Shrinking lung syndrome as a presenting manifestation of systemic lupus erythematosus in a female Kuwaiti.
Identifieur interne : 000441 ( PubMed/Corpus ); précédent : 000440; suivant : 000442Shrinking lung syndrome as a presenting manifestation of systemic lupus erythematosus in a female Kuwaiti.
Auteurs : Haneen Adel Al-Raqum ; Sukhbir Singh Uppal ; Moudi Al-Mutairy ; Rakesh KumariSource :
- Clinical rheumatology [ 0770-3198 ] ; 2006.
English descriptors
- KwdEn :
- Adult, Diagnosis, Differential, Drug Therapy, Combination, Dyspnea (diagnosis), Dyspnea (etiology), Dyspnea (physiopathology), Female, Glucocorticoids (therapeutic use), Humans, Hydroxychloroquine (therapeutic use), Kuwait, Lung (diagnostic imaging), Lung (pathology), Lung (physiopathology), Lung Diseases (diagnosis), Lung Diseases (drug therapy), Lung Diseases (etiology), Lung Diseases (physiopathology), Lung Volume Measurements, Lupus Erythematosus, Systemic (complications), Lupus Erythematosus, Systemic (diagnosis), Lupus Erythematosus, Systemic (drug therapy), Lupus Erythematosus, Systemic (physiopathology), Methylprednisolone Hemisuccinate (therapeutic use), Radiography, Thoracic, Respiratory Function Tests, Syndrome, Treatment Outcome.
- MESH :
- chemical , therapeutic use : Glucocorticoids, Hydroxychloroquine, Methylprednisolone Hemisuccinate.
- complications : Lupus Erythematosus, Systemic.
- diagnosis : Dyspnea, Lung Diseases, Lupus Erythematosus, Systemic.
- diagnostic imaging : Lung.
- drug therapy : Lung Diseases, Lupus Erythematosus, Systemic.
- etiology : Dyspnea, Lung Diseases.
- pathology : Lung.
- physiopathology : Dyspnea, Lung, Lung Diseases, Lupus Erythematosus, Systemic.
- Adult, Diagnosis, Differential, Drug Therapy, Combination, Female, Humans, Kuwait, Lung Volume Measurements, Radiography, Thoracic, Respiratory Function Tests, Syndrome, Treatment Outcome.
Abstract
The shrinking lung syndrome (SLS) is a rare manifestation in patients with established systemic lupus erythematosus (SLE). Only two cases have been reported in which this syndrome was the presenting manifestation of SLE. We describe a 21-year-old female Kuwaiti who presented with SLS. In addition to clinical and serological features of lupus, she had dyspnea, respiratory muscle dysfunction, characteristic chest radiographic findings of small lung volumes, elevated right hemidiaphragm, and basilar atelectasis. There was no pulmonary parenchymal or pulmonary vascular involvement. Nerve conduction study showed right phrenic nerve palsy. She responded well to treatment with corticosteroids.
DOI: 10.1007/s10067-005-0020-5
PubMed: 16378163
Links to Exploration step
pubmed:16378163Le document en format XML
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<author><name sortKey="Al Raqum, Haneen Adel" sort="Al Raqum, Haneen Adel" uniqKey="Al Raqum H" first="Haneen Adel" last="Al-Raqum">Haneen Adel Al-Raqum</name>
<affiliation><nlm:affiliation>Department of Medicine, Faculty of Medicine, Kuwait University, Safat 13110, Kuwait.</nlm:affiliation>
</affiliation>
</author>
<author><name sortKey="Uppal, Sukhbir Singh" sort="Uppal, Sukhbir Singh" uniqKey="Uppal S" first="Sukhbir Singh" last="Uppal">Sukhbir Singh Uppal</name>
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<author><name sortKey="Al Mutairy, Moudi" sort="Al Mutairy, Moudi" uniqKey="Al Mutairy M" first="Moudi" last="Al-Mutairy">Moudi Al-Mutairy</name>
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<author><name sortKey="Kumari, Rakesh" sort="Kumari, Rakesh" uniqKey="Kumari R" first="Rakesh" last="Kumari">Rakesh Kumari</name>
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<term>Diagnosis, Differential</term>
<term>Drug Therapy, Combination</term>
<term>Dyspnea (diagnosis)</term>
<term>Dyspnea (etiology)</term>
<term>Dyspnea (physiopathology)</term>
<term>Female</term>
<term>Glucocorticoids (therapeutic use)</term>
<term>Humans</term>
<term>Hydroxychloroquine (therapeutic use)</term>
<term>Kuwait</term>
<term>Lung (diagnostic imaging)</term>
<term>Lung (pathology)</term>
<term>Lung (physiopathology)</term>
<term>Lung Diseases (diagnosis)</term>
<term>Lung Diseases (drug therapy)</term>
<term>Lung Diseases (etiology)</term>
<term>Lung Diseases (physiopathology)</term>
<term>Lung Volume Measurements</term>
<term>Lupus Erythematosus, Systemic (complications)</term>
<term>Lupus Erythematosus, Systemic (diagnosis)</term>
<term>Lupus Erythematosus, Systemic (drug therapy)</term>
