La maladie de Parkinson au Canada (serveur d'exploration)

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Pathologic correlates of supranuclear gaze palsy with parkinsonism.

Identifieur interne : 000039 ( PubMed/Checkpoint ); précédent : 000038; suivant : 000040

Pathologic correlates of supranuclear gaze palsy with parkinsonism.

Auteurs : W R W. Martin [Canada] ; J. Hartlein [États-Unis] ; B A Racette [Afrique du Sud] ; N. Cairns [États-Unis] ; J S Perlmutter [États-Unis]

Source :

RBID : pubmed:28256434

English descriptors

Abstract

Supranuclear gaze palsy (SGP) is a classic clinical feature of progressive supranuclear palsy (PSP) but is not specific for this diagnosis and has been reported to occur in several other neurodegenerative parkinsonian conditions. Our objective was to evaluate the association between SGP and autopsy-proven diagnoses in a large population of patients with parkinsonism referred to a tertiary movement disorders clinic.

DOI: 10.1016/j.parkreldis.2017.02.027
PubMed: 28256434


Affiliations:


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pubmed:28256434

Le document en format XML

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<div type="abstract" xml:lang="en">Supranuclear gaze palsy (SGP) is a classic clinical feature of progressive supranuclear palsy (PSP) but is not specific for this diagnosis and has been reported to occur in several other neurodegenerative parkinsonian conditions. Our objective was to evaluate the association between SGP and autopsy-proven diagnoses in a large population of patients with parkinsonism referred to a tertiary movement disorders clinic.</div>
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<AbstractText Label="INTRODUCTION" NlmCategory="BACKGROUND">Supranuclear gaze palsy (SGP) is a classic clinical feature of progressive supranuclear palsy (PSP) but is not specific for this diagnosis and has been reported to occur in several other neurodegenerative parkinsonian conditions. Our objective was to evaluate the association between SGP and autopsy-proven diagnoses in a large population of patients with parkinsonism referred to a tertiary movement disorders clinic.</AbstractText>
<AbstractText Label="METHODS" NlmCategory="METHODS">We reviewed clinical and autopsy data maintained in an electronic medical record from all patients seen in the Movement Disorders Clinic at Washington University, St. Louis between 1996 and 2015. All patients with parkinsonism from this population who had subsequent autopsy confirmation of diagnosis underwent further analysis.</AbstractText>
<AbstractText Label="RESULTS" NlmCategory="RESULTS">221 unique parkinsonian patients had autopsy-proven diagnoses, 27 of whom had SGP documented at some point during their illness. Major diagnoses associated with SGP were: PSP (9 patients), Parkinson disease (PD) (10 patients), multiple system atrophy (2 patients), corticobasal degeneration (2 patients), Creutzfeld-Jakob disease (1 patient) and Huntington disease (1 patient). In none of the diagnostic groups was the age of onset or disease duration significantly different between cases with SGP and those without SGP. In the PD patients, the UPDRS motor score differed significantly between groups (p = 0.01) with the PD/SGP patients having greater motor deficit than those without SGP.</AbstractText>
<AbstractText Label="CONCLUSION" NlmCategory="CONCLUSIONS">Although a common feature of PSP, SGP is not diagnostic for this condition and can be associated with other neurodegenerative causes of parkinsonism including PD.</AbstractText>
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</MeshHeading>
</MeshHeadingList>
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<Keyword MajorTopicYN="N">Parkinson disease</Keyword>
<Keyword MajorTopicYN="N">Parkinsonism</Keyword>
<Keyword MajorTopicYN="N">Progressive supranuclear palsy</Keyword>
<Keyword MajorTopicYN="N">Supranuclear gaze palsy</Keyword>
</KeywordList>
</MedlineCitation>
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<Year>2016</Year>
<Month>12</Month>
<Day>17</Day>
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<PubMedPubDate PubStatus="revised">
<Year>2017</Year>
<Month>02</Month>
<Day>07</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="accepted">
<Year>2017</Year>
<Month>02</Month>
<Day>21</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="pmc-release">
<Year>2018</Year>
<Month>05</Month>
<Day>01</Day>
</PubMedPubDate>
<PubMedPubDate PubStatus="pubmed">
<Year>2017</Year>
<Month>3</Month>
<Day>4</Day>
<Hour>6</Hour>
<Minute>0</Minute>
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<PubMedPubDate PubStatus="medline">
<Year>2017</Year>
<Month>5</Month>
<Day>2</Day>
<Hour>6</Hour>
<Minute>0</Minute>
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<PubMedPubDate PubStatus="entrez">
<Year>2017</Year>
<Month>3</Month>
<Day>4</Day>
<Hour>6</Hour>
<Minute>0</Minute>
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</History>
<PublicationStatus>ppublish</PublicationStatus>
<ArticleIdList>
<ArticleId IdType="pubmed">28256434</ArticleId>
<ArticleId IdType="pii">S1353-8020(17)30077-9</ArticleId>
<ArticleId IdType="doi">10.1016/j.parkreldis.2017.02.027</ArticleId>
<ArticleId IdType="pmc">PMC5397329</ArticleId>
<ArticleId IdType="mid">NIHMS856171</ArticleId>
</ArticleIdList>
</PubmedData>
</pubmed>
<affiliations>
<list>
<country>
<li>Afrique du Sud</li>
<li>Canada</li>
<li>États-Unis</li>
</country>
<region>
<li>Missouri (État)</li>
</region>
<settlement>
<li>Saint-Louis (Missouri)</li>
</settlement>
<orgName>
<li>Université Washington de Saint-Louis</li>
</orgName>
</list>
<tree>
<country name="Canada">
<noRegion>
<name sortKey="Martin, W R W" sort="Martin, W R W" uniqKey="Martin W" first="W R W" last="Martin">W R W. Martin</name>
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</country>
<country name="États-Unis">
<region name="Missouri (État)">
<name sortKey="Hartlein, J" sort="Hartlein, J" uniqKey="Hartlein J" first="J" last="Hartlein">J. Hartlein</name>
</region>
<name sortKey="Cairns, N" sort="Cairns, N" uniqKey="Cairns N" first="N" last="Cairns">N. Cairns</name>
<name sortKey="Perlmutter, J S" sort="Perlmutter, J S" uniqKey="Perlmutter J" first="J S" last="Perlmutter">J S Perlmutter</name>
</country>
<country name="Afrique du Sud">
<region name="Missouri (État)">
<name sortKey="Racette, B A" sort="Racette, B A" uniqKey="Racette B" first="B A" last="Racette">B A Racette</name>
</region>
</country>
</tree>
</affiliations>
</record>

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