Motor features in posterior cortical atrophy and their imaging correlates☆
Identifieur interne : 000254 ( Ncbi/Checkpoint ); précédent : 000253; suivant : 000255Motor features in posterior cortical atrophy and their imaging correlates☆
Auteurs : Natalie S. Ryan [Royaume-Uni] ; Timothy J. Shakespeare [Royaume-Uni] ; Manja Lehmann [Royaume-Uni] ; Shiva Keihaninejad [Royaume-Uni] ; Jennifer M. Nicholas [Royaume-Uni] ; Kelvin K. Leung [Royaume-Uni] ; Nick C. Fox [Royaume-Uni] ; Sebastian J. Crutch [Royaume-Uni]Source :
- Neurobiology of Aging [ 0197-4580 ] ; 2014.
Abstract
Posterior cortical atrophy (PCA) is a neurodegenerative syndrome characterized by impaired higher visual processing skills; however, motor features more commonly associated with corticobasal syndrome may also occur. We investigated the frequency and clinical characteristics of motor features in 44 PCA patients and, with 30 controls, conducted voxel-based morphometry, cortical thickness, and subcortical volumetric analyses of their magnetic resonance imaging. Prominent limb rigidity was used to define a PCA-motor subgroup. A total of 30% (13) had PCA-motor; all demonstrating asymmetrical left upper limb rigidity. Limb apraxia was more frequent and asymmetrical in PCA-motor, as was myoclonus. Tremor and alien limb phenomena only occurred in this subgroup. The subgroups did not differ in neuropsychological test performance or apolipoprotein E4 allele frequency. Greater asymmetry of atrophy occurred in PCA-motor, particularly involving right frontoparietal and peri-rolandic cortices, putamen, and thalamus. The 9 patients (including 4 PCA-motor) with pathology or cerebrospinal fluid all showed evidence of Alzheimer's disease. Our data suggest that PCA patients with motor features have greater atrophy of contralateral sensorimotor areas but are still likely to have underlying Alzheimer's disease.
Url:
DOI: 10.1016/j.neurobiolaging.2014.05.028
PubMed: 25086839
PubMed Central: 4236588
Affiliations:
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<front><div type="abstract" xml:lang="en"><p>Posterior cortical atrophy (PCA) is a neurodegenerative syndrome characterized by impaired higher visual processing skills; however, motor features more commonly associated with corticobasal syndrome may also occur. We investigated the frequency and clinical characteristics of motor features in 44 PCA patients and, with 30 controls, conducted voxel-based morphometry, cortical thickness, and subcortical volumetric analyses of their magnetic resonance imaging. Prominent limb rigidity was used to define a PCA-motor subgroup. A total of 30% (13) had PCA-motor; all demonstrating asymmetrical left upper limb rigidity. Limb apraxia was more frequent and asymmetrical in PCA-motor, as was myoclonus. Tremor and alien limb phenomena only occurred in this subgroup. The subgroups did not differ in neuropsychological test performance or apolipoprotein E4 allele frequency. Greater asymmetry of atrophy occurred in PCA-motor, particularly involving right frontoparietal and peri-rolandic cortices, putamen, and thalamus. The 9 patients (including 4 PCA-motor) with pathology or cerebrospinal fluid all showed evidence of Alzheimer's disease. Our data suggest that PCA patients with motor features have greater atrophy of contralateral sensorimotor areas but are still likely to have underlying Alzheimer's disease.</p>
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</div1>
</back>
</TEI>
<affiliations><list><country><li>Royaume-Uni</li>
</country>
<region><li>Angleterre</li>
<li>Grand Londres</li>
</region>
<settlement><li>Londres</li>
</settlement>
<orgName><li>University College de Londres</li>
</orgName>
</list>
<tree><country name="Royaume-Uni"><region name="Angleterre"><name sortKey="Ryan, Natalie S" sort="Ryan, Natalie S" uniqKey="Ryan N" first="Natalie S." last="Ryan">Natalie S. Ryan</name>
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<name sortKey="Fox, Nick C" sort="Fox, Nick C" uniqKey="Fox N" first="Nick C." last="Fox">Nick C. Fox</name>
<name sortKey="Keihaninejad, Shiva" sort="Keihaninejad, Shiva" uniqKey="Keihaninejad S" first="Shiva" last="Keihaninejad">Shiva Keihaninejad</name>
<name sortKey="Lehmann, Manja" sort="Lehmann, Manja" uniqKey="Lehmann M" first="Manja" last="Lehmann">Manja Lehmann</name>
<name sortKey="Leung, Kelvin K" sort="Leung, Kelvin K" uniqKey="Leung K" first="Kelvin K." last="Leung">Kelvin K. Leung</name>
<name sortKey="Nicholas, Jennifer M" sort="Nicholas, Jennifer M" uniqKey="Nicholas J" first="Jennifer M." last="Nicholas">Jennifer M. Nicholas</name>
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</country>
</tree>
</affiliations>
</record>
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