[Thrombosed scapular intramuscular venous malformation: A pediatric case report].
Identifieur interne : 000077 ( PubMed/Corpus ); précédent : 000076; suivant : 000078[Thrombosed scapular intramuscular venous malformation: A pediatric case report].
Auteurs : A. Fekir ; X. Balguerie ; I. Bardoux ; J-N Dacher ; P-H VivierSource :
- Archives de pediatrie : organe officiel de la Societe francaise de pediatrie [ 1769-664X ] ; 2015.
English descriptors
- KwdEn :
- MESH :
- blood supply : Muscle, Skeletal.
- complications : Thrombosis, Vascular Malformations.
- diagnosis : Thrombosis, Vascular Malformations.
- Child, Humans, Male, Scapula.
Abstract
Venous malformation (VM) is a frequent soft tissue mass in children that should not be confused with vascular tumors. We report the case of a 10-year-old boy with a bulky thrombosed VM of the shoulder with functional disability. D-dimer levels were high. Pathognomonic phleboliths were demonstrated on conventional x-rays. Echo-doppler confirmed the venous nature of the lesion and areas without flow suspicious for thrombosis. MRI provides the deep extension and can show non-calcified thrombi that are difficult to see with ultrasound. Localized intravascular coagulopathy is often associated with thrombosis phenomena and has to be confirmed by measurement of D-dimer levels in order to initiate anticoagulation quickly with low-molecular-weight heparin. Follow-up includes measurement of D-dimer levels and potentially MRI to evaluate the anticoagulation efficacy and tailor treatment duration.
DOI: 10.1016/j.arcped.2015.04.014
PubMed: 26047748
Links to Exploration step
pubmed:26047748Le document en format XML
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<author><name sortKey="Fekir, A" sort="Fekir, A" uniqKey="Fekir A" first="A" last="Fekir">A. Fekir</name>
<affiliation><nlm:affiliation>Service d'imagerie pédiatrique et fœtale, CHU Charles-Nicolle, 1, rue de Germont, 76031 Rouen cedex, France. Electronic address: amel9219@hotmail.com.</nlm:affiliation>
</affiliation>
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<author><name sortKey="Balguerie, X" sort="Balguerie, X" uniqKey="Balguerie X" first="X" last="Balguerie">X. Balguerie</name>
<affiliation><nlm:affiliation>Service de dermatologie, CHU Charles-Nicolle, 1, rue de Germont, 76031 Rouen cedex, France.</nlm:affiliation>
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<author><name sortKey="Bardoux, I" sort="Bardoux, I" uniqKey="Bardoux I" first="I" last="Bardoux">I. Bardoux</name>
<affiliation><nlm:affiliation>Service d'imagerie pédiatrique et fœtale, CHU Charles-Nicolle, 1, rue de Germont, 76031 Rouen cedex, France.</nlm:affiliation>
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<author><name sortKey="Dacher, J N" sort="Dacher, J N" uniqKey="Dacher J" first="J-N" last="Dacher">J-N Dacher</name>
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<author><name sortKey="Vivier, P H" sort="Vivier, P H" uniqKey="Vivier P" first="P-H" last="Vivier">P-H Vivier</name>
<affiliation><nlm:affiliation>Service d'imagerie pédiatrique et fœtale, CHU Charles-Nicolle, 1, rue de Germont, 76031 Rouen cedex, France; X-Ray expert, Maison médicale de l'Hôpital privé de l'Estuaire, 505, rue Irène-Joliot-Curie, 76620 Le Havre, France.</nlm:affiliation>
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<affiliation><nlm:affiliation>Service d'imagerie pédiatrique et fœtale, CHU Charles-Nicolle, 1, rue de Germont, 76031 Rouen cedex, France; X-Ray expert, Maison médicale de l'Hôpital privé de l'Estuaire, 505, rue Irène-Joliot-Curie, 76620 Le Havre, France.</nlm:affiliation>
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<term>Muscle, Skeletal (blood supply)</term>
<term>Scapula</term>
<term>Thrombosis (complications)</term>
<term>Thrombosis (diagnosis)</term>
<term>Vascular Malformations (complications)</term>
<term>Vascular Malformations (diagnosis)</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Thrombosis</term>
<term>Vascular Malformations</term>
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<term>Vascular Malformations</term>
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<front><div type="abstract" xml:lang="en">Venous malformation (VM) is a frequent soft tissue mass in children that should not be confused with vascular tumors. We report the case of a 10-year-old boy with a bulky thrombosed VM of the shoulder with functional disability. D-dimer levels were high. Pathognomonic phleboliths were demonstrated on conventional x-rays. Echo-doppler confirmed the venous nature of the lesion and areas without flow suspicious for thrombosis. MRI provides the deep extension and can show non-calcified thrombi that are difficult to see with ultrasound. Localized intravascular coagulopathy is often associated with thrombosis phenomena and has to be confirmed by measurement of D-dimer levels in order to initiate anticoagulation quickly with low-molecular-weight heparin. Follow-up includes measurement of D-dimer levels and potentially MRI to evaluate the anticoagulation efficacy and tailor treatment duration.</div>
</front>
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<ArticleTitle>[Thrombosed scapular intramuscular venous malformation: A pediatric case report].</ArticleTitle>
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<Abstract><AbstractText>Venous malformation (VM) is a frequent soft tissue mass in children that should not be confused with vascular tumors. We report the case of a 10-year-old boy with a bulky thrombosed VM of the shoulder with functional disability. D-dimer levels were high. Pathognomonic phleboliths were demonstrated on conventional x-rays. Echo-doppler confirmed the venous nature of the lesion and areas without flow suspicious for thrombosis. MRI provides the deep extension and can show non-calcified thrombi that are difficult to see with ultrasound. Localized intravascular coagulopathy is often associated with thrombosis phenomena and has to be confirmed by measurement of D-dimer levels in order to initiate anticoagulation quickly with low-molecular-weight heparin. Follow-up includes measurement of D-dimer levels and potentially MRI to evaluate the anticoagulation efficacy and tailor treatment duration.</AbstractText>
<CopyrightInformation>Copyright © 2015 Elsevier Masson SAS. All rights reserved.</CopyrightInformation>
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<VernacularTitle>Malformation veineuse intramusculaire scapulaire thrombosée : à propos d'un cas chez un enfant.</VernacularTitle>
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