[Segmental aganglionosis of the small intestine--myth or reality? (A case report)].
Identifieur interne : 000A78 ( PubMed/Corpus ); précédent : 000A77; suivant : 000A79[Segmental aganglionosis of the small intestine--myth or reality? (A case report)].
Auteurs : R. Gonzalez-Vasquez ; W H HeissSource :
- Zeitschrift fur Kinderchirurgie : organ der Deutschen, der Schweizerischen und der Osterreichischen Gesellschaft fur Kinderchirurgie = Surgery in infancy and childhood [ 0174-3082 ] ; 1988.
English descriptors
- KwdEn :
- MESH :
- pathology : Hirschsprung Disease, Intestine, Small.
- surgery : Hirschsprung Disease, Intestine, Small.
- Follow-Up Studies, Humans, Infant, Male, Reoperation.
Abstract
Reports on zonal aganglionosis of the bowel are very rare and the few cases reported concern colon and rectum. We present a case of segmental aganglionosis of the jejunum in a 2-months-old boy. He had to be operated upon twice because of an ileus of the short bowel. At the second operation, a 10 cm long narrow segment of the jejunum was resected. The histological examination revealed a segmental aganglionosis of the plexus myentericus. Possible causes of this rare zonal aganglionosis could be: 1. Local damage of the plexus myentericus through anoxia. 2. Primary abnormity in the gastrointestinal anlage. 3. An intrauterine inflammation. 4. A double migration and development gradient of the precursors of the neuroblasts, from each end to the middle of the gut. A defect in the microenvironment of the enteric neurons would result in their failure in differentiation. This possible explanation would challenge the accepted theory of pathogenesis of colonic aganglionosis.
DOI: 10.1055/s-2008-1043501
PubMed: 3239256
Links to Exploration step
pubmed:3239256Le document en format XML
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Gonzalez-Vasquez</name><affiliation><nlm:affiliation>Kinderchirurgische Abteilung, Mutterhaus der Borromäerinnen, Trier.</nlm:affiliation></affiliation></author><author><name sortKey="Heiss, W H" sort="Heiss, W H" uniqKey="Heiss W" first="W H" last="Heiss">W H Heiss</name></author></titleStmt><publicationStmt><idno type="wicri:source">PubMed</idno><date when="1988">1988</date><idno type="RBID">pubmed:3239256</idno><idno type="pmid">3239256</idno><idno type="doi">10.1055/s-2008-1043501</idno><idno type="wicri:Area/PubMed/Corpus">000A78</idno><idno type="wicri:explorRef" wicri:stream="PubMed" wicri:step="Corpus" wicri:corpus="PubMed">000A78</idno></publicationStmt><sourceDesc><biblStruct><analytic><title xml:lang="en">[Segmental aganglionosis of the small intestine--myth or reality? (A case report)].</title><author><name sortKey="Gonzalez Vasquez, R" sort="Gonzalez Vasquez, R" uniqKey="Gonzalez Vasquez R" first="R" last="Gonzalez-Vasquez">R. Gonzalez-Vasquez</name><affiliation><nlm:affiliation>Kinderchirurgische Abteilung, Mutterhaus der Borromäerinnen, Trier.</nlm:affiliation></affiliation></author><author><name sortKey="Heiss, W H" sort="Heiss, W H" uniqKey="Heiss W" first="W H" last="Heiss">W H Heiss</name></author></analytic><series><title level="j">Zeitschrift fur Kinderchirurgie : organ der Deutschen, der Schweizerischen und der Osterreichischen Gesellschaft fur Kinderchirurgie = Surgery in infancy and childhood</title><idno type="ISSN">0174-3082</idno><imprint><date when="1988" type="published">1988</date></imprint></series></biblStruct></sourceDesc></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Follow-Up Studies</term><term>Hirschsprung Disease (pathology)</term><term>Hirschsprung Disease (surgery)</term><term>Humans</term><term>Infant</term><term>Intestine, Small (pathology)</term><term>Intestine, Small (surgery)</term><term>Male</term><term>Reoperation</term></keywords><keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Hirschsprung Disease</term><term>Intestine, Small</term></keywords><keywords scheme="MESH" qualifier="surgery" xml:lang="en"><term>Hirschsprung Disease</term><term>Intestine, Small</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Follow-Up Studies</term><term>Humans</term><term>Infant</term><term>Male</term><term>Reoperation</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Reports on zonal aganglionosis of the bowel are very rare and the few cases reported concern colon and rectum. We present a case of segmental aganglionosis of the jejunum in a 2-months-old boy. He had to be operated upon twice because of an ileus of the short bowel. At the second operation, a 10 cm long narrow segment of the jejunum was resected. The histological examination revealed a segmental aganglionosis of the plexus myentericus. Possible causes of this rare zonal aganglionosis could be: 1. Local damage of the plexus myentericus through anoxia. 2. Primary abnormity in the gastrointestinal anlage. 3. An intrauterine inflammation. 