Pulmonary amyloidosis in Sjögren’s syndrome: a rare diagnosis for nodular lung lesions
Identifieur interne : 000E22 ( Istex/Curation ); précédent : 000E21; suivant : 000E23Pulmonary amyloidosis in Sjögren’s syndrome: a rare diagnosis for nodular lung lesions
Auteurs : Kenia Rodrigues ; Fabricio S. Neves ; Karin B. L. Stoeterau ; Gláucio R. Werner Castro ; Luiz F. Nobre [Brésil] ; Adriana F. Zimmermann ; Ivânio A. PereiraSource :
- International Journal of Rheumatic Diseases [ 1756-1841 ] ; 2009-12.
Abstract
Lung involvement in Sjögren’s syndrome (SS) can affect trachea, bronchus, small airways, pleura and may cause interstitial lung injury. It may also be associated with malignancies, particularly non‐Hodgkin’s lymphoma, which is a well‐recognized complication of this disease. Here we describe the occurrence of localized amyloidosis presenting as pulmonary nodules in a patient with newly diagnosed SS. We highlight this rare occurrence as a diagnostic possibility that should be considered in the evaluation of pulmonary involvement in this disease.
Url:
DOI: 10.1111/j.1756-185X.2009.01436.x
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Kenia Rodrigues<affiliation><mods:affiliation>Rheumatology Division, Federal University of Santa Catarina (UFSC)</mods:affiliation>
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<affiliation><mods:affiliation>Hematology and Hemotherapy Center of Santa Catarina (HEMOSC)</mods:affiliation>
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<front><div type="abstract" xml:lang="en">Lung involvement in Sjögren’s syndrome (SS) can affect trachea, bronchus, small airways, pleura and may cause interstitial lung injury. It may also be associated with malignancies, particularly non‐Hodgkin’s lymphoma, which is a well‐recognized complication of this disease. Here we describe the occurrence of localized amyloidosis presenting as pulmonary nodules in a patient with newly diagnosed SS. We highlight this rare occurrence as a diagnostic possibility that should be considered in the evaluation of pulmonary involvement in this disease.</div>
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