Effects of 1-month withdrawal of ventilatory support in hypercapnic myotonic dystrophy type 1.
Identifieur interne : 004787 ( Ncbi/Checkpoint ); précédent : 004786; suivant : 004788Effects of 1-month withdrawal of ventilatory support in hypercapnic myotonic dystrophy type 1.
Auteurs : Fergal J. O'Donoghue [Australie] ; Jean-Christian Borel [France] ; Yves Dauvilliers [France] ; Patrick Levy [France] ; Renaud Tamisier [France] ; Jean-Louis Pépin [France]Source :
- Respirology (Carlton, Vic.) [ 1440-1843 ] ; 2017.
Abstract
The benefits of domiciliary non-invasive ventilation (NIV) in myotonic dystrophy type 1 (DM1) are unclear. We sought to determine the effects of elective discontinuation of ventilatory support for 1 month in DM1 patients receiving NIV for chronic hypercapnic respiratory failure.
DOI: 10.1111/resp.13068
PubMed: 28485522
Affiliations:
- Australie, France
- Auvergne-Rhône-Alpes, Languedoc-Roussillon, Occitanie (région administrative), Rhône-Alpes
- Grenoble, Montpellier
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<front><div type="abstract" xml:lang="en">The benefits of domiciliary non-invasive ventilation (NIV) in myotonic dystrophy type 1 (DM1) are unclear. We sought to determine the effects of elective discontinuation of ventilatory support for 1 month in DM1 patients receiving NIV for chronic hypercapnic respiratory failure.</div>
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