Interstitial lung disease in infancy: A general approach
Identifieur interne : 000569 ( Istex/Curation ); précédent : 000568; suivant : 000570Interstitial lung disease in infancy: A general approach
Auteurs : Erica J. Hines [Australie] ; Mark Walsh [Australie] ; Jane E. Armes [Australie] ; Tonia Douglas [Australie] ; Jasneek Chawla [Australie]Source :
- Journal of Paediatrics and Child Health [ 1034-4810 ] ; 2016-04.
Abstract
Childhood Interstitial lung disease (chILD) is an umbrella term used to define a broad range of rare, diffuse pulmonary disorders with altered interstitial structure that leads to abnormal gas exchange. Presentation of chILD in infancy can be difficult to differentiate from other common causes of diffuse lung disease. This article aimed at paediatricians provides an overview of interstitial lung disease presenting in infancy and includes key clinical features, a suggested approach to investigation and a summary of management. An overview of three clinical cases has been included to demonstrate the diagnostic approach, characteristic investigation findings and varied clinical outcomes.
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DOI: 10.1111/jpc.13162
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<front><div type="abstract">Childhood Interstitial lung disease (chILD) is an umbrella term used to define a broad range of rare, diffuse pulmonary disorders with altered interstitial structure that leads to abnormal gas exchange. Presentation of chILD in infancy can be difficult to differentiate from other common causes of diffuse lung disease. This article aimed at paediatricians provides an overview of interstitial lung disease presenting in infancy and includes key clinical features, a suggested approach to investigation and a summary of management. An overview of three clinical cases has been included to demonstrate the diagnostic approach, characteristic investigation findings and varied clinical outcomes.</div>
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