Dermatomyositis: An Acute Flare and Current Treatments
Identifieur interne : 000731 ( Ncbi/Checkpoint ); précédent : 000730; suivant : 000732Dermatomyositis: An Acute Flare and Current Treatments
Auteurs : John Okogbaa [États-Unis] ; Lakeasha Batiste [États-Unis]Source :
- Clinical Medicine Insights. Case Reports [ 1179-5476 ] ; 2019.
Abstract
The purpose of this case report is to assess and review the literature to determine the frequency of occurrence of dermatomyositis (DM). Dermatomyositis is a rare autoimmune condition that disproportionately affects adolescence and pediatric patients. The symptomatology experienced in this condition includes but not limited to fatigue, reduced mobility, and dysphagia. Symptoms of dysphonia and dyspnea have been reported due to weakened esophageal and respiratory muscle. Another major complication seen in DM is calcinosis. Calcinosis is a calcium deposit on soft tissue. This is mostly been attributed to late diagnosis or use of ineffective treatment regimen. Systemic corticosteroid is the first-line treatment for DM; however, other agents such as anti-malaria, IVIG, and immunosuppressive therapies have been used successfully.
Url:
DOI: 10.1177/1179547619855370
PubMed: 31244526
PubMed Central: 6582284
Affiliations:
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<front><div type="abstract" xml:lang="en"><p>The purpose of this case report is to assess and review the literature to determine the frequency of occurrence of dermatomyositis (DM). Dermatomyositis is a rare autoimmune condition that disproportionately affects adolescence and pediatric patients. The symptomatology experienced in this condition includes but not limited to fatigue, reduced mobility, and dysphagia. Symptoms of dysphonia and dyspnea have been reported due to weakened esophageal and respiratory muscle. Another major complication seen in DM is calcinosis. Calcinosis is a calcium deposit on soft tissue. This is mostly been attributed to late diagnosis or use of ineffective treatment regimen. Systemic corticosteroid is the first-line treatment for DM; however, other agents such as anti-malaria, IVIG, and immunosuppressive therapies have been used successfully.</p>
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