Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland
Identifieur interne : 000055 ( PascalFrancis/Checkpoint ); précédent : 000054; suivant : 000056Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland
Auteurs : R. Dinwiddie [Royaume-Uni] ; N. Sharief [Royaume-Uni] ; O. Crawford [Royaume-Uni]Source :
- Pediatric pulmonology [ 8755-6863 ] ; 2002.
Descripteurs français
- Pascal (Inist)
- Wicri :
- topic : Enfant.
English descriptors
- KwdEn :
Abstract
Interstitial lung disease (ILD) of unknown etiology in immunocompetent patients is rare in children. A national survey was carried out in the United Kingdom and Ireland over a 3-year period in order to identify prevalence, age distribution, histopathology, natural history of the illness, and response to current treatment. Forty-six cases were identified, including 29 males and 17 females. Seventy-six percent presented in the first year of life. Nine (16%) occurred within four families. Conventional treatment with pulsed methylprednisolone, prednisolone, or hydroxychloroquine, singly or in combination, resulted in an excellent response in 65% of cases. Seven children died (15%). The recurrence risk for further children within the same family to develop ILD is estimated to be approximately 10%. The prevalence rate of this condition in the United Kingdom and Ireland during the period of study for children aged 0-16 years is estimated to be 3.6 cases/million.
Affiliations:
Links toward previous steps (curation, corpus...)
Links to Exploration step
Pascal:02-0413454Le document en format XML
<record><TEI><teiHeader><fileDesc><titleStmt><title xml:lang="en" level="a">Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland</title>
<author><name sortKey="Dinwiddie, R" sort="Dinwiddie, R" uniqKey="Dinwiddie R" first="R." last="Dinwiddie">R. Dinwiddie</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Respiratory Unit, Great Ormond Street Hospital for Children</s1>
<s2>London</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<placeName><settlement type="city">Londres</settlement>
<region type="country">Angleterre</region>
<region type="région" nuts="1">Grand Londres</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Sharief, N" sort="Sharief, N" uniqKey="Sharief N" first="N." last="Sharief">N. Sharief</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Department of Pediatrics, Basildon Hospital</s1>
<s2>Basildon, Essex</s2>
<s3>GBR</s3>
<sZ>2 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<wicri:noRegion>Basildon, Essex</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Crawford, O" sort="Crawford, O" uniqKey="Crawford O" first="O." last="Crawford">O. Crawford</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Respiratory Unit, Great Ormond Street Hospital for Children</s1>
<s2>London</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<placeName><settlement type="city">Londres</settlement>
<region type="country">Angleterre</region>
<region type="région" nuts="1">Grand Londres</region>
</placeName>
</affiliation>
</author>
</titleStmt>
<publicationStmt><idno type="wicri:source">INIST</idno>
<idno type="inist">02-0413454</idno>
<date when="2002">2002</date>
<idno type="stanalyst">PASCAL 02-0413454 INIST</idno>
<idno type="RBID">Pascal:02-0413454</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">000052</idno>
