Idiopathic pulmonary haemosiderosis in a child with Down's syndrome: case report and review of the literature.
Identifieur interne : 001305 ( Main/Curation ); précédent : 001304; suivant : 001306Idiopathic pulmonary haemosiderosis in a child with Down's syndrome: case report and review of the literature.
Auteurs : A. Aceti [Italie] ; R. Sciutti ; P R Bracci ; L. Bertelli ; F. Melchionda ; S. CazzatoSource :
- Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG [ 1124-0490 ] ; 2012.
Descripteurs français
- KwdFr :
- Enfant d'âge préscolaire, Femelle, Humains, Hydroxychloroquine (usage thérapeutique), Hémosidérose (), Hémosidérose (diagnostic), Hémosidérose (traitement médicamenteux), Maladies pulmonaires (), Maladies pulmonaires (diagnostic), Maladies pulmonaires (traitement médicamenteux), Résultat thérapeutique, Syndrome de Down (), Tomodensitométrie, Valeur prédictive des tests.
- MESH :
- diagnostic : Hémosidérose, Maladies pulmonaires.
- traitement médicamenteux : Hémosidérose, Maladies pulmonaires.
- usage thérapeutique : Hydroxychloroquine.
- Enfant d'âge préscolaire, Femelle, Humains, Hémosidérose, Maladies pulmonaires, Résultat thérapeutique, Syndrome de Down, Tomodensitométrie, Valeur prédictive des tests.
English descriptors
- KwdEn :
- Child, Preschool, Down Syndrome (complications), Female, Hemosiderosis (complications), Hemosiderosis (diagnosis), Hemosiderosis (drug therapy), Humans, Hydroxychloroquine (therapeutic use), Lung Diseases (complications), Lung Diseases (diagnosis), Lung Diseases (drug therapy), Predictive Value of Tests, Tomography, X-Ray Computed, Treatment Outcome.
- MESH :
- chemical , therapeutic use : Hydroxychloroquine.
- complications : Down Syndrome, Hemosiderosis, Lung Diseases.
- diagnosis : Hemosiderosis, Lung Diseases.
- drug therapy : Hemosiderosis, Lung Diseases.
- Child, Preschool, Female, Humans, Predictive Value of Tests, Tomography, X-Ray Computed, Treatment Outcome.
Abstract
We report the case of a female child with Down's syndrome affected by idiopathic pulmonary haemosiderosis (IPH), who was successfully treated with hydroxychloroquine. First-line conventional treatment of IPH is traditionally based on systemic corticosteroids; however, many steroid-sparing agents are being increasingly used as adjuncts to corticosteroids in children with recurrent or refractory bleeding. The use of these drugs is particularly promising for maintenance treatment, because it tends to avoid the adverse effects of long-term corticosteroids.
PubMed: 23311126
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pubmed:23311126Le document en format XML
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<term>Hemosiderosis (complications)</term>
<term>Hemosiderosis (diagnosis)</term>
<term>Hemosiderosis (drug therapy)</term>
<term>Humans</term>
<term>Hydroxychloroquine (therapeutic use)</term>
<term>Lung Diseases (complications)</term>
<term>Lung Diseases (diagnosis)</term>
<term>Lung Diseases (drug therapy)</term>
<term>Predictive Value of Tests</term>
<term>Tomography, X-Ray Computed</term>
<term>Treatment Outcome</term>
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<term>Femelle</term>
<term>Humains</term>
<term>Hydroxychloroquine (usage thérapeutique)</term>
<term>Hémosidérose ()</term>
<term>Hémosidérose (diagnostic)</term>
<term>Hémosidérose (traitement médicamenteux)</term>
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<term>Maladies pulmonaires (diagnostic)</term>
<term>Maladies pulmonaires (traitement médicamenteux)</term>
<term>Résultat thérapeutique</term>
<term>Syndrome de Down ()</term>
<term>Tomodensitométrie</term>
<term>Valeur prédictive des tests</term>
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<term>Hemosiderosis</term>
<term>Lung Diseases</term>
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<term>Lung Diseases</term>
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<term>Maladies pulmonaires</term>
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<term>Lung Diseases</term>
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<term>Maladies pulmonaires</term>
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<term>Tomography, X-Ray Computed</term>
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<term>Femelle</term>
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<term>Maladies pulmonaires</term>
<term>Résultat thérapeutique</term>
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<term>Tomodensitométrie</term>
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<front><div type="abstract" xml:lang="en">We report the case of a female child with Down's syndrome affected by idiopathic pulmonary haemosiderosis (IPH), who was successfully treated with hydroxychloroquine. First-line conventional treatment of IPH is traditionally based on systemic corticosteroids; however, many steroid-sparing agents are being increasingly used as adjuncts to corticosteroids in children with recurrent or refractory bleeding. The use of these drugs is particularly promising for maintenance treatment, because it tends to avoid the adverse effects of long-term corticosteroids.</div>
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