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Gorlin's syndrome with associated odontogenic cysts

Identifieur interne : 00B639 ( Main/Curation ); précédent : 00B638; suivant : 00B640

Gorlin's syndrome with associated odontogenic cysts

Auteurs : J. D. Lovin [États-Unis] ; C. L. Talarico [États-Unis] ; S. L. Wegert [États-Unis] ; L. E. Gaynor [États-Unis] ; S. S. Sutley [États-Unis]

Source :

RBID : ISTEX:0B094AE1DB8966B303A8246AC0C029656E92B292

English descriptors

Abstract

Abstract: Multiple maxillary and mandibular cysts are principle features of basal cell nevus syndrome (Gorlin-Goltz). We present cases from an affected family in which magnetic resonance imaging (MRI) was helpful in evaluation of the cystic lesions. A middle ear anomaly was identified which may represent an additional abnormality associated with the syndrome.

Url:
DOI: 10.1007/BF02012604

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ISTEX:0B094AE1DB8966B303A8246AC0C029656E92B292

Le document en format XML

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<name sortKey="Wegert, S L" sort="Wegert, S L" uniqKey="Wegert S" first="S. L." last="Wegert">S. L. Wegert</name>
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<name sortKey="Gaynor, L E" sort="Gaynor, L E" uniqKey="Gaynor L" first="L. E." last="Gaynor">L. E. Gaynor</name>
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<term>Bilateral conductive hearing loss</term>
<term>Bony erosion</term>
<term>Carcinoma</term>
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<term>Extraosseous extension</term>
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<term>Multiple basal cell carcinomas</term>
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<term>Odontogenic keratocysts</term>
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<term>Physical examination</term>
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<term>Bilateral conductive hearing loss</term>
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<term>Carcinoma</term>
<term>Cyst</term>
<term>Dentigerous cyst</term>
<term>Extraosseous extension</term>
<term>Keratocysts</term>
<term>Lesion</term>
<term>Magnetic resonance imaging</term>
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<term>Multiple basal cell carcinomas</term>
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<term>Odontogenic keratocysts</term>
<term>Oral maxillofac surg</term>
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<term>Oval window</term>
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<front>
<div type="abstract" xml:lang="en">Abstract: Multiple maxillary and mandibular cysts are principle features of basal cell nevus syndrome (Gorlin-Goltz). We present cases from an affected family in which magnetic resonance imaging (MRI) was helpful in evaluation of the cystic lesions. A middle ear anomaly was identified which may represent an additional abnormality associated with the syndrome.</div>
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