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Effects of 1-month withdrawal of ventilatory support in hypercapnic myotonic dystrophy type 1.

Identifieur interne : 004787 ( Ncbi/Checkpoint ); précédent : 004786; suivant : 004788

Effects of 1-month withdrawal of ventilatory support in hypercapnic myotonic dystrophy type 1.

Auteurs : Fergal J. O'Donoghue [Australie] ; Jean-Christian Borel [France] ; Yves Dauvilliers [France] ; Patrick Levy [France] ; Renaud Tamisier [France] ; Jean-Louis Pépin [France]

Source :

RBID : pubmed:28485522

Abstract

The benefits of domiciliary non-invasive ventilation (NIV) in myotonic dystrophy type 1 (DM1) are unclear. We sought to determine the effects of elective discontinuation of ventilatory support for 1 month in DM1 patients receiving NIV for chronic hypercapnic respiratory failure.

DOI: 10.1111/resp.13068
PubMed: 28485522


Affiliations:


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pubmed:28485522

Le document en format XML

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