<term>Lupus Erythematosus, Systemic (physiopathology)</term>
<term>Methylprednisolone Hemisuccinate (therapeutic use)</term>
<term>Radiography, Thoracic</term>
<term>Respiratory Function Tests</term>
<term>Syndrome</term>
<term>Treatment Outcome</term>
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<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en"><term>Glucocorticoids</term>
<term>Hydroxychloroquine</term>
<term>Methylprednisolone Hemisuccinate</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lupus Erythematosus, Systemic</term>
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<term>Lupus Erythematosus, Systemic</term>
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<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en"><term>Lung Diseases</term>
<term>Lupus Erythematosus, Systemic</term>
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<keywords scheme="MESH" qualifier="etiology" xml:lang="en"><term>Dyspnea</term>
<term>Lung Diseases</term>
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<keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Lung</term>
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<term>Diagnosis, Differential</term>
<term>Drug Therapy, Combination</term>
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<term>Kuwait</term>
<term>Lung Volume Measurements</term>
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<front><div type="abstract" xml:lang="en">The shrinking lung syndrome (SLS) is a rare manifestation in patients with established systemic lupus erythematosus (SLE). Only two cases have been reported in which this syndrome was the presenting manifestation of SLE. We describe a 21-year-old female Kuwaiti who presented with SLS. In addition to clinical and serological features of lupus, she had dyspnea, respiratory muscle dysfunction, characteristic chest radiographic findings of small lung volumes, elevated right hemidiaphragm, and basilar atelectasis. There was no pulmonary parenchymal or pulmonary vascular involvement. Nerve conduction study showed right phrenic nerve palsy. She responded well to treatment with corticosteroids.</div>
</front>
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<ArticleTitle>Shrinking lung syndrome as a presenting manifestation of systemic lupus erythematosus in a female Kuwaiti.</ArticleTitle>
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<Abstract><AbstractText>The shrinking lung syndrome (SLS) is a rare manifestation in patients with established systemic lupus erythematosus (SLE). Only two cases have been reported in which this syndrome was the presenting manifestation of SLE. We describe a 21-year-old female Kuwaiti who presented with SLS. In addition to clinical and serological features of lupus, she had dyspnea, respiratory muscle dysfunction, characteristic chest radiographic findings of small lung volumes, elevated right hemidiaphragm, and basilar atelectasis. There was no pulmonary parenchymal or pulmonary vascular involvement. Nerve conduction study showed right phrenic nerve palsy. She responded well to treatment with corticosteroids.</AbstractText>
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<ReferenceList><Reference><Citation>Q J Med. 1989 May;71(265):429-39</Citation>
<ArticleIdList><ArticleId IdType="pubmed">2602542</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>Crit Care Clin. 2002 Oct;18(4):781-803</Citation>
<ArticleIdList><ArticleId IdType="pubmed">12418441</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>J Rheumatol. 1976 Sep;3(3):262-8</Citation>
<ArticleIdList><ArticleId IdType="pubmed">1086364</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>Chest. 2001 Apr;119(4):1274-7</Citation>
<ArticleIdList><ArticleId IdType="pubmed">11296200</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>J Rheumatol. 1983 Dec;10(6):973-6</Citation>
<ArticleIdList><ArticleId IdType="pubmed">6663599</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>Aust N Z J Med. 1990 Feb;20(1):67-70</Citation>
<ArticleIdList><ArticleId IdType="pubmed">2322204</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>Arthritis Rheum. 1982 Nov;25(11):1271-7</Citation>
<ArticleIdList><ArticleId IdType="pubmed">7138600</ArticleId>
</ArticleIdList>
</Reference>
<Reference><Citation>Rev Med Interne. 2004 Jan;25(1):83-90</Citation>
<ArticleIdList><ArticleId IdType="pubmed">14736565</ArticleId>
</ArticleIdList>
</Reference>
</ReferenceList>
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