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Intraosseous Nerve Sheath Tumors in the Jaws

Identifieur interne : 006C66 ( Main/Exploration ); précédent : 006C65; suivant : 006C67

Intraosseous Nerve Sheath Tumors in the Jaws

Auteurs : Zhongmin Che [Corée du Sud] ; Woong Nam [Corée du Sud] ; Won-Se Park [Corée du Sud] ; Hyung-Jun Kim [Corée du Sud] ; In-Ho Cha [Corée du Sud] ; Hyun-Sil Kim [Corée du Sud] ; Jong-In Yook [Corée du Sud] ; Jin Kim [Corée du Sud] ; Sang-Hwy Lee [Corée du Sud]

Source :

RBID : PMC:2687639

Abstract

Although the head and neck region is recognized as the most common location for peripheral nerve sheath tumors, central involvement, particularly in the jaw bones, is quite unusual. Neurofibroma is one of the most common nerve sheath tumors occurring in the soft tissue and generally appears in neurofibromatosis 1 (NF1 or von Recklinghausen's disease). Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon sarcomas that almost always arise in the soft tissue. Here, we report four cases of intraosseous peripheral nerve sheath tumors occurring in the jaw bones and compare the clinical, radiologic, and pathologic findings in order to make a differential diagnosis.


Url:
DOI: 10.3349/ymj.2006.47.2.264
PubMed: 16642559
PubMed Central: 2687639


Affiliations:


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Le document en format XML

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<p>Although the head and neck region is recognized as the most common location for peripheral nerve sheath tumors, central involvement, particularly in the jaw bones, is quite unusual. Neurofibroma is one of the most common nerve sheath tumors occurring in the soft tissue and generally appears in neurofibromatosis 1 (NF1 or von Recklinghausen's disease). Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon sarcomas that almost always arise in the soft tissue. Here, we report four cases of intraosseous peripheral nerve sheath tumors occurring in the jaw bones and compare the clinical, radiologic, and pathologic findings in order to make a differential diagnosis.</p>
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<list>
<country>
<li>Corée du Sud</li>
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<li>Région capitale de Séoul</li>
</region>
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<li>Séoul</li>
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<name sortKey="Park, Won Se" sort="Park, Won Se" uniqKey="Park W" first="Won-Se" last="Park">Won-Se Park</name>
<name sortKey="Yook, Jong In" sort="Yook, Jong In" uniqKey="Yook J" first="Jong-In" last="Yook">Jong-In Yook</name>
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</record>

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