[Ehler-Danlos syndrome type VIII].
Identifieur interne : 002C74 ( Ncbi/Checkpoint ); précédent : 002C73; suivant : 002C75[Ehler-Danlos syndrome type VIII].
Auteurs : L. Ciarloni [France] ; C. Perrigouard ; D. Lipsker ; B. CribierSource :
- Annales de dermatologie et de venereologie [ 0151-9638 ] ; 2010.
Descripteurs français
- KwdFr :
- MESH :
- diagnostic : Syndrome d'Ehlers-Danlos, Syndrome de Marfan.
- étiologie : Bouche édentée, Ulcère de la jambe.
- Adulte, Diagnostic différentiel, Humains, Mâle, Syndrome d'Ehlers-Danlos.
English descriptors
- KwdEn :
- MESH :
- classification : Ehlers-Danlos Syndrome.
- diagnosis : Ehlers-Danlos Syndrome, Marfan Syndrome.
- etiology : Leg Ulcer, Mouth, Edentulous.
- Adult, Diagnosis, Differential, Humans, Male.
Abstract
Ehlers-Danlos syndrome (EDS) comprises a heterogeneous group of diseases involving genetic collagen fibre impairment. We describe a case of a patient presenting the rare type VIII, in which dermatitis ocre was associated with parodontal disease, and which was diagnosed late.
DOI: 10.1016/j.annder.2009.11.009
PubMed: 20227561
Affiliations:
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pubmed:20227561Le document en format XML
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<term>Humans</term>
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<term>Mâle</term>
<term>Syndrome d'Ehlers-Danlos ()</term>
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<front><div type="abstract" xml:lang="en">Ehlers-Danlos syndrome (EDS) comprises a heterogeneous group of diseases involving genetic collagen fibre impairment. We describe a case of a patient presenting the rare type VIII, in which dermatitis ocre was associated with parodontal disease, and which was diagnosed late.</div>
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