<idno type="wicri:Area/PascalFrancis/Curation">000014</idno>
<idno type="wicri:Area/PascalFrancis/Checkpoint">000055</idno>
<idno type="wicri:explorRef" wicri:stream="PascalFrancis" wicri:step="Checkpoint">000055</idno>
</publicationStmt>
<sourceDesc><biblStruct><analytic><title xml:lang="en" level="a">Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland</title>
<author><name sortKey="Dinwiddie, R" sort="Dinwiddie, R" uniqKey="Dinwiddie R" first="R." last="Dinwiddie">R. Dinwiddie</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Respiratory Unit, Great Ormond Street Hospital for Children</s1>
<s2>London</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<placeName><settlement type="city">Londres</settlement>
<region type="country">Angleterre</region>
<region type="région" nuts="1">Grand Londres</region>
</placeName>
</affiliation>
</author>
<author><name sortKey="Sharief, N" sort="Sharief, N" uniqKey="Sharief N" first="N." last="Sharief">N. Sharief</name>
<affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Department of Pediatrics, Basildon Hospital</s1>
<s2>Basildon, Essex</s2>
<s3>GBR</s3>
<sZ>2 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<wicri:noRegion>Basildon, Essex</wicri:noRegion>
</affiliation>
</author>
<author><name sortKey="Crawford, O" sort="Crawford, O" uniqKey="Crawford O" first="O." last="Crawford">O. Crawford</name>
<affiliation wicri:level="3"><inist:fA14 i1="01"><s1>Respiratory Unit, Great Ormond Street Hospital for Children</s1>
<s2>London</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>3 aut.</sZ>
</inist:fA14>
<country>Royaume-Uni</country>
<placeName><settlement type="city">Londres</settlement>
<region type="country">Angleterre</region>
<region type="région" nuts="1">Grand Londres</region>
</placeName>
</affiliation>
</author>
</analytic>
<series><title level="j" type="main">Pediatric pulmonology</title>
<title level="j" type="abbreviated">Pediatr. pulmonol.</title>
<idno type="ISSN">8755-6863</idno>
<imprint><date when="2002">2002</date>
</imprint>
</series>
</biblStruct>
</sourceDesc>
<seriesStmt><title level="j" type="main">Pediatric pulmonology</title>
<title level="j" type="abbreviated">Pediatr. pulmonol.</title>
<idno type="ISSN">8755-6863</idno>
</seriesStmt>
</fileDesc>
<profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Child</term>
<term>Clinical form</term>
<term>Idiopathic</term>
<term>Interstitial pneumonitis</term>
<term>Prognosis</term>
<term>Treatment</term>
<term>United Kingdom</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr"><term>Pneumopathie interstitielle</term>
<term>Idiopathique</term>
<term>Royaume Uni</term>
<term>Forme clinique</term>
<term>Traitement</term>
<term>Pronostic</term>
<term>Enfant</term>
</keywords>
<keywords scheme="Wicri" type="topic" xml:lang="fr"><term>Enfant</term>
</keywords>
</textClass>
</profileDesc>
</teiHeader>