4. A double migration and development gradient of the precursors of the neuroblasts, from each end to the middle of the gut. A defect in the microenvironment of the enteric neurons would result in their failure in differentiation. This possible explanation would challenge the accepted theory of pathogenesis of colonic aganglionosis.</div></front></TEI><pubmed><MedlineCitation Status="MEDLINE" Owner="NLM"><PMID Version="1">3239256</PMID><DateCreated><Year>1989</Year><Month>05</Month><Day>05</Day></DateCreated><DateCompleted><Year>1989</Year><Month>05</Month><Day>05</Day></DateCompleted><DateRevised><Year>2006</Year><Month>11</Month><Day>15</Day></DateRevised><Article PubModel="Print"><Journal><ISSN IssnType="Print">0174-3082</ISSN><JournalIssue CitedMedium="Print"><Volume>43</Volume><Issue>6</Issue><PubDate><Year>1988</Year><Month>Dec</Month></PubDate></JournalIssue><Title>Zeitschrift fur Kinderchirurgie : organ der Deutschen, der Schweizerischen und der Osterreichischen Gesellschaft fur Kinderchirurgie = Surgery in infancy and childhood</Title><ISOAbbreviation>Z Kinderchir</ISOAbbreviation></Journal><ArticleTitle>[Segmental aganglionosis of the small intestine--myth or reality? (A case report)].</ArticleTitle><Pagination><MedlinePgn>424-6</MedlinePgn></Pagination><Abstract><AbstractText>Reports on zonal aganglionosis of the bowel are very rare and the few cases reported concern colon and rectum. We present a case of segmental aganglionosis of the jejunum in a 2-months-old boy. He had to be operated upon twice because of an ileus of the short bowel. At the second operation, a 10 cm long narrow segment of the jejunum was resected. The histological examination revealed a segmental aganglionosis of the plexus myentericus. Possible causes of this rare zonal aganglionosis could be: 1. Local damage of the plexus myentericus through anoxia. 2. Primary abnormity in the gastrointestinal anlage. 3. An intrauterine inflammation. 4. A double migration and development gradient of the precursors of the neuroblasts, from each end to the middle of the gut. A defect in the microenvironment of the enteric neurons would result in their failure in differentiation. This possible explanation would challenge the accepted theory of pathogenesis of colonic aganglionosis.</AbstractText></Abstract><AuthorList CompleteYN="Y"><Author ValidYN="Y"><LastName>Gonzalez-Vasquez</LastName><ForeName>R</ForeName><Initials>R</Initials><AffiliationInfo><Affiliation>Kinderchirurgische Abteilung, Mutterhaus der Borromäerinnen, Trier.</Affiliation></AffiliationInfo></Author><Author ValidYN="Y"><LastName>Heiss</LastName><ForeName>W H</ForeName><Initials>WH</Initials></Author></AuthorList><Language>ger</Language><PublicationTypeList><PublicationType UI="D002363">Case Reports</PublicationType><PublicationType UI="D004740">English Abstract</PublicationType><PublicationType UI="D016428">Journal Article</PublicationType></PublicationTypeList><VernacularTitle>Segmentale Aganglionose des Dünndarms--Mythos oder Wirklichkeit? (Eine Falldarstellung).</VernacularTitle></Article><MedlineJournalInfo><Country>Germany</Country><MedlineTA>Z Kinderchir</MedlineTA><NlmUniqueID>8103794</NlmUniqueID><ISSNLinking>0174-3082</ISSNLinking></MedlineJournalInfo><CitationSubset>IM</CitationSubset><MeshHeadingList><MeshHeading><DescriptorName UI="D005500" MajorTopicYN="N">Follow-Up Studies</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D006627" MajorTopicYN="N">Hirschsprung Disease</DescriptorName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName><QualifierName UI="Q000601" MajorTopicYN="Y">surgery</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D006801" MajorTopicYN="N">Humans</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D007223" MajorTopicYN="N">Infant</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D007421" MajorTopicYN="N">Intestine, Small</DescriptorName><QualifierName UI="Q000473" MajorTopicYN="N">pathology</QualifierName><QualifierName UI="Q000601" MajorTopicYN="Y">surgery</QualifierName></MeshHeading><MeshHeading><DescriptorName UI="D008297" MajorTopicYN="N">Male</DescriptorName></MeshHeading><MeshHeading><DescriptorName UI="D012086" MajorTopicYN="N">Reoperation</DescriptorName></MeshHeading></MeshHeadingList></MedlineCitation><PubmedData><History><PubMedPubDate PubStatus="pubmed"><Year>1988</Year><Month>12</Month><Day>1</Day></PubMedPubDate><PubMedPubDate PubStatus="medline"><Year>1988</Year><Month>12</Month><Day>1</Day><Hour>0</Hour><Minute>1</Minute></PubMedPubDate><PubMedPubDate PubStatus="entrez"><Year>1988</Year><Month>12</Month><Day>1</Day><Hour>0</Hour><Minute>0</Minute></PubMedPubDate></History><PublicationStatus>ppublish</PublicationStatus><ArticleIdList><ArticleId IdType="pubmed">3239256</ArticleId><ArticleId IdType="doi">10.1055/s-2008-1043501</ArticleId></ArticleIdList></PubmedData></pubmed></record>Pour manipuler ce document sous Unix (Dilib)
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