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Pulmonary amyloidosis in Sjögren’s syndrome: a rare diagnosis for nodular lung lesions

Identifieur interne : 000E22 ( Istex/Curation ); précédent : 000E21; suivant : 000E23

Pulmonary amyloidosis in Sjögren’s syndrome: a rare diagnosis for nodular lung lesions

Auteurs : Kenia Rodrigues ; Fabricio S. Neves ; Karin B. L. Stoeterau ; Gláucio R. Werner Castro ; Luiz F. Nobre [Brésil] ; Adriana F. Zimmermann ; Ivânio A. Pereira

Source :

RBID : ISTEX:E4A308EA499A360FDCFE78E1F7D85D1ACB893C5F

Abstract

Lung involvement in Sjögren’s syndrome (SS) can affect trachea, bronchus, small airways, pleura and may cause interstitial lung injury. It may also be associated with malignancies, particularly non‐Hodgkin’s lymphoma, which is a well‐recognized complication of this disease. Here we describe the occurrence of localized amyloidosis presenting as pulmonary nodules in a patient with newly diagnosed SS. We highlight this rare occurrence as a diagnostic possibility that should be considered in the evaluation of pulmonary involvement in this disease.

Url:
DOI: 10.1111/j.1756-185X.2009.01436.x

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ISTEX:E4A308EA499A360FDCFE78E1F7D85D1ACB893C5F

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Kenia Rodrigues
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Fabricio S. Neves
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Karin B. L. Stoeterau
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Gláucio R. Werner Castro
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Adriana F. Zimmermann
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Ivânio A. Pereira
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