<front><div type="abstract" xml:lang="en">Interstitial lung disease (ILD) of unknown etiology in immunocompetent patients is rare in children. A national survey was carried out in the United Kingdom and Ireland over a 3-year period in order to identify prevalence, age distribution, histopathology, natural history of the illness, and response to current treatment. Forty-six cases were identified, including 29 males and 17 females. Seventy-six percent presented in the first year of life. Nine (16%) occurred within four families. Conventional treatment with pulsed methylprednisolone, prednisolone, or hydroxychloroquine, singly or in combination, resulted in an excellent response in 65% of cases. Seven children died (15%). The recurrence risk for further children within the same family to develop ILD is estimated to be approximately 10%. The prevalence rate of this condition in the United Kingdom and Ireland during the period of study for children aged 0-16 years is estimated to be 3.6 cases/million.</div>
</front>
</TEI>
<inist><standard h6="B"><pA><fA01 i1="01" i2="1"><s0>8755-6863</s0>
</fA01>
<fA02 i1="01"><s0>PEPUES</s0>
</fA02>
<fA03 i2="1"><s0>Pediatr. pulmonol.</s0>
</fA03>
<fA05><s2>34</s2>
</fA05>
<fA06><s2>1</s2>
</fA06>
<fA08 i1="01" i2="1" l="ENG"><s1>Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland</s1>
</fA08>
<fA11 i1="01" i2="1"><s1>DINWIDDIE (R.)</s1>
</fA11>
<fA11 i1="02" i2="1"><s1>SHARIEF (N.)</s1>
</fA11>
<fA11 i1="03" i2="1"><s1>CRAWFORD (O.)</s1>
</fA11>
<fA14 i1="01"><s1>Respiratory Unit, Great Ormond Street Hospital for Children</s1>
<s2>London</s2>
<s3>GBR</s3>
<sZ>1 aut.</sZ>
<sZ>3 aut.</sZ>
</fA14>
<fA14 i1="02"><s1>Department of Pediatrics, Basildon Hospital</s1>
<s2>Basildon, Essex</s2>
<s3>GBR</s3>
<sZ>2 aut.</sZ>
</fA14>
<fA20><s1>23-29</s1>
</fA20>
<fA21><s1>2002</s1>
</fA21>
<fA23 i1="01"><s0>ENG</s0>
</fA23>
<fA43 i1="01"><s1>INIST</s1>
<s2>21407</s2>
<s5>354000108747180040</s5>
</fA43>
<fA44><s0>0000</s0>
<s1>© 2002 INIST-CNRS. All rights reserved.</s1>
</fA44>
<fA45><s0>21 ref.</s0>
</fA45>
<fA47 i1="01" i2="1"><s0>02-0413454</s0>
</fA47>
<fA60><s1>P</s1>
</fA60>
<fA61><s0>A</s0>
</fA61>
<fA64 i1="01" i2="1"><s0>Pediatric pulmonology</s0>
</fA64>
<fA66 i1="01"><s0>USA</s0>
</fA66>
<fC01 i1="01" l="ENG"><s0>Interstitial lung disease (ILD) of unknown etiology in immunocompetent patients is rare in children. A national survey was carried out in the United Kingdom and Ireland over a 3-year period in order to identify prevalence, age distribution, histopathology, natural history of the illness, and response to current treatment. Forty-six cases were identified, including 29 males and 17 females. Seventy-six percent presented in the first year of life. Nine (16%) occurred within four families. Conventional treatment with pulsed methylprednisolone, prednisolone, or hydroxychloroquine, singly or in combination, resulted in an excellent response in 65% of cases. Seven children died (15%). The recurrence risk for further children within the same family to develop ILD is estimated to be approximately 10%. The prevalence rate of this condition in the United Kingdom and Ireland during the period of study for children aged 0-16 years is estimated to be 3.6 cases/million.</s0>
</fC01>
<fC02 i1="01" i2="X"><s0>002B11D</s0>
</fC02>
<fC03 i1="01" i2="X" l="FRE"><s0>Pneumopathie interstitielle</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="ENG"><s0>Interstitial pneumonitis</s0>
<s5>01</s5>
</fC03>
<fC03 i1="01" i2="X" l="SPA"><s0>Neumopatía intersticial</s0>
<s5>01</s5>
</fC03>
<fC03 i1="02" i2="X" l="FRE"><s0>Idiopathique</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="ENG"><s0>Idiopathic</s0>
<s5>02</s5>
</fC03>
