="Kandregula C" first="Chaitanya Ram" last="Kandregula">Chaitanya Ram Kandregula</name>
<name sortKey="Koya, Srikanth" sort="Koya, Srikanth" uniqKey="Koya S" first="Srikanth" last="Koya">Srikanth Koya</name>
<name sortKey="Lakhotia, Disha" sort="Lakhotia, Disha" uniqKey="Lakhotia D" first="Disha" last="Lakhotia">Disha Lakhotia</name>
<name sortKey="Ravichandra, Ks" sort="Ravichandra, Ks" uniqKey="Ravichandra K" first="Ks" last="Ravichandra">Ks Ravichandra</name>
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