Neonatal congenital microvillus atrophy
Identifieur interne : 000813 ( Pmc/Curation ); précédent : 000812Neonatal congenital microvillus atrophy
Auteurs : N. Pecache ; S. Patole ; R. Hagan ; D. Hill ; A. Charles ; J. PapadimitriouSource :
- Postgraduate Medical Journal [ 0032-5473 ] ; 2004.
Abstract
Congenital microvillous atrophy (CMVA) is the leading cause of neonatal secretory diarrhoea with onset either in the first 72 hours of life (early onset) or at 6–8 weeks after birth (late onset). To date over 30 cases have been reported worldwide. The prognosis for this life threatening condition continues to be poor. Therapeutic agents like somatostatin and epidermal growth factor are either ineffective or of marginal benefit. Overall five year survival after small bowel transplantation is currently ∼50%. The following brief review is aimed towards helping neonatologists/perinatologists in the early diagnosis, and management of CMVA and in counselling the parents appropriately.
Url:
DOI: 10.1136/pmj.2003.007930
PubMed: 14970294
PubMed Central: 1742937
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<front><journal-meta><journal-id journal-id-type="nlm-ta">Postgrad Med J</journal-id><journal-title>Postgraduate Medical Journal</journal-title><issn pub-type="ppub">0032-5473</issn><issn pub-type="epub">1469-0756</issn><publisher><publisher-name>BMJ Group</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="pmid">14970294</article-id><article-id pub-id-type="pmc">1742937</article-id><article-id pub-id-type="doi">10.1136/pmj.2003.007930</article-id><article-categories><subj-group subj-group-type="heading"><subject>Review</subject></subj-group></article-categories><title-group><article-title>Neonatal congenital microvillus atrophy</article-title></title-group><contrib-group><contrib contrib-type="author"><name><surname>Pecache</surname><given-names>N</given-names></name></contrib><contrib contrib-type="author"><name><surname>Patole</surname><given-names>S</given-names></name></contrib><contrib contrib-type="author"><name><surname>Hagan</surname><given-names>R</given-names></name></contrib><contrib contrib-type="author"><name><surname>Hill</surname><given-names>D</given-names></name></contrib><contrib contrib-type="author"><name><surname>Charles</surname><given-names>A</given-names></name></contrib><contrib contrib-type="author"><name><surname>Papadimitriou</surname><given-names>J</given-names></name></contrib></contrib-group><aff>Princess Margaret and King Edward Memorial Hospitals, Neonatal Clinical Care Unit, Subiaco, Western Australia.</aff><pub-date pub-type="ppub"><month>2</month><year>2004</year></pub-date><volume>80</volume><issue>940</issue><fpage>80</fpage><lpage>83</lpage><self-uri xlink:role="pdf" xlink:type="simple" xlink:href="http://pmj.bmj.com/cgi/reprint/80/940/80.pdf"></self-uri><self-uri xlink:role="abstract" xlink:type="simple" xlink:href="http://pmj.bmj.com/cgi/content/abstract/80/940/80"></self-uri><self-uri xlink:role="fulltext" xlink:type="simple" xlink:href="http://pmj.bmj.com/cgi/content/full/80/940/80"></self-uri><abstract><p> Congenital microvillous atrophy (CMVA) is the leading cause of neonatal secretory diarrhoea with onset either in the first 72 hours of life (early onset) or at 6–8 weeks after birth (late onset). To date over 30 cases have been reported worldwide. The prognosis for this life threatening condition continues to be poor. Therapeutic agents like somatostatin and epidermal growth factor are either ineffective or of marginal benefit. Overall five year survival after small bowel transplantation is currently ∼50%. The following brief review is aimed towards helping neonatologists/perinatologists in the early diagnosis, and management of CMVA and in counselling the parents appropriately. </p></abstract></article-meta></front></pmc></record>Pour manipuler ce document sous Unix (Dilib)
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