<fC03 i1="02" i2="X" l="SPA"><s0>Idiopático</s0>
<s5>02</s5>
</fC03>
<fC03 i1="03" i2="X" l="FRE"><s0>Royaume Uni</s0>
<s2>NG</s2>
<s5>04</s5>
</fC03>
<fC03 i1="03" i2="X" l="ENG"><s0>United Kingdom</s0>
<s2>NG</s2>
<s5>04</s5>
</fC03>
<fC03 i1="03" i2="X" l="SPA"><s0>Reino Unido</s0>
<s2>NG</s2>
<s5>04</s5>
</fC03>
<fC03 i1="04" i2="X" l="FRE"><s0>Forme clinique</s0>
<s5>17</s5>
</fC03>
<fC03 i1="04" i2="X" l="ENG"><s0>Clinical form</s0>
<s5>17</s5>
</fC03>
<fC03 i1="04" i2="X" l="SPA"><s0>Forma clínica</s0>
<s5>17</s5>
</fC03>
<fC03 i1="05" i2="X" l="FRE"><s0>Traitement</s0>
<s5>18</s5>
</fC03>
<fC03 i1="05" i2="X" l="ENG"><s0>Treatment</s0>
<s5>18</s5>
</fC03>
<fC03 i1="05" i2="X" l="SPA"><s0>Tratamiento</s0>
<s5>18</s5>
</fC03>
<fC03 i1="06" i2="X" l="FRE"><s0>Pronostic</s0>
<s5>19</s5>
</fC03>
<fC03 i1="06" i2="X" l="ENG"><s0>Prognosis</s0>
<s5>19</s5>
</fC03>
<fC03 i1="06" i2="X" l="SPA"><s0>Pronóstico</s0>
<s5>19</s5>
</fC03>
<fC03 i1="07" i2="X" l="FRE"><s0>Enfant</s0>
<s5>20</s5>
</fC03>
<fC03 i1="07" i2="X" l="ENG"><s0>Child</s0>
<s5>20</s5>
</fC03>
<fC03 i1="07" i2="X" l="SPA"><s0>Niño</s0>
<s5>20</s5>
</fC03>
<fC07 i1="01" i2="X" l="FRE"><s0>Europe</s0>
<s2>NG</s2>
</fC07>
<fC07 i1="01" i2="X" l="ENG"><s0>Europe</s0>
<s2>NG</s2>
</fC07>
<fC07 i1="01" i2="X" l="SPA"><s0>Europa</s0>
<s2>NG</s2>
</fC07>
<fC07 i1="02" i2="X" l="FRE"><s0>Homme</s0>
</fC07>
<fC07 i1="02" i2="X" l="ENG"><s0>Human</s0>
</fC07>
<fC07 i1="02" i2="X" l="SPA"><s0>Hombre</s0>
</fC07>
<fC07 i1="03" i2="X" l="FRE"><s0>Appareil respiratoire pathologie</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="ENG"><s0>Respiratory disease</s0>
<s5>37</s5>
</fC07>
<fC07 i1="03" i2="X" l="SPA"><s0>Aparato respiratorio patología</s0>
<s5>37</s5>
</fC07>
<fC07 i1="04" i2="X" l="FRE"><s0>Poumon pathologie</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="ENG"><s0>Lung disease</s0>
<s5>38</s5>
</fC07>
<fC07 i1="04" i2="X" l="SPA"><s0>Pulmón patología</s0>
<s5>38</s5>
</fC07>
<fN21><s1>238</s1>
</fN21>
<fN82><s1>PSI</s1>
</fN82>
</pA>
</standard>
</inist>
<affiliations><list><country><li>Royaume-Uni</li>
</country>
<region><li>Angleterre</li>
<li>Grand Londres</li>
</region>
<settlement><li>Londres</li>
</settlement>
</list>
<tree><country name="Royaume-Uni"><region name="Angleterre"><name sortKey="Dinwiddie, R" sort="Dinwiddie, R" uniqKey="Dinwiddie R" first="R." last="Dinwiddie">R. Dinwiddie</name>
</region>
<name sortKey="Crawford, O" sort="Crawford, O" uniqKey="Crawford O" first="O." last="Crawford">O. Crawford</name>
<name sortKey="Sharief, N" sort="Sharief, N" uniqKey="Sharief N" first="N." last="Sharief">N. Sharief</name>
</country>
</tree>
</affiliations>
</record>
Pour manipuler ce document sous Unix (Dilib)
EXPLOR_STEP=$WICRI_ROOT/Sante/explor/ChloroquineV1/Data/PascalFrancis/Checkpoint
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 000055 | SxmlIndent | more
Ou
HfdSelect -h $EXPLOR_AREA/Data/PascalFrancis/Checkpoint/biblio.hfd -nk 000055 | SxmlIndent | more
Pour mettre un lien sur cette page dans le réseau Wicri
{{Explor lien |wiki= Sante |area= ChloroquineV1 |flux= PascalFrancis |étape= Checkpoint |type= RBID |clé= Pascal:02-0413454 |texte= Idiopathic interstitial pneumonitis in children: A national survey in the United Kingdom and Ireland }}
This area was generated with Dilib version V0.6.33. |