Acute pulmonary embolism in a child with ANCA-negative Idiopathic Pulmonary Capillaritis.
Identifieur interne : 000073 ( PubMed/Checkpoint ); précédent : 000072; suivant : 000074Acute pulmonary embolism in a child with ANCA-negative Idiopathic Pulmonary Capillaritis.
Auteurs : Ali A. Asseri [Oman] ; Yi Zeng ; Cori L. DainesSource :
- Saudi medical journal [ 0379-5284 ] ; 2019.
Descripteurs français
- KwdFr :
- Alvéoles pulmonaires, Anticorps anticytoplasme des polynucléaires neutrophiles, Douleur thoracique (étiologie), Embolie pulmonaire (diagnostic), Embolie pulmonaire (traitement médicamenteux), Embolie pulmonaire (étiologie), Enfant, Femelle, Humains, Hydroxychloroquine (administration et posologie), Hypoxie (étiologie), Hémorragie (étiologie), Héparine bas poids moléculaire (administration et posologie), Maladie aigüe, Maladies pulmonaires (étiologie), Poumon (), Prednisolone (administration et posologie), Résultat thérapeutique, Vaisseaux capillaires, Vascularite ().
- MESH :
- administration et posologie : Hydroxychloroquine, Héparine bas poids moléculaire, Prednisolone.
- diagnostic : Embolie pulmonaire.
- traitement médicamenteux : Embolie pulmonaire.
- étiologie : Douleur thoracique, Embolie pulmonaire, Hypoxie, Hémorragie, Maladies pulmonaires.
- Alvéoles pulmonaires, Anticorps anticytoplasme des polynucléaires neutrophiles, Enfant, Femelle, Humains, Maladie aigüe, Poumon, Résultat thérapeutique, Vaisseaux capillaires, Vascularite.
English descriptors
- KwdEn :
- Acute Disease, Antibodies, Antineutrophil Cytoplasmic, Capillaries, Chest Pain (etiology), Child, Female, Hemorrhage (etiology), Heparin, Low-Molecular-Weight (administration & dosage), Humans, Hydroxychloroquine (administration & dosage), Hypoxia (etiology), Lung (blood supply), Lung Diseases (etiology), Mercaptopurine (administration & dosage), Mercaptopurine (analogs & derivatives), Prednisolone (administration & dosage), Pulmonary Alveoli, Pulmonary Embolism (diagnosis), Pulmonary Embolism (drug therapy), Pulmonary Embolism (etiology), Treatment Outcome, Vasculitis (complications).
- MESH :
- chemical , administration & dosage : Heparin, Low-Molecular-Weight, Hydroxychloroquine, Mercaptopurine, Prednisolone.
- chemical , analogs & derivatives : Mercaptopurine.
- chemical : Antibodies, Antineutrophil Cytoplasmic.
- blood supply : Lung.
- complications : Vasculitis.
- diagnosis : Pulmonary Embolism.
- drug therapy : Pulmonary Embolism.
- etiology : Chest Pain, Hemorrhage, Hypoxia, Lung Diseases, Pulmonary Embolism.
- Acute Disease, Capillaries, Child, Female, Humans, Pulmonary Alveoli, Treatment Outcome.
Abstract
Diffuse alveolar hemorrhage is an uncommon and often fatal condition in children that is characterized by distinct histopathological etiologies. Herein, we discuss the case of an 11-year-old girl who presented with acute worsening of hypoxia and left-sided chest pain. The patient had lung biopsy-proven idiopathic pulmonary capillaritis and was being treated with prednisolone every alternate day, azathioprine, and hydroxychloroquine. A contrast-computed tomography (CT) scan of the chest showed an acute left lower-lobe pulmonary embolism. Negative results were obtained on a test for thrombophilia. In children, pulmonary embolism with anti-neutrophil cytoplasmic antibody-negative idiopathic pulmonary capillaritis is a rare clinical condition. The exact cause of thrombus formation in this case is unknown; however, obesity, immobility, and chronic systemic corticosteroid therapy probably played a role.
DOI: 10.15537/smj.2019.6.24210
PubMed: 31219497
Affiliations:
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pubmed:31219497Le document en format XML
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<author><name sortKey="Zeng, Yi" sort="Zeng, Yi" uniqKey="Zeng Y" first="Yi" last="Zeng">Yi Zeng</name>
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<author><name sortKey="Daines, Cori L" sort="Daines, Cori L" uniqKey="Daines C" first="Cori L" last="Daines">Cori L. Daines</name>
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<front><div type="abstract" xml:lang="en">Diffuse alveolar hemorrhage is an uncommon and often fatal condition in children that is characterized by distinct histopathological etiologies. Herein, we discuss the case of an 11-year-old girl who presented with acute worsening of hypoxia and left-sided chest pain. The patient had lung biopsy-proven idiopathic pulmonary capillaritis and was being treated with prednisolone every alternate day, azathioprine, and hydroxychloroquine. A contrast-computed tomography (CT) scan of the chest showed an acute left lower-lobe pulmonary embolism. Negative results were obtained on a test for thrombophilia. In children, pulmonary embolism with anti-neutrophil cytoplasmic antibody-negative idiopathic pulmonary capillaritis is a rare clinical condition. The exact cause of thrombus formation in this case is unknown; however, obesity, immobility, and chronic systemic corticosteroid therapy probably played a role.</div>
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