Papillon–Lefèvre syndrome: a report of two cases
Identifieur interne : 006893 ( Istex/Curation ); précédent : 006892; suivant : 006894Papillon–Lefèvre syndrome: a report of two cases
Auteurs : S. Patel [Royaume-Uni] ; L. E. Davidson [Royaume-Uni]Source :
- International Journal of Paediatric Dentistry [ 0960-7439 ] ; 2004-07.
English descriptors
- KwdEn :
- Actinobacillus actinomycetemcomitans, Alveolar bone, Anatomical defects, Bone biopsy, Bspd, Case report, Case reports, Charles clifford, Clinical periodontology, Dentistry, Dentition, Effective treatment, Extensive destruction, General anaesthesia, Generalized recession, Host response, Hyperkeratosis, Iapd, Incisor, Initial presentation, International journal, Intraoral examination, Lateral incisor, Lefevre syndrome, Lesion, Local antimicrobial therapy, Lower right, Medical history, Normal limits, Paediatric, Paediatric dentistry, Paediatric dentistry department, Papillon, Periodontal, Periodontal disease, Periodontal effects, Periodontal lesions, Periodontal therapy, Periodontology, Permanent dentition, Permanent dentitions, Plaque accumulation, Primary dentition, Primary molars, Primary teeth, Radiographic examination, Severe alveolar bone loss, Skin lesions, Syndrome, Tooth eruption, Treatment regime.
- Teeft :
- Actinobacillus actinomycetemcomitans, Alveolar bone, Anatomical defects, Bone biopsy, Bspd, Case report, Case reports, Charles clifford, Clinical periodontology, Dentistry, Dentition, Effective treatment, Extensive destruction, General anaesthesia, Generalized recession, Host response, Hyperkeratosis, Iapd, Incisor, Initial presentation, International journal, Intraoral examination, Lateral incisor, Lefevre syndrome, Lesion, Local antimicrobial therapy, Lower right, Medical history, Normal limits, Paediatric, Paediatric dentistry, Paediatric dentistry department, Papillon, Periodontal, Periodontal disease, Periodontal effects, Periodontal lesions, Periodontal therapy, Periodontology, Permanent dentition, Permanent dentitions, Plaque accumulation, Primary dentition, Primary molars, Primary teeth, Radiographic examination, Severe alveolar bone loss, Skin lesions, Syndrome, Tooth eruption, Treatment regime.
Abstract
Papillon–Lefèvre syndrome is a rare disease characterized by skin lesions caused by palmar‐plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. It is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one‐third of cases. This paper describes two preschool children who presented at the Paediatric Dentistry Department, Sheffield, UK, with progressively loosening teeth and discomfort during eating. The medical history revealed scaling on the hands and feet, which had been medically diagnosed as eczema. Papillon–Lefèvre syndrome was diagnosed in both cases.
Url:
DOI: 10.1111/j.1365-263X.2004.00559.x
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<term>Alveolar bone</term>
<term>Anatomical defects</term>
<term>Bone biopsy</term>
<term>Bspd</term>
<term>Case report</term>
<term>Case reports</term>
<term>Charles clifford</term>
<term>Clinical periodontology</term>
<term>Dentistry</term>
<term>Dentition</term>
<term>Effective treatment</term>
<term>Extensive destruction</term>
<term>General anaesthesia</term>
<term>Generalized recession</term>
<term>Host response</term>
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<term>Iapd</term>
<term>Incisor</term>
<term>Initial presentation</term>
<term>International journal</term>
<term>Intraoral examination</term>
<term>Lateral incisor</term>
<term>Lefevre syndrome</term>
<term>Lesion</term>
<term>Local antimicrobial therapy</term>
<term>Lower right</term>
<term>Medical history</term>
<term>Normal limits</term>
<term>Paediatric</term>
<term>Paediatric dentistry</term>
<term>Paediatric dentistry department</term>
<term>Papillon</term>
<term>Periodontal</term>
<term>Periodontal disease</term>
<term>Periodontal effects</term>
<term>Periodontal lesions</term>
<term>Periodontal therapy</term>
<term>Periodontology</term>
<term>Permanent dentition</term>
<term>Permanent dentitions</term>
<term>Plaque accumulation</term>
<term>Primary dentition</term>
<term>Primary molars</term>
<term>Primary teeth</term>
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<term>Syndrome</term>
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<term>Treatment regime</term>
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<term>Case report</term>
<term>Case reports</term>
<term>Charles clifford</term>
<term>Clinical periodontology</term>
<term>Dentistry</term>
<term>Dentition</term>
<term>Effective treatment</term>
<term>Extensive destruction</term>
<term>General anaesthesia</term>
<term>Generalized recession</term>
<term>Host response</term>
<term>Hyperkeratosis</term>
<term>Iapd</term>
<term>Incisor</term>
<term>Initial presentation</term>
<term>International journal</term>
<term>Intraoral examination</term>
<term>Lateral incisor</term>
<term>Lefevre syndrome</term>
<term>Lesion</term>
<term>Local antimicrobial therapy</term>
<term>Lower right</term>
<term>Medical history</term>
<term>Normal limits</term>
<term>Paediatric</term>
<term>Paediatric dentistry</term>
<term>Paediatric dentistry department</term>
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<term>Periodontal</term>
<term>Periodontal disease</term>
<term>Periodontal effects</term>
<term>Periodontal lesions</term>
<term>Periodontal therapy</term>
<term>Periodontology</term>
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<term>Plaque accumulation</term>
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<term>Primary molars</term>
<term>Primary teeth</term>
<term>Radiographic examination</term>
<term>Severe alveolar bone loss</term>
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<front><div type="abstract" xml:lang="en">Papillon–Lefèvre syndrome is a rare disease characterized by skin lesions caused by palmar‐plantar hyperkeratosis, and severe periodontal destruction involving both the primary and permanent dentitions. It is transmitted as an autosomal recessive condition and consanguinity of parents is evident in about one‐third of cases. This paper describes two preschool children who presented at the Paediatric Dentistry Department, Sheffield, UK, with progressively loosening teeth and discomfort during eating. The medical history revealed scaling on the hands and feet, which had been medically diagnosed as eczema. Papillon–Lefèvre syndrome was diagnosed in both cases.</div>
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