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Idiopathic pulmonary hemosiderosis.

Identifieur interne : 000016 ( Ncbi/Curation ); précédent : 000015; suivant : 000017

Idiopathic pulmonary hemosiderosis.

Auteurs : T. Dua ; J. Chandra ; M. Jain ; S M Passah ; A K Dutta

Source :

RBID : pubmed:11028126

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Abstract

Two cases of idiopathic pulmonary hemosiderosis in children are reported. Both cases presented with a combination of acute/recurrent respiratory symptoms along with iron deficiency anemia. In one case diagnosis was delayed for 18 months after onset of symptoms. After initial stabilisation with corticosteroid therapy, both cases were put on chloroquine therapy and showed improvement. Various other forms of therapy and outcome are discussed. It is suggested that in cases with recurrent respiratory symptoms, idiopathic pulmonary hemosiderosis should also be considered after excluding infectious etiology.

DOI: 10.1007/bf02762188
PubMed: 11028126

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pubmed:11028126

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T. Dua
<affiliation>
<nlm:affiliation>Department of Pediatrics, Lady Hardinge Medical College, New Delhi.</nlm:affiliation>
<wicri:noCountry code="subField">New Delhi</wicri:noCountry>
</affiliation>

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<term>Female</term>
<term>Hemosiderosis (diagnosis)</term>
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<term>Hormones corticosurrénaliennes (usage thérapeutique)</term>
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<term>Hémosidérose (diagnostic)</term>
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<term>Hemosiderosis</term>
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<div type="abstract" xml:lang="en">Two cases of idiopathic pulmonary hemosiderosis in children are reported. Both cases presented with a combination of acute/recurrent respiratory symptoms along with iron deficiency anemia. In one case diagnosis was delayed for 18 months after onset of symptoms. After initial stabilisation with corticosteroid therapy, both cases were put on chloroquine therapy and showed improvement. Various other forms of therapy and outcome are discussed. It is suggested that in cases with recurrent respiratory symptoms, idiopathic pulmonary hemosiderosis should also be considered after excluding infectious etiology.</div>
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